ICD-10 Diagnosis Code E76.3

Mucopolysaccharidosis, unspecified

Diagnosis Code E76.3

ICD-10: E76.3
Short Description: Mucopolysaccharidosis, unspecified
Long Description: Mucopolysaccharidosis, unspecified
This is the 2017 version of the ICD-10-CM diagnosis code E76.3

Valid for Submission
The code E76.3 is valid for submission for HIPAA-covered transactions.

Code Classification
  • Endocrine, nutritional and metabolic diseases (E00–E90)
    • Metabolic disorders (E70-E88)
      • Disorders of glycosaminoglycan metabolism (E76)

Information for Medical Professionals

Convert to ICD-9 Additional informationCallout TooltipGeneral Equivalence Map
The ICD-10 and ICD-9 GEMs are used to facilitate linking between the diagnosis codes in ICD-9-CM and the new ICD-10-CM code set. The GEMs are the raw material from which providers, health information vendors and payers can derive specific applied mappings to meet their needs.

  • Cerebral degeneration in mucopolysaccharidosis
  • Dilated cardiomyopathy secondary to metabolic disorder
  • Dilated cardiomyopathy secondary to mucopolysaccharidosis
  • Mucopolysaccharidosis
  • Mucopolysaccharidosis cardiomyopathy
  • Mucopolysaccharidosis type I
  • Nutritional and metabolic cardiomyopathies
  • Restrictive cardiomyopathy secondary to mucopolysaccharidosis
  • Secondary restrictive cardiomyopathy

Information for Patients

Carbohydrate Metabolism Disorders

Metabolism is the process your body uses to make energy from the food you eat. Food is made up of proteins, carbohydrates, and fats. Chemicals in your digestive system (enzymes) break the food parts down into sugars and acids, your body's fuel. Your body can use this fuel right away, or it can store the energy in your body tissues. If you have a metabolic disorder, something goes wrong with this process.

Carbohydrate metabolism disorders are a group of metabolic disorders. Normally your enzymes break carbohydrates down into glucose (a type of sugar). If you have one of these disorders, you may not have enough enzymes to break down the carbohydrates. Or the enzymes may not work properly. This causes a harmful amount of sugar to build up in your body. That can lead to health problems, some of which can be serious. Some of the disorders are fatal.

These disorders are inherited. Newborn babies get screened for many of them, using blood tests. If there is a family history of one of these disorders, parents can get genetic testing to see whether they carry the gene. Other genetic tests can tell whether the fetus has the disorder or carries the gene for the disorder.

Treatments may include special diets, supplements, and medicines. Some babies may also need additional treatments, if there are complications. For some disorders, there is no cure, but treatments may help with symptoms.

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