2026 ICD-10-CM Diagnosis Code I77.6Arteritis, unspecified

AHRQ’s CCSR groups this code into broader clinical categories.

• Arteritis

  inflammation of any arteries.

• Equartevirus

  a genus of the family arteriviridae.

• Giant Cell Arteritis

  a systemic autoimmune disorder that typically affects medium and large arteries, usually leading to occlusive granulomatous vasculitis with transmural infiltrate containing multinucleated giant cells. the temporal artery is commonly involved. this disorder appears primarily in people over the age of 50. symptoms include fever; fatigue; headache; visual impairment; pain in the jaw and tongue; and aggravation of pain by cold temperatures. (from adams et al., principles of neurology, 6th ed)

• Polyarteritis Nodosa

  a form of necrotizing non-granulomatous inflammation occurring primarily in medium-sized arteries, often with microaneurysms. it is characterized by muscle, joint, and abdominal pain resulting from arterial infarction and scarring in affected organs. polyarteritis nodosa with lung involvement is called churg-strauss syndrome.

• Takayasu Arteritis

  a chronic inflammatory process that affects the aorta and its primary branches, such as the brachiocephalic artery (brachiocephalic trunk) and carotid arteries. it results in progressive arterial stenosis, occlusion, and aneurysm formation. the pulse in the arm is hard to detect. patients with aortitis syndrome often exhibit retinopathy.

• Vasculitis, Central Nervous System

  inflammation of blood vessels within the central nervous system. primary vasculitis is usually caused by autoimmune or idiopathic factors, while secondary vasculitis is caused by existing disease process. clinical manifestations are highly variable but include headache; seizures; behavioral alterations; intracranial hemorrhages; transient ischemic attack; and brain infarction. (from adams et al., principles of neurology, 6th ed, pp856-61)

• AIDS Arteritis, Central Nervous System

  inflammation of arteries in the central nervous system that occurs in patients with acquired immunodeficiency syndrome or aids-related opportunistic infections.

• Anti-Neutrophil Cytoplasmic Antibody-Associated Vasculitis

  group of systemic vasculitis with a strong association with anca. the disorders are characterized by necrotizing inflammation of small and medium size vessels, with little or no immune-complex deposits in vessel walls.

• Churg-Strauss Syndrome

  widespread necrotizing angiitis with granulomas. pulmonary involvement is frequent. asthma or other respiratory infection may precede evidence of vasculitis. eosinophilia and lung involvement differentiate this disease from polyarteritis nodosa.

• IgA Vasculitis

  a systemic non-thrombocytopenic purpura caused by hypersensitivity vasculitis and deposition of iga-containing immune complexes within the blood vessels throughout the body, including those in the kidney (kidney glomerulus). clinical symptoms include urticaria; erythema; arthritis; gastrointestinal hemorrhage; and renal involvement. most cases are seen in children after acute upper respiratory infections.

• Livedoid Vasculopathy

  a rare cutaneous thrombotic disease due to occlusion of dermal vessels. it is characterized by purpuric maculae and ulcerations especially during summer which form scars called atrophie blanche. it is more associated with other syndromes (e.g., protein c deficiency; hyperhomocysteinemia). livedo reticularis with systemic involvement and stroke is sneddon syndrome.

• Retinal Vasculitis

  inflammation of the retinal vasculature with various causes including infectious disease; lupus erythematosus, systemic; multiple sclerosis; behcet syndrome; and chorioretinitis.

• Rheumatoid Vasculitis

  necrotizing vasculitis of small and medium size vessels, developing as a complication in rheumatoid arthritis patients. it is characterized by peripheral vascular lesions, cutaneous ulcers, peripheral gangrene, and mononeuritis multiplex.

• Skin Diseases, Vascular

  skin diseases affecting or involving the cutaneous blood vessels and generally manifested as inflammation, swelling, erythema, or necrosis in the affected area.

• Systemic Vasculitis

  a heterogeneous group of diseases characterized by inflammation and necrosis of the blood vessel walls.

• Vasculitis

  inflammation of any one of the blood vessels, including the arteries; veins; and rest of the vasculature system in the body.

