2026 ICD-10-CM Diagnosis Code D18.00Hemangioma unspecified site
ICD-10-CM Codes›C00–D49›D10-D36›D18
- Billable — Valid for Submission
- Not Chronic
D18.00 is a billable ICD-10-CM diagnosis code for hemangioma unspecified site. It is valid on HIPAA claims for fiscal year 2026 (October 1, 2025 through September 30, 2026) and groups to MS-DRG 314 through 316. In AHRQ's Clinical Classifications Software (CCSR), this diagnosis falls under Benign neoplasms.
Code Identity
Code Classification
Approximate SynonymsGuidance
Alternate terms and clinical phrases that map to this code.
- Anastomosing hemangioma
- Arteriovenous hemangioma
- Atypical epithelioid hemangioma
- Benign glomus tumor
- Cavernous hemangioma
- Cavernous hemangioma of skin
- Cellular epithelioid hemangioma
- Compression of spinal cord due to cavernous hemangioma
- Congenital capillary hemangioma
- Congenital hemangioma
- Epithelioid hemangioma
- Giant infantile hemangioma
- Glomangioma
- Glomangiomatosis
- Glomangiomyoma
- Glomeruloid hemangioma
- Hemangioma
- Infantile hemangioma
- Infantile hemangioma of rare localization
- Intramuscular hemangioma
- Microvenular hemangioma
- Mixed hemangioma
- Myelopathy due to benign neoplastic disease
- Noninvoluting congenital hemangioma
- Partially involuting congenital hemangioma
- PHACE syndrome
- Rapidly involuting congenital hemangioma
- Reactive vascular proliferation of skin
- Segmental infantile hemangioma
- Sinusoidal hemangioma
- Spinal cord compression due to neoplasm
- Spindle cell hemangioma
- Tufted angioma
- Venous hemangioma
Index to Diseases and InjuriesGuidance
Alphabetical index entries that point to this code.
- Angioendothelioma - See: Neoplasm, uncertain behavior, by site;
- benign - D18.00
- Glomangioma - D18.00
- Glomangiomyoma - D18.00
- Hemangioendothelioma - See Also: Neoplasm, uncertain behavior, by site;
- benign - D18.00
- Hemangioma - D18.00
- arteriovenous - D18.00
- cavernous - D18.00
- epithelioid - D18.00
- histiocytoid - D18.00
- infantile - D18.00
- intramuscular - D18.00
- juvenile - D18.00
- plexiform - D18.00
- racemose - D18.00
- simplex - D18.00
- venous - D18.00
- verrucous keratotic - D18.00
- capillary - D18.00
- cavernous - D18.00
- hemangiomatous - D18.00
- meaning hemangioma - D18.00
External Cause of Injuries IndexGuidance
References for this code in the External Cause of Injuries Index.
- Angioendothelioma
- benign
- Angioma
- plexiform
- Cyst(colloid) (mucous) (simple) (retention)
- hemangiomatous
- Glomangioma
- Glomangiomyoma
- Hemangioendothelioma
- benign
- Hemangioma
- Hemangioma
- arteriovenous
- Hemangioma
- cavernous
- Hemangioma
- epithelioid
- Hemangioma
- histiocytoid
- Hemangioma
- infantile
- Hemangioma
- intramuscular
- Hemangioma
- juvenile
- Hemangioma
- plexiform
- Hemangioma
- racemose
- Hemangioma
- simplex
- Hemangioma
- venous
- Hemangioma
- verrucous keratotic
- Nevus
- capillary
- Nevus
- cavernous
- Nevus
- hemangiomatous
- Nevus
- meaning hemangioma
- Tumor
- glomus
Clinical ClassificationClinical
AHRQ’s CCSR groups this code into broader clinical categories.
Clinical InformationClinical
Branchio-Oto-Renal Syndrome
an autosomal dominant disorder manifested by various combinations of preauricular pits, branchial fistulae or cysts, lacrimal duct stenosis, hearing loss, structural defects of the outer, middle, or inner ear, and renal dysplasia. associated defects include asthenic habitus, long narrow facies, constricted palate, deep overbite, and myopia. hearing loss may be due to mondini type cochlear defect and stapes fixation. (jablonski's dictionary of syndromes & eponymic diseases, 2d ed)Enchondromatosis
benign growths of cartilage in the metaphyses of several bones.Granuloma, Pyogenic
a disorder of the skin, the oral mucosa, and the gingiva, that usually presents as a solitary polypoid capillary hemangioma often resulting from trauma. it is manifested as an inflammatory response with similar characteristics to those of a granuloma.Hemangioma
a vascular anomaly due to proliferation of blood vessels that forms a tumor-like mass. the common types involve capillaries and veins. it can occur anywhere in the body but is most frequently noticed in the skin and subcutaneous tissue. (from stedman, 27th ed, 2000)Hemangioma, Capillary
a dull red, firm, dome-shaped hemangioma, sharply demarcated from surrounding skin, usually located on the head and neck, which grows rapidly and generally undergoes regression and involution without scarring. it is caused by proliferation of immature capillary vessels in active stroma, and is usually present at birth or occurs within the first two or three months of life. (dorland, 27th ed)Hemangioma, Cavernous
a vascular anomaly that is a collection of tortuous blood vessels and connective tissue. this tumor-like mass with the large vascular space is filled with blood and usually appears as a strawberry-like lesion in the subcutaneous areas of the face, extremities, or other regions of the body including the central nervous system.Hemangioma, Cavernous, Central Nervous System
a vascular anomaly composed of a collection of large, thin walled tortuous veins that can occur in any part of the central nervous system but lack intervening nervous tissue. familial occurrence is common and has been associated with a number of genes mapped to 7q, 7p and 3q. clinical features include seizures; headache; stroke; and progressive neurological deficit.Histiocytoma, Benign Fibrous
