ICD-10-CM Mucopolysaccharidosis References

"Mucopolysaccharidosis" Annotation Back-References in the ICD-10-CM Index to Diseases and Injuries

Browse the ICD-10-CM codes with references applicable to the clinical term "mucopolysaccharidosis"

  • Mucopolysaccharidosis - E76.3 Mucopolysaccharidosis, unspecified
    • beta-gluduronidase deficiency - E76.29 Other mucopolysaccharidoses
    • cardiopathy - E76.3 Mucopolysaccharidosis, unspecified
    • Hunter's syndrome - E76.1 Mucopolysaccharidosis, type II
    • Hurler's syndrome - E76.01 Hurler's syndrome
    • Hurler-Scheie syndrome - E76.02 Hurler-Scheie syndrome
    • Maroteaux-Lamy syndrome - E76.29 Other mucopolysaccharidoses
    • Morquio syndrome - E76.219 Morquio mucopolysaccharidoses, unspecified
      • A - E76.210 Morquio A mucopolysaccharidoses
      • B - E76.211 Morquio B mucopolysaccharidoses
      • classic - E76.210 Morquio A mucopolysaccharidoses
    • Sanfilippo syndrome - E76.22 Sanfilippo mucopolysaccharidoses
    • Scheie's syndrome - E76.03 Scheie's syndrome
    • specified NEC - E76.29 Other mucopolysaccharidoses
    • type
      • I
        • Hurler's syndrome - E76.01 Hurler's syndrome
        • Hurler-Scheie syndrome - E76.02 Hurler-Scheie syndrome
        • Scheie's syndrome - E76.03 Scheie's syndrome
      • II - E76.1 Mucopolysaccharidosis, type II
      • III - E76.22 Sanfilippo mucopolysaccharidoses
      • IV - E76.219 Morquio mucopolysaccharidoses, unspecified
      • IVA - E76.210 Morquio A mucopolysaccharidoses
      • IVB - E76.211 Morquio B mucopolysaccharidoses
      • VI - E76.29 Other mucopolysaccharidoses
      • VII - E76.29 Other mucopolysaccharidoses