2026 ICD-10-CM Diagnosis Code M34.1CR(E)ST syndrome

ICD-10-CM Codes›M00–M99›M30-M36›M34

ICD-10-CM M34.1
CMSSource: CMS FY 2026 ICD-10-CM dataset · Effective Oct 1, 2025 – Sep 30, 2026

M34.1 is a billable ICD-10-CM diagnosis code for CR(E)ST syndrome. It is valid on HIPAA claims for fiscal year 2026 (October 1, 2025 through September 30, 2026) and groups to MS-DRG 545 through 547. Coders also document this condition as CREST syndrome. In AHRQ's Clinical Classifications Software (CCSR), this diagnosis falls under Systemic lupus erythematosus and connective tissue disorders.

Code Identity

ICD-10-CM Code
M34.1
Billable Status
Yes — Valid for Submission
Code Describes
CR(E)ST syndrome
Short Description
CR(E)ST syndrome
Same as the full description in the CMS dataset.
Parent Code
M34
Systemic sclerosis [scleroderma]

Code Classification

ChapterM00–M99Diseases of the musculoskeletal system and connective tissue
SectionM30-M36Systemic connective tissue disorders
CategoryM34Systemic sclerosis [scleroderma]
This CodeM34.1CR(E)ST syndrome

Approximate SynonymsGuidance

Alternate terms and clinical phrases that map to this code.

  • CREST syndrome
  • CRST syndrome
  • Limited systemic sclerosis
  • Raynaud's phenomenon
  • Secondary Raynaud's phenomenon
  • Systemic sclerosis with limited cutaneous involvement

Tabular List NotesGuidance

Coding notes and annotation back-references applicable to this code.

Inclusion Terms

  • Combination of calcinosis, Raynaud's phenomenon, esophageal dysfunction, sclerodactyly, telangiectasia

Index to Diseases and InjuriesGuidance

Alphabetical index entries that point to this code.

External Cause of Injuries IndexGuidance

References for this code in the External Cause of Injuries Index.

    • Calcinosis(interstitial) (tumoral) (universalis)
      • with Raynaud's phenomenon, esophageal dysfunction, sclerodactyly, telangiectasia (CREST syndrome)
    • CREST syndrome
    • CRST syndrome

Clinical ClassificationClinical

AHRQ’s CCSR groups this code into broader clinical categories.

CCSR MUS024
Systemic lupus erythematosus and connective tissue disorders
Default principal diagnosis: inpatient Yes · outpatient Yes

Clinical InformationClinical

  • CREST Syndrome

    a mild form of limited scleroderma, a multi-system disorder. its features include symptoms of calcinosis; raynaud disease; esophageal motility disorders; sclerodactyly, and telangiectasis. when the defect in esophageal function is not prominent, it is known as crst syndrome.

Patient EducationClinical

Scleroderma

Scleroderma means "hard skin." It's the name of an autoimmune disease that causes inflammation and thickening in the skin and other areas of the body. This inflammation causes you to have areas of tight, hard skin. Scleroderma may affect just one area of your body, or it can affect many systems in your body.

The full article covers:

  • What is scleroderma?
  • What are the types of scleroderma?
  • What causes scleroderma?
  • Who is more likely to develop scleroderma?
  • What are the symptoms of scleroderma?
  • How is scleroderma diagnosed?
  • What are the treatments for scleroderma?

Read the full article at MedlinePlus

Courtesy of MedlinePlus, a service of the U.S. National Library of Medicine.

Convert M34.1 to ICD-9-CMHistory

The closest ICD-9-CM equivalents under the General Equivalence Mappings.

ICD-9-CM
710.1 Systemic sclerosis
Approximate The match is approximate rather than exact.

Code HistoryHistory

FY 2016AddedAdded to the ICD-10-CM code setEffective October 1, 2015, the first year of ICD-10-CM.
FY 2017–2025No changes
FY 2026CurrentCurrent code set, no changesEffective October 1, 2025 through September 30, 2026.

Questions About M34.1Overview

Is M34.1 (Systemic sclerosis [scleroderma]) a billable code?

Yes. This is a billable ICD-10-CM code, specific enough to report CR(E)ST syndrome on HIPAA-covered claims from October 1, 2025 through September 30, 2026.

What MS-DRG does M34.1 group to?

When CR(E)ST syndrome is the principal diagnosis on an inpatient stay, it groups to MS-DRG 545, 546, 547, with relative weights from 0.8362 to 2.4817 depending on complications. Higher weights mean higher Medicare reimbursement.

What is the ICD-9 equivalent of M34.1?

Under the General Equivalence Mappings, CR(E)ST syndrome converts to ICD-9-CM 710.1 (systemic sclerosis). The mapping is approximate, so confirm the match fits the documentation.

Footnotes

[1] Chronic - a chronic condition code indicates a condition lasting 12 months or longer and its effect on the patient based on one or both of the following criteria:

  • The condition results in the need for ongoing intervention with medical products,treatment, services, and special equipment
  • The condition places limitations on self-care, independent living, and social interactions.