ICD-10-CM Code Q04.6

Congenital cerebral cysts

Version 2020 Billable Code POA Exempt

Valid for Submission

Q04.6 is a billable code used to specify a medical diagnosis of congenital cerebral cysts. The code is valid for the year 2020 for the submission of HIPAA-covered transactions. The ICD-10-CM code Q04.6 might also be used to specify conditions or terms like absent tibia, polydactyly, arachnoid cyst syndrome, arachnoid cyst, arachnoid cyst, bilateral congenital cataract of eyes, cerebellar ataxia, intellectual disability, oculomotor apraxia, cerebellar cysts syndrome, choroid plexus cyst, etc The code is exempt from present on admission (POA) reporting for inpatient admissions to general acute care hospitals.

Short Description:Congenital cerebral cysts
Long Description:Congenital cerebral cysts

Tabular List of Diseases and Injuries

The Tabular List of Diseases and Injuries is a list of ICD-10 codes, organized "head to toe" into chapters and sections with guidance for inclusions, exclusions, descriptions and more. The following references are applicable to the code Q04.6:

Inclusion Terms

Inclusion Terms
These terms are the conditions for which that code is to be used. The terms may be synonyms of the code title, or, in the case of "other specified" codes, the terms are a list of the various conditions assigned to that code. The inclusion terms are not necessarily exhaustive. Additional terms found only in the Alphabetic Index may also be assigned to a code.
  • Porencephaly
  • Schizencephaly

Type 1 Excludes

Type 1 Excludes
A type 1 excludes note is a pure excludes note. It means "NOT CODED HERE!" An Excludes1 note indicates that the code excluded should never be used at the same time as the code above the Excludes1 note. An Excludes1 is used when two conditions cannot occur together, such as a congenital form versus an acquired form of the same condition.
  • acquired porencephalic cyst G93.0

Index to Diseases and Injuries

The Index to Diseases and Injuries is an alphabetical listing of medical terms, with each term mapped to one or more ICD-10 code(s). The following references for the code Q04.6 are found in the index:


The following clinical terms are approximate synonyms or lay terms that might be used to identify the correct diagnosis code:

  • Absent tibia, polydactyly, arachnoid cyst syndrome
  • Arachnoid cyst
  • Arachnoid cyst
  • Bilateral congenital cataract of eyes
  • Cerebellar ataxia, intellectual disability, oculomotor apraxia, cerebellar cysts syndrome
  • Choroid plexus cyst
  • Colloid brain cyst
  • Colloid cyst of third ventricle
  • Congenital cataract of left eye
  • Congenital cataract of right eye
  • Congenital cerebral cyst
  • Congenital choroid plexus cyst
  • Congenital porencephalic cyst
  • Congenital porencephaly
  • Congenital pseudoporencephaly
  • Early secondary malformation of the central nervous system
  • Multiple congenital cerebral cysts
  • Oculomotor apraxia
  • Partial corpus callosum agenesis, cerebellar vermis hypoplasia with posterior fossa cysts syndrome
  • Persistent Blake's pouch cyst
  • Porencephalic cyst
  • Porencephaly, cerebellar hypoplasia, internal malformations syndrome
  • Porencephaly, microcephaly, bilateral congenital cataract syndrome
  • Posterior fossa arachnoid cyst
  • Pseudoporencephaly
  • Schizencephaly
  • Single congenital cerebral cyst

Present on Admission (POA)

Q04.6 is exempt from POA reporting - The Present on Admission (POA) indicator is used for diagnosis codes included in claims involving inpatient admissions to general acute care hospitals. POA indicators must be reported to CMS on each claim to facilitate the grouping of diagnoses codes into the proper Diagnostic Related Groups (DRG). CMS publishes a listing of specific diagnosis codes that are exempt from the POA reporting requirement. Review other POA exempt codes here .

CMS POA Indicator Options and Definitions
POA Indicator CodePOA Reason for CodeCMS will pay the CC/MCC DRG?
YDiagnosis was present at time of inpatient admission.YES
NDiagnosis was not present at time of inpatient admission.NO
UDocumentation insufficient to determine if the condition was present at the time of inpatient admission.NO
WClinically undetermined - unable to clinically determine whether the condition was present at the time of inpatient admission.YES
1Unreported/Not used - Exempt from POA reporting. NO

Convert Q04.6 to ICD-9

  • 742.4 - Brain anomaly NEC (Approximate Flag)

Code Classification

  • Congenital malformations, deformations and chromosomal abnormalities (Q00-Q99)
    • Congenital malformations of the nervous system (Q00-Q07)
      • Other congenital malformations of brain (Q04)

Code History

  • FY 2016 - New Code, effective from 10/1/2015 through 9/30/2016
    (First year ICD-10-CM implemented into the HIPAA code set)
  • FY 2017 - No Change, effective from 10/1/2016 through 9/30/2017
  • FY 2018 - No Change, effective from 10/1/2017 through 9/30/2018
  • FY 2019 - No Change, effective from 10/1/2018 through 9/30/2019
  • FY 2020 - No Change, effective from 10/1/2019 through 9/30/2020

Information for Patients

Brain Diseases

The brain is the control center of the body. It controls thoughts, memory, speech, and movement. It regulates the function of many organs. When the brain is healthy, it works quickly and automatically. However, when problems occur, the results can be devastating.

Inflammation in the brain can lead to problems such as vision loss, weakness and paralysis. Loss of brain cells, which happens if you suffer a stroke, can affect your ability to think clearly. Brain tumors can also press on nerves and affect brain function. Some brain diseases are genetic. And we do not know what causes some brain diseases, such as Alzheimer's disease.

The symptoms of brain diseases vary widely depending on the specific problem. In some cases, damage is permanent. In other cases, treatments such as surgery, medicines, or physical therapy can correct the source of the problem or improve symptoms.

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Familial porencephaly Familial porencephaly is part of a group of conditions called the COL4A1-related disorders. The conditions in this group have a range of signs and symptoms that involve fragile blood vessels. In familial porencephaly, fluid-filled cysts develop in the brain (porencephaly) during fetal development or soon after birth. These cysts typically occur in only one side of the brain and vary in size. The cysts are thought to be the result of bleeding within the brain (hemorrhagic stroke). People with this condition also have leukoencephalopathy, which is a change in a type of brain tissue called white matter that can be seen with magnetic resonance imaging (MRI).During infancy, people with familial porencephaly typically have paralysis affecting one side of the body (infantile hemiplegia). Affected individuals may also have recurrent seizures (epilepsy), migraine headaches, speech problems, intellectual disability, and uncontrolled muscle tensing (dystonia). Some people are severely affected, and others may have no symptoms related to the brain cysts.
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