2026 ICD-10-CM Diagnosis Code I01.0Acute rheumatic pericarditis

ICD-10-CM CodesI00–I99I00-I02I01

ICD-10-CM I01.0
CMSSource: CMS FY 2026 ICD-10-CM dataset · Effective Oct 1, 2025 – Sep 30, 2026

I01.0 is a billable ICD-10-CM diagnosis code for acute rheumatic pericarditis. It is valid on HIPAA claims for fiscal year 2026 (October 1, 2025 through September 30, 2026) and groups to MS-DRG 314 through 316. Coders also document this condition as acute rheumatic fever. In AHRQ's Clinical Classifications Software (CCSR), this diagnosis falls under Acute rheumatic heart disease and Pericarditis and pericardial disease.

Code Identity

ICD-10-CM Code
I01.0
Billable Status
Yes — Valid for Submission
Code Describes
Acute rheumatic pericarditis
Short Description
Acute rheumatic pericarditis
Same as the full description in the CMS dataset.
Parent Code
Rheumatic fever with heart involvement

Code Classification

ChapterI00–I99Diseases of the circulatory system
SectionI00-I02Acute rheumatic fever
CategoryI01Rheumatic fever with heart involvement
This CodeI01.0Acute rheumatic pericarditis

Approximate SynonymsGuidance

Alternate terms and clinical phrases that map to this code.

  • Acute rheumatic fever
  • Acute rheumatic heart disease
  • Acute rheumatic pericarditis

Tabular List NotesGuidance

Coding notes and annotation back-references applicable to this code.

Inclusion Terms

  • Any condition in I00
  • Rheumatic pericarditis (acute)

Type 1 Excludes

  • acute pericarditis not specified as rheumatic I30

Index to Diseases and InjuriesGuidance

External Cause of Injuries IndexGuidance

References for this code in the External Cause of Injuries Index.

    • Pericarditis(with decompensation) (with effusion)
      • acute (hemorrhagic) (nonrheumatic) (Sicca)
        • rheumatic
    • Pericarditis(with decompensation) (with effusion)
      • rheumatic (active) (acute) (with effusion) (with pneumonia)
    • Rheumatic(acute) (subacute)
      • pericarditis (active) (acute) (with effusion) (with pneumonia)

Clinical ClassificationClinical

AHRQ’s CCSR groups this code into broader clinical categories.

CCSR CIR002
Acute rheumatic heart disease
Default principal diagnosis: inpatient Yes · outpatient Yes
CCSR CIR006
Pericarditis and pericardial disease
Default principal diagnosis: inpatient No · outpatient No

Clinical InformationClinical

  • Acute Rheumatic Pericarditis

    inflammation of the pericardium in acute rheumatic heart disease.

Patient EducationClinical

Pericardial Disorders

The pericardium is a membrane, or sac, that surrounds your heart. It holds the heart in place and helps it work properly. Problems with the pericardium include:

Read the full article at MedlinePlus

Courtesy of MedlinePlus, a service of the U.S. National Library of Medicine.

Convert I01.0 to ICD-9-CMHistory

The closest ICD-9-CM equivalents under the General Equivalence Mappings.

ICD-9-CM
391.0 Acute rheumatic pericard
Exact Match The mapping is direct, with no qualifiers.

Code HistoryHistory

FY 2016AddedAdded to the ICD-10-CM code setEffective October 1, 2015, the first year of ICD-10-CM.
FY 2017–2025No changes
FY 2026CurrentCurrent code set, no changesEffective October 1, 2025 through September 30, 2026.

Questions About I01.0Overview

Is I01.0 (Rheumatic fever with heart involvement) a billable code?

Yes. This is a billable ICD-10-CM code, specific enough to report acute rheumatic pericarditis on HIPAA-covered claims from October 1, 2025 through September 30, 2026.

What MS-DRG does I01.0 group to?

When acute rheumatic pericarditis is the principal diagnosis on an inpatient stay, it groups to MS-DRG 314, 315, 316, with relative weights from 0.6821 to 2.0852 depending on complications. Higher weights mean higher Medicare reimbursement.

What is the ICD-9 equivalent of I01.0?

Under the General Equivalence Mappings, acute rheumatic pericarditis converts to ICD-9-CM 391.0 (acute rheumatic pericard). The mapping is a direct match.

Footnotes

[1] Not chronic - A diagnosis code that does not fit the criteria for chronic condition (duration, ongoing medical treatment, and limitations) is considered not chronic. Some codes designated as not chronic are acute conditions. Other diagnosis codes that indicate a possible chronic condition, but for which the duration of the illness is not specified in the code description (i.e., we do not know the condition has lasted 12 months or longer) also are considered not chronic.