2027 ICD-10-CM Diagnosis Code M33Dermatopolymyositis

ICD-10-CM Codes›M00–M99›M30-M36›M33

ICD-10-CM M33
CMSSource: CMS FY 2027 ICD-10-CM dataset · Effective Oct 1, 2026 – Sep 30, 2027

M33 is a non-billable ICD-10-CM category code for dermatopolymyositis, so it cannot be submitted on claims. Use a more specific code from this category instead, such as M33.00, M33.01, M33.02, and M33.03.

Code Identity

ICD-10-CM Code
M33
Billable Status
No — Non-Billable Category
Code Describes
Dermatopolymyositis
Short Description
Dermatopolymyositis
Same as the full description in the CMS dataset.
Chapter
M30-M36
Systemic connective tissue disorders

Code Classification

ChapterM00–M99Diseases of the musculoskeletal system and connective tissue
SectionM30-M36Systemic connective tissue disorders
CategoryM33Dermatopolymyositis
This CodeM33Dermatopolymyositis

Specific Coding for DermatopolymyositisOverview

Non-specific codes like M33 require more characters. Use one of these billable codes instead:

  • M33.0 for Juvenile dermatomyositis

  • Use M33.00 for Juvenile dermatomyositis, organ involvement unspecified

  • Use M33.01 for Juvenile dermatomyositis with respiratory involvement

  • Use M33.02 for Juvenile dermatomyositis with myopathy

  • Use M33.03 for Juvenile dermatomyositis without myopathy

  • Use M33.09 for Juvenile dermatomyositis with other organ involvement

  • M33.1 for Other dermatomyositis

  • Use M33.10 for Other dermatomyositis, organ involvement unspecified

  • Use M33.11 for Other dermatomyositis with respiratory involvement

  • Use M33.12 for Other dermatomyositis with myopathy

  • Use M33.13 for Other dermatomyositis without myopathy

  • Use M33.19 for Other dermatomyositis with other organ involvement

  • M33.2 for Polymyositis

  • Use M33.20 for Polymyositis, organ involvement unspecified

  • Use M33.21 for Polymyositis with respiratory involvement

  • Use M33.22 for Polymyositis with myopathy

  • Use M33.29 for Polymyositis with other organ involvement

  • M33.9 for Dermatopolymyositis, unspecified

  • Use M33.90 for Dermatopolymyositis, unspecified, organ involvement unspecified

  • Use M33.91 for Dermatopolymyositis, unspecified with respiratory involvement

  • Use M33.92 for Dermatopolymyositis, unspecified with myopathy

  • Use M33.93 for Dermatopolymyositis, unspecified without myopathy

  • Use M33.99 for Dermatopolymyositis, unspecified with other organ involvement

Instructional NotesGuidance

Instructions from the official ICD-10-CM Tabular List that apply to M33: its own notes plus those printed at block M30-M36 and Chapter 13. A note printed at a category, block or chapter applies to every code under it.

Includes

Further defines, or gives examples of, the content of the category.

From Block M30-M36 Systemic connective tissue disorders applies to 84 codes
  • autoimmune disease NOS
  • collagen (vascular) disease NOS
  • systemic autoimmune disease
  • systemic collagen (vascular) disease

Excludes1

Not coded here: the excluded code is never reported together with this one, unless the two conditions are unrelated.

From Block M30-M36 Systemic connective tissue disorders applies to 84 codes
  • autoimmune disease, single organ or single cell-type -code to relevant condition category

Excludes2

Not included here: the excluded condition is not part of this code, but a patient may have both, so both codes may be reported.

From Chapter 13 (M00-M99) Diseases of the musculoskeletal system and connective tissue applies to 6,687 codes
  • arthropathic psoriasis (L40.5-)
  • certain conditions originating in the perinatal period (P04-P96)
  • certain infectious and parasitic diseases (A00-B99)
  • compartment syndrome (traumatic) (T79.A-)
  • complications of pregnancy, childbirth and the puerperium (O00-O9A)
  • congenital malformations, deformations, and chromosomal abnormalities (Q00-Q99)
  • endocrine, nutritional and metabolic diseases (E00-E88)
  • injury, poisoning and certain other consequences of external causes (S00-T88)
  • neoplasms (C00-D49)
  • symptoms, signs and abnormal clinical and laboratory findings, not elsewhere classified (R00-R94)

Notes

General instructions on how these codes are used.

