ICD-10 Diagnosis Code E80.5

Crigler-Najjar syndrome

Diagnosis Code E80.5

ICD-10: E80.5
Short Description: Crigler-Najjar syndrome
Long Description: Crigler-Najjar syndrome
This is the 2017 version of the ICD-10-CM diagnosis code E80.5

Valid for Submission
The code E80.5 is valid for submission for HIPAA-covered transactions.

Code Classification
  • Endocrine, nutritional and metabolic diseases (E00–E90)
    • Metabolic disorders (E70-E88)
      • Disorders of porphyrin and bilirubin metabolism (E80)

Information for Medical Professionals

Diagnostic Related Groups
The diagnosis code E80.5 is grouped in the following Diagnostic Related Group(s) (MS-DRG v33.0)

  • DISORDERS OF LIVER EXCEPT MALIGNANCY, CIRRHOSIS OR ALCOHOLIC HEPATITIS WITH MCC 441
  • DISORDERS OF LIVER EXCEPT MALIGNANCY, CIRRHOSIS OR ALCOHOLIC HEPATITIS WITH CC 442
  • DISORDERS OF LIVER EXCEPT MALIGNANCY, CIRRHOSIS OR ALCOHOLIC HEPATITIS WITHOUT CC/MCC 443

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The ICD-10 and ICD-9 GEMs are used to facilitate linking between the diagnosis codes in ICD-9-CM and the new ICD-10-CM code set. The GEMs are the raw material from which providers, health information vendors and payers can derive specific applied mappings to meet their needs.

Synonyms
  • Crigler-Najjar syndrome
  • Crigler-Najjar syndrome, type I
  • Crigler-Najjar syndrome, type II
  • Inherited disorder of bilirubin metabolism
  • Neonatal jaundice with Crigler-Najjar syndrome

Information for Patients


Liver Diseases

Also called: Hepatic disease

Your liver is the largest organ inside your body. It helps your body digest food, store energy, and remove poisons.

There are many kinds of liver diseases. Viruses cause some of them, like hepatitis A, hepatitis B, and hepatitis C. Others can be the result of drugs, poisons or drinking too much alcohol. If the liver forms scar tissue because of an illness, it's called cirrhosis. Jaundice, or yellowing of the skin, can be one sign of liver disease.

Cancer can affect the liver. You could also inherit a liver disease such as hemochromatosis.

Tests such as imaging tests and liver function tests can check for liver damage and help to diagnose liver diseases.

  • Alcoholic liver disease
  • ALP isoenzyme test
  • Ascites
  • Diet - liver disease
  • Fatty liver -- nonalcoholic
  • Hepatic encephalopathy
  • Hepatomegaly
  • Liver disease
  • Liver scan


[Read More]

Crigler-Najjar syndrome Crigler-Najjar syndrome is a severe condition characterized by high levels of a toxic substance called bilirubin in the blood (hyperbilirubinemia). Bilirubin is produced when red blood cells are broken down. This substance is removed from the body only after it undergoes a chemical reaction in the liver, which converts the toxic form of bilirubin (called unconjugated bilirubin) to a nontoxic form called conjugated bilirubin. People with Crigler-Najjar syndrome have a buildup of unconjugated bilirubin in their blood (unconjugated hyperbilirubinemia).Bilirubin has an orange-yellow tint, and hyperbilirubinemia causes yellowing of the skin and whites of the eyes (jaundice). In Crigler-Najjar syndrome, jaundice is apparent at birth or in infancy. Severe unconjugated hyperbilirubinemia can lead to a condition called kernicterus, which is a form of brain damage caused by the accumulation of unconjugated bilirubin in the brain and nerve tissues. Babies with kernicterus are often extremely tired (lethargic) and may have weak muscle tone (hypotonia). These babies may experience episodes of increased muscle tone (hypertonia) and arching of their backs. Kernicterus can lead to other neurological problems, including involuntary writhing movements of the body (choreoathetosis), hearing problems, or intellectual disability.Crigler-Najjar syndrome is divided into two types. Type 1 (CN1) is very severe, and affected individuals can die in childhood due to kernicterus, although with proper treatment, they may survive longer. Type 2 (CN2) is less severe. People with CN2 are less likely to develop kernicterus, and most affected individuals survive into adulthood.
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