2026 ICD-10-CM Diagnosis Code I28.0Arteriovenous fistula of pulmonary vessels

ICD-10-CM Codes›I00–I99›I26-I28›I28

ICD-10-CM I28.0
CMSSource: CMS FY 2026 ICD-10-CM dataset · Effective Oct 1, 2025 – Sep 30, 2026

I28.0 is a billable ICD-10-CM diagnosis code for arteriovenous fistula of pulmonary vessels. It is valid on HIPAA claims for fiscal year 2026 (October 1, 2025 through September 30, 2026) and groups to MS-DRG 314 through 316. In AHRQ's Clinical Classifications Software (CCSR), this diagnosis falls under Pulmonary heart disease.

Code Identity

ICD-10-CM Code
I28.0
Billable Status
Yes — Valid for Submission
Code Describes
Arteriovenous fistula of pulmonary vessels
Short Description
Arteriovenous fistula of pulmonary vessels
Same as the full description in the CMS dataset.
Parent Code
I28
Other diseases of pulmonary vessels

Code Classification

ChapterI00–I99Diseases of the circulatory system
SectionI26-I28Pulmonary heart disease and diseases of pulmonary circulation
CategoryI28Other diseases of pulmonary vessels
This CodeI28.0Arteriovenous fistula of pulmonary vessels

Approximate SynonymsGuidance

Alternate terms and clinical phrases that map to this code.

  • Arteriovenous fistula of pulmonary vessels
  • Arteriovenous fistula of pulmonary vessels following superior cavopulmonary anastomosis
  • Postoperative fistula
  • Pulmonary arteriovenous aneurysm
  • Pulmonary arteriovenous malformation
  • TEMPI syndrome

Tabular List NotesGuidance

Coding notes and annotation back-references applicable to this code.

Type 1 Excludes

  • congenital arteriovenous fistula Q25.72

Index to Diseases and InjuriesGuidance

Alphabetical index entries that point to this code.

External Cause of Injuries IndexGuidance

References for this code in the External Cause of Injuries Index.

    • Aneurysm(anastomotic) (artery) (cirsoid) (diffuse) (false) (fusiform) (multiple) (saccular)
      • arteriovenous (congenital)
        • acquired
          • pulmonary
    • Aneurysm(anastomotic) (artery) (cirsoid) (diffuse) (false) (fusiform) (multiple) (saccular)
      • pulmonary
        • arteriovenous
          • acquired
    • Fistula(cutaneous)
      • arteriovenous (acquired) (nonruptured)
        • pulmonary
    • Fistula(cutaneous)
      • pulmonary
        • arteriovenous
    • Shunt
      • arteriovenous, pulmonary (acquired)

Clinical ClassificationClinical

AHRQ’s CCSR groups this code into broader clinical categories.

CCSR CIR014
Pulmonary heart disease
Default principal diagnosis: inpatient Yes · outpatient Yes

Clinical InformationClinical

  • TEMPI Syndrome

    a rare syndrome characterized by telangiectasias, elevated erythropoietin level and erythrocytosis, monoclonal gammopathy, perinephric fluid collections, and intrapulmonary shunting. it is best classified as a type of plasma cell dyscrasia with paraneoplastic manifestations.

Patient EducationClinical

Fistulas

A fistula is an abnormal connection between two parts inside of the body. Fistulas may develop between different organs, such as between the esophagus and the windpipe or the bowel and the vagina. They can also develop between two blood vessels, such as between an artery and a vein or between two arteries.

Read the full article at MedlinePlus

Courtesy of MedlinePlus, a service of the U.S. National Library of Medicine.

Convert I28.0 to ICD-9-CMHistory

The closest ICD-9-CM equivalents under the General Equivalence Mappings.

ICD-9-CM
417.0 Arterioven fistu pul ves
Exact Match The mapping is direct, with no qualifiers.

Code HistoryHistory

FY 2016AddedAdded to the ICD-10-CM code setEffective October 1, 2015, the first year of ICD-10-CM.
FY 2017–2025No changes
FY 2026CurrentCurrent code set, no changesEffective October 1, 2025 through September 30, 2026.

Questions About I28.0Overview

Is I28.0 (Other diseases of pulmonary vessels) a billable code?

Yes. This is a billable ICD-10-CM code, specific enough to report arteriovenous fistula of pulmonary vessels on HIPAA-covered claims from October 1, 2025 through September 30, 2026.

What MS-DRG does I28.0 group to?

When arteriovenous fistula of pulmonary vessels is the principal diagnosis on an inpatient stay, it groups to MS-DRG 314, 315, 316, with relative weights from 0.6821 to 2.0852 depending on complications. Higher weights mean higher Medicare reimbursement.

What is the ICD-9 equivalent of I28.0?

Under the General Equivalence Mappings, arteriovenous fistula of pulmonary vessels converts to ICD-9-CM 417.0 (arterioven fistu pul ves). The mapping is a direct match.

Footnotes

[1] Chronic - a chronic condition code indicates a condition lasting 12 months or longer and its effect on the patient based on one or both of the following criteria:

  • The condition results in the need for ongoing intervention with medical products,treatment, services, and special equipment
  • The condition places limitations on self-care, independent living, and social interactions.