From Chapter 13 (M00-M99) Diseases of the musculoskeletal system and connective tissue applies to 6,687 codes
  • Use an external cause code following the code for the musculoskeletal condition, if applicable, to identify the cause of the musculoskeletal condition

Source: CMS ICD-10-CM Tabular List. How to read instructional notes.

Referenced in Other NotesGuidance

Instructional notes printed at other codes that name M33, its category, or a range that includes it.

Excludes1 3

These codes carry an Excludes1 note naming M33: they are not reported together with it, unless the two conditions are unrelated.

  • G72 Other and unspecified myopathies
    dermatopolymyositis (M33.-)
  • Block M60-M63 Disorders of muscles
    dermatopolymyositis (M33.-)
  • L94 Other localized connective tissue disorders
    systemic connective tissue disorders (M30-M36) names M30-M36, which includes this code

Excludes2 4

These codes carry an Excludes2 note naming M33: its condition is not part of those codes, and both may be reported when the patient has both.

  • Chapter 9 (I00-I99) Diseases of the circulatory system
    systemic connective tissue disorders (M30-M36) names M30-M36, which includes this code
  • I77 Other disorders of arteries and arterioles
    collagen (vascular) diseases (M30-M36) names M30-M36, which includes this code
  • J82 Pulmonary eosinophilia, not elsewhere classified
    pulmonary eosinophilia due to systemic connective tissue disorders (M30-M36) names M30-M36, which includes this code
  • Chapter 12 (L00-L99) Diseases of the skin and subcutaneous tissue
    systemic connective tissue disorders (M30-M36) names M30-M36, which includes this code

Code First 1

These codes say to code first a condition named in the note, and M33 is one of the conditions named.

  • J84.170 Interstitial lung disease with progressive fibrotic phenotype in diseases classified elsewhere
    systemic connective tissue disorders (M30-M36) names M30-M36, which includes this code

Clinical InformationClinical

  • Dermatomyositis

    a subacute or chronic inflammatory disease of muscle and skin, marked by proximal muscle weakness and a characteristic skin rash. the illness occurs with approximately equal frequency in children and adults. the skin lesions usually take the form of a purplish rash (or less often an exfoliative dermatitis) involving the nose, cheeks, forehead, upper trunk, and arms. the disease is associated with a complement mediated intramuscular microangiopathy, leading to loss of capillaries, muscle ischemia, muscle-fiber necrosis, and perifascicular atrophy. the childhood form of this disease tends to evolve into a systemic vasculitis. dermatomyositis may occur in association with malignant neoplasms. (from adams et al., principles of neurology, 6th ed, pp1405-6)

Patient EducationClinical

Myositis

Myositis means inflammation of the muscles that you use to move your body. An injury, infection, or autoimmune disease can cause it. Two specific kinds are polymyositis and dermatomyositis. Polymyositis causes muscle weakness, usually in the muscles closest to the trunk of your body.

Read the full article at MedlinePlus

Courtesy of MedlinePlus, a service of the U.S. National Library of Medicine.

Code HistoryHistory

FY 2016AddedAdded to the ICD-10-CM code setEffective October 1, 2015, the first year of ICD-10-CM.
FY 2017–2026No changes
FY 2027CurrentCurrent code set, no changesEffective October 1, 2026 through September 30, 2027.

Questions About M33Overview

What is the ICD-10 code for dermatopolymyositis?

M33 is the ICD-10-CM category for dermatopolymyositis, but it is a non-billable header: claims need a more specific code from this category, listed on this page.

Is M33 (Dermatopolymyositis) a billable code?

No. This is a category header that groups the codes for dermatopolymyositis, and headers cannot be submitted on claims. Claims for dermatopolymyositis need a more specific code from this category, such as M33.00, M33.01, and M33.02.