• Vasculitis, Leukocytoclastic, Cutaneous

  disorder characterized by a vasculitic syndrome associated with exposure to an antigen such as a drug, infectious agent, or other foreign or endogenous substance. its pathophysiology includes immune complex deposition and a wide range of skin lesions. hypersensitivity or allergy is present in some but not all cases.

• Endarteritis

  inflammation of the inner endothelial lining (tunica intima) of an artery.

• Aortitis

  inflammation of the wall of the aorta.

• Syphilis, Cardiovascular

  cardiovascular manifestations of syphilis, an infection of treponema pallidum. in the late stage of syphilis, sometimes 20-30 years after the initial infection, damages are often seen in the blood vessels including the aorta and the aortic valve. clinical signs include syphilitic aortitis, aortic insufficiency, or aortic aneurysm.

• Tunica Intima

  the innermost layer of an artery or vein, made up of one layer of endothelial cells and supported by an internal elastic lamina.

• Aorta

  the main trunk of the systemic arteries.

• Arteriviridae

  a family of viruses, of the order nidovirales, containing spherical virions. in contrast to coronaviridae, no protruding spikes are obvious on the surface.

• Antineutrophil Cytoplasmic Antibody-Associated Vasculitis|AAV|ANCA-Associated Vasculitis|Antineutrophil Cytoplasmic Autoantibody-Associated Vasculitis|Antineutrophilic Cytoplasmic Antibody-Associated Vasculitis

  a group of rare autoimmune disorders characterized by small-to-medium vessel vasculitis and the presence of anti-neutrophil cytoplasmic autoantibodies (anca). some cases may be associated with infection or the use of certain medications.

• Mononeuritis Multiplex

  a painful asymmetric asynchronous sensory and motor peripheral neuropathy involving isolated damage to at least 2 separate nerve areas; associated with (but not limited to) systemic disorders such as diabetes, vasculitis, amyloidosis, direct tumor involvement, polyarteritis nodosa, rheumatoid arthritis, systemic lupus erythematosus, and paraneoplastic syndromes. it also may be associated with lyme disease, wegener's granulomatosis, sjogren syndrome, cryoglobulinemia, hypereosinophilia, temporal arteritis, scleroderma, sarcoidosis, leprosy, acute viral hepatitis a, and acquired immunodeficiency syndrome.

• Birmingham Vasculitis Activity Score|BVAS|BVAS

  a set of criteria used to determine the activity of vasculitis.

• Central Nervous System Vasculitis

  vasculitis affecting the blood vessels of the brain and/or spinal cord.

• Chronic Uteroplacental Vasculitis

  a lymphocytic inflammation of the uteroplacental vessels.

• Cutaneous Small Vessel Vasculitis|Cutaneous Leukocytoclastic Vasculitis|Cutaneous Small-Vessel Vasculitis

  a skin hypersensitivity reaction characterized by raised purpuric lesions, red macules, hemorrhagic blisters and ulcerations.

• Cutaneous Vasculitis

  inflammation of the blood vessel wall characterized by palpable purpura.

• Drug Induced Cutaneous Vasculitis|Drug Induced Vasculitis|Drug Induced Vasculitis

  a skin hypersensitivity reaction due to exposure to a pharmacologic substance that is characterized by raised purpuric lesions, red macules, hemorrhagic blisters and ulcerations.

• Fetal Chorionic Vasculitis|Acute Chorionic Vasculitis|Acute Chorionic Vasculitis

  a neutrophilic infiltrate arising from fetal vessels in the chorionic plate and oriented towards the amniotic cavity.

• Grade 1 Vasculitis, CTCAE|Grade 1 Vasculitis|Grade 1 Vasculitis

  asymptomatic, intervention not indicated

• Grade 2 Vasculitis, CTCAE|Grade 2 Vasculitis|Grade 2 Vasculitis

  moderate symptoms, medical intervention indicated

• Grade 3 Vasculitis, CTCAE|Grade 3 Vasculitis|Grade 3 Vasculitis

  severe symptoms, medical intervention indicated (e.g., steroids)

• Grade 4 Vasculitis, CTCAE|Grade 4 Vasculitis|Grade 4 Vasculitis

  life-threatening consequences; evidence of peripheral or visceral ischemia; urgent intervention indicated

• Grade 5 Vasculitis, CTCAE|Grade 5 Vasculitis|Grade 5 Vasculitis

  death

• Leukocytoclastic Vasculitis|Hypersensitivity Vasculitis|Hypersensitivity angiitis

  a small vessel vasculitis affecting the skin and/or internal organs. it is characterized by the presence of neutrophils and fibrinoid necrosis in small arteries and venules. it may be idiopathic or the result of drug treatment, infections, food intake, collagen vascular disorders, inflammatory bowel disease, or cancer.