a benign tumor composed, wholly or in part, of cells with the morphologic characteristics of histiocytes and with various fibroblastic components. fibrous histiocytomas can occur anywhere in the body. when they occur in the skin, they are called dermatofibromas or sclerosing hemangiomas. (from devita jr et al., cancer: principles & practice of oncology, 5th ed, p1747)Kasabach-Merritt Syndrome
rapidly growing vascular lesion along the midline axis of the neck, upper trunk, and extremities that is characterized by consumption coagulopathy; thrombocytopenia; and hemolytic anemia. it is often associated with infantile kaposiform hemangioendothelioma and other vascular tumors such as tufted angioma.Pulmonary Sclerosing Hemangioma
a benign neoplasm of pneumocytes, cells of the pulmonary alveoli. originally considered to be vascular in origin, it is now classified as an epithelial tumor with several elements, including solid cellular areas, papillary structure, sclerotic regions, and dilated blood-filled spaces resembling hemangioma.Sturge-Weber Syndrome
a non-inherited congenital condition with vascular and neurological abnormalities. it is characterized by facial vascular nevi (port-wine stain), and capillary angiomatosis of intracranial membranes (meninges; choroid). neurological features include epilepsy; cognitive deficits; glaucoma; and visual defects.Blood Vessels
any of the tubular vessels conveying the blood (arteries, arterioles, capillaries, venules, and veins).Histiocytes
macrophages found in the tissues, as opposed to those found in the blood (monocytes) or serous cavities (serous membrane).Sinusoidal Hemangioma
a rare hemangioma occurring mainly in middle-aged adults. the most common location is in the trunk. the lesions are small, asymptomatic, and bluish. they are composed of irregular, dilated, congested thin-walled vascular channels with scant smooth muscle in a sinusoidal or sieve-like pattern. (who 2018)Glomeruloid Hemangioma
a hemangioma associated with castleman disease and poems syndrome. the lesions affect the trunk and extremities and present as erythematous papules. (who 2018)Glomangiomatosis
a benign multifocal proliferation of glomus cells forming clusters around dilated vascular spaces.Anastomosing Hemangioma
an unusual variant of capillary hemangioma. it is characterized by a unique anastomosing sinusoidal-like architecture which may mimic angiosarcoma. it was originally described in the kidney but rare cases have been reported in other sites.Glomangiomyoma
a morphologic variant of the glomus tumor with architectural features similar to solid glomus tumor. it is characterized by the presence of elongated glomus cells which resemble mature smooth muscle.Microvenular Hemangioma
a rare hemangioma that affects the reticular dermis and consists of small vascular channels that resemble venules.Sinusoidal Hemangioma
a rare variant of cavernous hemangioma that manifests as a solitary, painless, bluish nodule in the reticular dermis or subcutaneous tissue. morphologically, it is characterized by the presence of irregular, dilated, interconnecting thin-walled vascular channels in a sinusoidal or sieve-like pattern.Glomeruloid Hemangioma
a rare cutaneous hemangioma that manifests with solitary or multiple blue-red papules that morphologically resemble renal glomeruli. it is located mainly on the trunk and proximal limbs and is associated with polyneuropathy, organomegaly, endocrinopathy, monoclonal gammopathy, and skin changes (poems) syndrome and castleman disease.
Patient EducationClinical
Benign Tumors
Tumors are abnormal growths in your body. They can be either benign or malignant. Benign tumors aren't cancer. Malignant ones are. Benign tumors grow only in one place. They cannot spread or invade other parts of your body. Even so, they can be dangerous if they press on vital organs, such as your brain.
Read the full article at MedlinePlus
Courtesy of MedlinePlus, a service of the U.S. National Library of Medicine.
Convert D18.00 to ICD-9-CMHistory
The closest ICD-9-CM equivalents under the General Equivalence Mappings.
Code HistoryHistory
Questions About D18.00Overview
Is D18.00 (Hemangioma) a billable code?
Yes. This is a billable ICD-10-CM code, specific enough to report hemangioma unspecified site on HIPAA-covered claims from October 1, 2025 through September 30, 2026.
What MS-DRG does D18.00 group to?
When hemangioma unspecified site is the principal diagnosis on an inpatient stay, it groups to MS-DRG 314, 315, 316, with relative weights from 0.6821 to 2.0852 depending on complications. Higher weights mean higher Medicare reimbursement.
What is the ICD-9 equivalent of D18.00?
Under the General Equivalence Mappings, hemangioma unspecified site converts to ICD-9-CM 228.00 (hemangioma NOS). The mapping is a direct match.
Footnotes
[1] Not chronic - A diagnosis code that does not fit the criteria for chronic condition (duration, ongoing medical treatment, and limitations) is considered not chronic. Some codes designated as not chronic are acute conditions. Other diagnosis codes that indicate a possible chronic condition, but for which the duration of the illness is not specified in the code description (i.e., we do not know the condition has lasted 12 months or longer) also are considered not chronic.
