Congenital iodine-deficiency syndrome (E00) ICD-10-CM
The E00 code range covers congenital iodine-deficiency syndrome with 5 ICD-10-CM diagnosis codes. 4 of them are billable and valid for claim submission in fiscal year 2027, and the category headers group them but cannot themselves be billed.
Use Additional Code
The “use additional code” indicates that a secondary code could be used to further specify the patient’s condition. This note is not mandatory and is only used if enough information is available to assign an additional code.
Type 1 Excludes
A type 1 excludes note is a pure excludes note. It means "NOT CODED HERE!" An Excludes1 note indicates that the code excluded should never be used at the same time as the code above the Excludes1 note. An Excludes1 is used when two conditions cannot occur together, such as a congenital form versus an acquired form of the same condition.
- subclinical iodine-deficiency hypothyroidism E02
Codes in the E00 Range 5 codes · 4 billable
Clinical Terms in This Code Range
Definitions from the National Library of Medicine for conditions coded in the E00 range.
Congenital Iodine Deficiency Syndrome
A condition attributed to iodine deficiency during gestation. It is characterized by a spectrum of mental and physical disabilities.
Congenital Iodine Deficiency Syndrome, Mixed Type
Congenital iodine deficiency syndrome associated with overlapping features of both the neurological and myxedematous variants.
Congenital Iodine Deficiency Syndrome, Myxedematous Type
Congenital iodine deficiency syndrome associated with milder mental retardation, short stature, goiter, and hypothyroidism. It results from iodine deficiency and hypothyroidism in the fetus during late pregnancy or in the neonatal period.
Congenital Iodine Deficiency Syndrome, Neurological Type
Congenital iodine deficiency syndrome associated with mental retardation, deaf-mutism, and abnormal gait. It results from severe maternal iodine deficiency and hypothyroidism during pregnancy.
About the E00 Code Range
Congenital iodine-deficiency syndrome is linked to iodine deficiency during pregnancy and can involve mental and physical disabilities. It appears among disorders of the thyroid gland.
E00 separates the syndrome into neurological, myxedematous, mixed, and unspecified types. These appear under E00.0, E00.1, E00.2, and E00.9, respectively.
Questions About This Page
How many billable codes are in the E00 range?
Of the 5 codes in this range, 4 are billable and valid for claim submission from October 1, 2026 through September 30, 2027. Category header codes group them but cannot be reported on claims.
What does the E00 range classify?
The range classifies congenital iodine-deficiency syndrome. Each code links to its own reference page with billing status, MS-DRG grouping, coding notes, and clinical information.
Related References
Source: CMS FY 2027 ICD-10-CM Tabular List and order file, effective October 1, 2026 through September 30, 2027.
