ICD-10-CM Alphabetic Index · FY 2026 26 Entries

Mucopolysaccharidosis in the ICD-10-CM Index ICD-10-CM

The main term Mucopolysaccharidosis carries 26 index entries pointing to 10 ICD-10-CM codes. The default entry is E76.3, the code the bare main term maps to; every indented line below refines the term by site, cause, or type. Verify any candidate code in the Tabular List before using it.

✓ Built from the official CMS FY 2026 index fileEffective Oct 1, 2025 – Sep 30, 2026

Index Entries

Codes Referenced

E76.3

Default Code

Letter

26 of 26 shown

ICD-10-CM

Index Entries Under Mucopolysaccharidosis 26 entries · 10 codes

Mucopolysaccharidosis E76.3

beta-gluduronidase deficiency E76.29

cardiopathy E76.3

Hunter's syndrome E76.1

Hurler's syndrome E76.01

Hurler-Scheie syndrome E76.02

Maroteaux-Lamy syndrome E76.29

Morquio syndrome E76.219

A E76.210

B E76.211

classic E76.210

Sanfilippo syndrome E76.22

Scheie's syndrome E76.03

specified NEC E76.29

type

Hurler's syndrome E76.01

Hurler-Scheie syndrome E76.02

Scheie's syndrome E76.03

II E76.1

III E76.22

IV E76.219

IVA E76.210

IVB E76.211

VI E76.29

VII E76.29

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Related Index Terms

All index terms starting with M Index to Diseases and Injuries ICD-10-CM Code Lookup

Source: Centers for Medicare & Medicaid Services, FY 2026 ICD-10-CM Index to Diseases and Injuries release files, effective October 1, 2025 through September 30, 2026.