ICD-10 Diagnosis Code Q04.1


Diagnosis Code Q04.1

ICD-10: Q04.1
Short Description: Arhinencephaly
Long Description: Arhinencephaly
This is the 2017 version of the ICD-10-CM diagnosis code Q04.1

Code Classification
  • Congenital malformations, deformations and chromosomal abnormalities
    • Congenital malformations of the nervous system (Q00-Q07)
      • Other congenital malformations of brain (Q04)

Information for Patients

Brain Malformations

Also called: Cephalic disorders

Most brain malformations begin long before a baby is born. Something damages the developing nervous system or causes it to develop abnormally. Sometimes it's a genetic problem. In other cases, exposure to certain medicines, infections, or radiation during pregnancy interferes with brain development. Parts of the brain may be missing, abnormally small or large, or not fully developed.

Treatment depends upon the problem. In many cases, treatment only helps with symptoms. It may include antiseizure medicines, shunts to drain fluid from the brain, and physical therapy.

There are head malformations that do not involve the brain. Craniofacial disorders are the result of abnormal growth of soft tissue and bones in the face and head. It's common for new babies to have slightly uneven heads, but parents should watch the shape of their baby's head for possible problems.

NIH: National Institute of Neurological Disorders and Stroke

  • Brain surgery
  • Brain surgery - discharge

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Craniofacial Abnormalities

Craniofacial is a medical term that relates to the bones of the skull and face. Craniofacial abnormalities are birth defects of the face or head. Some, like cleft lip and palate, are among the most common of all birth defects. Others are very rare. Most of them affect how a person's face or head looks. These conditions may also affect other parts of the body.

Treatment depends on the type of problem. Plastic and reconstructive surgery may help the person's appearance.

  • Apert syndrome
  • Cleidocranial dysostosis
  • Craniosynostosis
  • Craniosynostosis repair
  • Head and face reconstruction
  • Pierre Robin syndrome

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