• Necrotizing Vasculitis

  a rare condition that involves inflammation and necrosis of the walls of the blood vessels; may occur in rheumatoid arthritis.

• Pediatric Vasculitis Activity Score|PVAS|PVAS

  a set of criteria used to determine the activity of childhood vasculitis.

• Placental Villous Stromal-Vascular Karyorrhexis|Hemorrhagic Placental Endovasculitis|Hemorrhagic Placental Endovasculitis

  three or more foci of two or more placental terminal villi showing karyorrhexis of fetal cells with preservation of the surrounding trophoblast. the villi may also show stromal hypercellularity and mineralization, and can either be hypovascular or only exhibit capillary degenerative changes. entrapped red blood cells and red blood cell fragments are often seen.

• Pseudomonas-Related Vasculitis

  a necrotizing vasculitis caused by pseudomonas aeruginosa.

• Rheumatoid Vasculitis with Rheumatoid Arthritis of Left Ankle and Foot|Rheumatoid vasculitis with rheumatoid arthritis of left ankle and foot

  evidence of rheumatoid vasculitis with rheumatoid arthritis of left ankle and foot.

• Rheumatoid Vasculitis with Rheumatoid Arthritis of Left Elbow|Rheumatoid vasculitis with rheumatoid arthritis of left elbow

  evidence of rheumatoid vasculitis with rheumatoid arthritis of left elbow.

• Rheumatoid Vasculitis with Rheumatoid Arthritis of Left Hand|Rheumatoid vasculitis with rheumatoid arthritis of left hand

  evidence of rheumatoid vasculitis with rheumatoid arthritis of left hand.

• Rheumatoid Vasculitis with Rheumatoid Arthritis of Left Hip|Rheumatoid vasculitis with rheumatoid arthritis of left hip

  evidence of rheumatoid vasculitis with rheumatoid arthritis of left hip.

• Rheumatoid Vasculitis with Rheumatoid Arthritis of Left Knee|Rheumatoid vasculitis with rheumatoid arthritis of left knee

  evidence of rheumatoid vasculitis with rheumatoid arthritis of left knee.

• Rheumatoid Vasculitis with Rheumatoid Arthritis of Left Shoulder|Rheumatoid vasculitis with rheumatoid arthritis of left shoulder

  evidence of rheumatoid vasculitis with rheumatoid arthritis of left shoulder.

• Rheumatoid Vasculitis with Rheumatoid Arthritis of Left Wrist|Rheumatoid vasculitis with rheumatoid arthritis of left wrist

  evidence of rheumatoid vasculitis with rheumatoid arthritis of left wrist.

• Rheumatoid Vasculitis with Rheumatoid Arthritis of Multiple Sites|Rheumatoid vasculitis with rheumatoid arthritis of multiple sites

  evidence of rheumatoid vasculitis with rheumatoid arthritis of multiple sites.

• Rheumatoid Vasculitis with Rheumatoid Arthritis of Right Ankle and Foot|Rheumatoid vasculitis with rheumatoid arthritis of right ankle and foot

  evidence of rheumatoid vasculitis with rheumatoid arthritis of right ankle and foot.

• Rheumatoid Vasculitis with Rheumatoid Arthritis of Right Elbow|Rheumatoid vasculitis with rheumatoid arthritis of right elbow

  evidence of rheumatoid vasculitis with rheumatoid arthritis of right elbow.

• Rheumatoid Vasculitis with Rheumatoid Arthritis of Right Hand|Rheumatoid vasculitis with rheumatoid arthritis of right hand

  evidence of rheumatoid vasculitis with rheumatoid arthritis of right hand.

• Rheumatoid Vasculitis with Rheumatoid Arthritis of Right Hip|Rheumatoid vasculitis with rheumatoid arthritis of right hip

  evidence of rheumatoid vasculitis with rheumatoid arthritis of right hip.

