ICD-10 Diagnosis Code Q82.4

Ectodermal dysplasia (anhidrotic)

Diagnosis Code Q82.4

ICD-10: Q82.4
Short Description: Ectodermal dysplasia (anhidrotic)
Long Description: Ectodermal dysplasia (anhidrotic)
This is the 2017 version of the ICD-10-CM diagnosis code Q82.4

Code Classification
  • Congenital malformations, deformations and chromosomal abnormalities
    • Other congenital malformations (Q80-Q89)
      • Other congenital malformations of skin (Q82)

Information for Medical Professionals

Diagnostic Related Groups
The diagnosis code Q82.4 is grouped in the following Diagnostic Related Group(s) (MS-DRG v33.0)


Convert to ICD-9 Additional informationCallout TooltipGeneral Equivalence Map
The ICD-10 and ICD-9 GEMs are used to facilitate linking between the diagnosis codes in ICD-9-CM and the new ICD-10-CM code set. The GEMs are the raw material from which providers, health information vendors and payers can derive specific applied mappings to meet their needs.
  • 757.31 - Cong ectodermal dysplas

Present on Admission (POA) Additional informationCallout TooltipPresent on Admission
The Present on Admission (POA) indicator is used for diagnosis codes included in claims involving inpatient admissions to general acute care hospitals. POA indicators must be reported to CMS on each claim to facilitate the grouping of diagnoses codes into the proper Diagnostic Related Groups (DRG). CMS publishes a listing of specific diagnosis codes that are exempt from the POA reporting requirement.

The code Q82.4 is exempt from POA reporting.

  • Acrorenal field defect, ectodermal dysplasia, and lipoatrophic diabetes
  • Alopecia, onychodysplasia, hypohidrosis, deafness ectodermal dysplasia
  • Anhidrotic ectodermal dysplasia with immune deficiency
  • Anonychia
  • Anonychia with bizarre flexural pigmentation
  • Autosomal dominant hypohidrotic ectodermal dysplasia syndrome
  • Basan syndrome
  • Berlin syndrome
  • Congenital ectodermal dysplasia of face
  • Cranioectodermal dysplasia
  • Curly hair, ankyloblepharon, nail dysplasia syndrome
  • Curry-Hall syndrome
  • Cutaneous syndrome with ichthyosis
  • Dento-oculocutaneous syndrome
  • Dermodental dysplasia
  • Ectodermal dysplasia
  • Ectodermal dysplasia with hair-nail defect
  • Ectodermal dysplasia with hair-tooth defects
  • Ectodermal dysplasia with hair-tooth-nail defects
  • Ectodermal dysplasia with hair-tooth-nail-sweating defect
  • Ectodermal dysplasia with nail defect
  • Ectodermal dysplasia with sweating defect
  • Ectodermal dysplasia with tooth-nail defects
  • Ectodermal dysplasia with tooth-nail-sweating defect
  • Ectodermal dysplasia with tooth-sweating defect
  • Ectodermal dysplasia, syndactyly and pili torti
  • Ectodermal dysplasia-ocular malformation syndrome
  • Ectodermal syndrome with hair-sweating defects
  • Ectodermal syndrome with hair-tooth-sweating defects
  • Excessive sweating
  • Familial focal facial dermal dysplasia
  • Fried's tooth and nail syndrome
  • Greither type of ectodermal dysplasia
  • Hay-Wells syndrome of ectodermal dysplasia
  • Hyperhidrosis, premature cavities and premolar aplasia
  • Hypohidrosis
  • Hypohidrosis
  • Hypohidrosis
  • Hypohidrosis-diabetes insipidus syndrome
  • Hypohidrotic X-linked ectodermal dysplasia
  • Johanson-Blizzard syndrome
  • Keratitis ichthyosis and deafness syndrome
  • Kirman syndrome
  • Laryngo-onychocutaneous syndrome
  • Marshall syndrome
  • Moynahan's syndrome
  • Odontomicronychial ectodermal dysplasia
  • Odonto-onychial dysplasia with alopecia
  • Odonto-onycho-dermal dysplasia
  • Robinson nail dystrophy-deafness syndrome
  • Roselli-Gulienetti ectodermal dysplasia
  • Salamon's syndrome
  • Sandman-Andra syndrome
  • Schinzel-Giedion syndrome
  • Schoepf-Schulz-Passage syndrome
  • Senter syndrome
  • Tricho-dento-osseous syndrome
  • Tricho-oculodermovertebral syndrome
  • Tricho-onychodental dysplasia

Index of Diseases and Injuries
References found for the code Q82.4 in the Index of Diseases and Injuries:

Information for Patients

Skin Conditions

Also called: Cutaneous disorders, Dermatologic disorders

Your skin is your body's largest organ. It covers and protects your body. Your skin

  • Holds body fluids in, preventing dehydration
  • Keeps harmful microbes out, preventing infections
  • Helps you feel things like heat, cold, and pain
  • Keeps your body temperature even
  • Makes vitamin D when the sun shines on it

Anything that irritates, clogs, or inflames your skin can cause symptoms such as redness, swelling, burning, and itching. Allergies, irritants, your genetic makeup, and certain diseases and immune system problems can cause rashes, hives, and other skin conditions. Many skin problems, such as acne, also affect your appearance.

