2026 ICD-10-CM Diagnosis Code E76Disorders of glycosaminoglycan metabolism

ICD-10-CM Codes›E00–E89›E70-E88›E76

ICD-10-CM E76
CMSSource: CMS FY 2026 ICD-10-CM dataset · Effective Oct 1, 2025 – Sep 30, 2026

E76 is a non-billable ICD-10-CM category code for disorders of glycosaminoglycan metabolism, so it cannot be submitted on claims. Use a more specific code from this category instead, such as E76.01, E76.02, E76.03, and E76.1.

Code Identity

ICD-10-CM Code
E76
Billable Status
No — Non-Billable Category
Code Describes
Disorders of glycosaminoglycan metabolism
Chapter
E70-E88
Metabolic disorders

Code Classification

ChapterE00–E89Endocrine, nutritional and metabolic diseases
SectionE70-E88Metabolic disorders
CategoryE76Disorders of glycosaminoglycan metabolism
This CodeE76Disorders of glycosaminoglycan metabolism

Specific Coding for Disorders of glycosaminoglycan metabolismOverview

Non-specific codes like E76 require more characters. Use one of these billable codes instead:

  • E76.0 for Mucopolysaccharidosis, type I

  • Use E76.01 for Hurler's syndrome

  • Use E76.02 for Hurler-Scheie syndrome

  • Use E76.03 for Scheie's syndrome

  • Use E76.1 for Mucopolysaccharidosis, type II

  • E76.2 for Other mucopolysaccharidoses

  • E76.21 for Morquio mucopolysaccharidoses

  • Use E76.22 for Sanfilippo mucopolysaccharidoses

  • Use E76.29 for Other mucopolysaccharidoses

  • Use E76.3 for Mucopolysaccharidosis, unspecified

  • Use E76.8 for Other disorders of glucosaminoglycan metabolism

  • Use E76.9 for Glucosaminoglycan metabolism disorder, unspecified

Patient EducationClinical

Carbohydrate Metabolism Disorders

Metabolism is the process your body uses to make energy from the food you eat. Food is made up of proteins, carbohydrates, and fats. Chemicals in your digestive system (enzymes) break the food parts down into sugars and acids, your body's fuel. Your body can use this fuel right away, or it can store the energy in your body tissues.

Read the full article at MedlinePlus

Courtesy of MedlinePlus, a service of the U.S. National Library of Medicine.

Code HistoryHistory

FY 2016AddedAdded to the ICD-10-CM code setEffective October 1, 2015, the first year of ICD-10-CM.
FY 2017–2025No changes
FY 2026CurrentCurrent code set, no changesEffective October 1, 2025 through September 30, 2026.

Questions About E76Overview

Is E76 (Disorders of glycosaminoglycan metabolism) a billable code?

No. This is a category header that groups the codes for disorders of glycosaminoglycan metabolism, and headers cannot be submitted on claims. Claims for disorders of glycosaminoglycan metabolism need a more specific code from this category, such as E76.01, E76.02, and E76.03.