• Rheumatoid Vasculitis with Rheumatoid Arthritis of Right Knee|Rheumatoid vasculitis with rheumatoid arthritis of right knee

  evidence of rheumatoid vasculitis with rheumatoid arthritis of right knee.

• Rheumatoid Vasculitis with Rheumatoid Arthritis of Right Shoulder|Rheumatoid vasculitis with rheumatoid arthritis of right shoulder

  evidence of rheumatoid vasculitis with rheumatoid arthritis of right shoulder.

• Rheumatoid Vasculitis with Rheumatoid Arthritis of Right Wrist|Rheumatoid vasculitis with rheumatoid arthritis of right wrist

  evidence of rheumatoid vasculitis with rheumatoid arthritis of right wrist.

• Rheumatoid Vasculitis with Rheumatoid Arthritis of Unspecified Ankle and Foot|Rheumatoid vasculitis with rheumatoid arthritis of unspecified ankle and foot

  evidence of rheumatoid vasculitis with rheumatoid arthritis of unspecified ankle and foot.

• Rheumatoid Vasculitis with Rheumatoid Arthritis of Unspecified Elbow|Rheumatoid vasculitis with rheumatoid arthritis of unspecified elbow

  evidence of rheumatoid vasculitis with rheumatoid arthritis of unspecified elbow.

• Rheumatoid Vasculitis with Rheumatoid Arthritis of Unspecified Hand|Rheumatoid vasculitis with rheumatoid arthritis of unspecified hand

  evidence of rheumatoid vasculitis with rheumatoid arthritis of unspecified hand.

• Rheumatoid Vasculitis with Rheumatoid Arthritis of Unspecified Hip|Rheumatoid vasculitis with rheumatoid arthritis of unspecified hip

  evidence of rheumatoid vasculitis with rheumatoid arthritis of unspecified hip.

• Rheumatoid Vasculitis with Rheumatoid Arthritis of Unspecified Knee|Rheumatoid vasculitis with rheumatoid arthritis of unspecified knee

  evidence of rheumatoid vasculitis with rheumatoid arthritis of unspecified knee.

• Rheumatoid Vasculitis with Rheumatoid Arthritis of Unspecified Shoulder|Rheumatoid vasculitis with rheumatoid arthritis of unspecified shoulder

  evidence of rheumatoid vasculitis with rheumatoid arthritis of unspecified shoulder.

• Rheumatoid Vasculitis with Rheumatoid Arthritis of Unspecified Site|Rheumatoid vasculitis with rheumatoid arthritis of unspecified site

  evidence of rheumatoid vasculitis with rheumatoid arthritis of unspecified site.

• Rheumatoid Vasculitis with Rheumatoid Arthritis of Unspecified Wrist|Rheumatoid vasculitis with rheumatoid arthritis of unspecified wrist

  evidence of rheumatoid vasculitis with rheumatoid arthritis of unspecified wrist.

• Umbilical Vasculitis|Acute Umbilical Vasculitis|Acute Umbilical Vasculitis

  a neutrophilic infiltrate arising from fetal vessels of the umbilical cord into the umbilical vessel wall and oriented towards the amniotic cavity.

• Vasculitis

  an inflammatory process involving the wall of the vessels (large, medium, or small-sized vessels). the inflammatory process may cause necrosis or formation of granulomas in the vascular wall. it may be the result of an autoimmune disorder, infection, or malignancy. representative examples include polyarteritis nodosa, temporal arteritis, wegener granulomatosis, kawasaki disease, takayasu arteritis, and henoch-schonlein purpura.

• Vasculitis, CTCAE|Vasculitis|Vasculitis|Vasculitis

  a disorder characterized by inflammation involving the wall of a vessel.

• Endarteritis

  inflammation of the arterial intima.

• Aortitis

  inflammation of the aorta. causes include trauma, infectious disorders, and connective tissue disorders.

• Aortitis in Diseases Classified Elsewhere|Aortitis in diseases classified elsewhere

  evidence of aortitis in diseases classified elsewhere.

• Syphilitic Aortitis|Syphilitic aortitis

  aortitis secondary to syphilis.

Vasculitis

Vasculitis is an inflammation of the blood vessels. It happens when the body's immune system attacks the blood vessel by mistake. It can happen because of an infection, a medicine, or another disease. The cause is often unknown.

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