NIH: National Institute of Arthritis and Musculoskeletal and Skin Diseases

  • Acrodermatitis
  • Cradle cap
  • Cryotherapy
  • Cutaneous skin tags
  • Dry skin -- self-care
  • Erythema multiforme
  • Granuloma annulare
  • Keratosis pilaris
  • Lichen planus
  • Milia
  • Sebaceous cyst
  • Seborrheic dermatitis
  • Seborrheic keratosis
  • Skin lesion removal
  • Skin lesion removal-aftercare
  • Stasis dermatitis and ulcers

[Read More]

Hypohidrotic ectodermal dysplasia Hypohidrotic ectodermal dysplasia is one of about 150 types of ectodermal dysplasia in humans. Before birth, these disorders result in the abnormal development of structures including the skin, hair, nails, teeth, and sweat glands.Most people with hypohidrotic ectodermal dysplasia have a reduced ability to sweat (hypohidrosis) because they have fewer sweat glands than normal or their sweat glands do not function properly. Sweating is a major way that the body controls its temperature; as sweat evaporates from the skin, it cools the body. An inability to sweat can lead to a dangerously high body temperature (hyperthermia), particularly in hot weather. In some cases, hyperthermia can cause life-threatening medical problems.Affected individuals tend to have sparse scalp and body hair (hypotrichosis). The hair is often light-colored, brittle, and slow-growing. This condition is also characterized by absent teeth (hypodontia) or teeth that are malformed. The teeth that are present are frequently small and pointed.Hypohidrotic ectodermal dysplasia is associated with distinctive facial features including a prominent forehead, thick lips, and a flattened bridge of the nose. Additional features of this condition include thin, wrinkled, and dark-colored skin around the eyes; chronic skin problems such as eczema; and a bad-smelling discharge from the nose (ozena).
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Anhidrotic ectodermal dysplasia with immune deficiency Anhidrotic ectodermal dysplasia with immune deficiency (EDA-ID) is a form of ectodermal dysplasia, which is a group of conditions characterized by abnormal development of ectodermal tissues including the skin, hair, teeth, and sweat glands. In addition, immune system function is reduced in people with EDA-ID. The signs and symptoms of EDA-ID are evident soon after birth.Skin abnormalities in people with EDA-ID include areas that are dry, wrinkled, or darker in color than the surrounding skin. Affected individuals tend to have sparse scalp and body hair (hypotrichosis). EDA-ID is also characterized by missing teeth (hypodontia) or teeth that are small and pointed. Most people with EDA-ID have a reduced ability to sweat (hypohidrosis) because they have fewer sweat glands than normal or their sweat glands do not function properly. An inability to sweat (anhidrosis) can lead to a dangerously high body temperature (hyperthermia), particularly in hot weather.The immune deficiency in EDA-ID varies among people with this condition. People with EDA-ID often produce abnormally low levels of proteins called antibodies or immunoglobulins. Antibodies help protect the body against infection by attaching to specific foreign particles and germs, marking them for destruction. A reduction in antibodies makes it difficult for people with this disorder to fight off infections. In EDA-ID, immune system cells called T cells and B cells have a decreased ability to recognize and respond to foreign invaders (such as bacteria, viruses, and yeast) that have sugar molecules attached to their surface (glycan antigens). Other key aspects of the immune system may also be impaired, leading to recurrent infections.People with EDA-ID commonly get infections in the lungs (pneumonia), ears (otitis media), sinuses (sinusitis), lymph nodes (lymphadenitis), skin, bones, and GI tract. Approximately one quarter of individuals with EDA-ID have disorders involving abnormal inflammation, such as inflammatory bowel disease or rheumatoid arthritis.The life expectancy of affected individuals depends of the severity of the immune deficiency; most people with this condition do not live past childhood.There are two forms of this condition that have similar signs and symptoms and are distinguished by the modes of inheritance: X-linked recessive or autosomal dominant.
[Read More]
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