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  6. 2026 ICD-10-CM Code I27.2

2026 ICD-10-CM Diagnosis Code I27.2

Other secondary pulmonary hypertension

ICD-10-CM Code:
I27.2
ICD-10 Code for:
Other secondary pulmonary hypertension
Is Billable?
Not Valid for Submission
Chronic Condition Indicator: [1]
Chronic
Code Navigator:

I27.2 is a non-specific and non-billable diagnosis code code, consider using a code with a higher level of specificity for a diagnosis of other secondary pulmonary hypertension. The code is not specific and is NOT valid for the year 2026 for the submission of HIPAA-covered transactions. Category or Header define the heading of a category of codes that may be further subdivided by the use of 4th, 5th, 6th or 7th characters.

The code is commonly used in cardiology medical specialties to specify clinical concepts such as hypertension.

Specific Coding Applicable to Other secondary pulmonary hypertension

Non-specific codes like I27.2 require more digits to indicate the appropriate level of specificity. Consider using any of the following ICD-10-CM codes with a higher level of specificity when coding for other secondary pulmonary hypertension:

  • Use I27.20 for Pulmonary hypertension, unspecified - BILLABLE CODE

  • Use I27.21 for Secondary pulmonary arterial hypertension - BILLABLE CODE

  • Use I27.22 for Pulmonary hypertension due to left heart disease - BILLABLE CODE

  • Use I27.23 for Pulmonary hypertension due to lung diseases and hypoxia - BILLABLE CODE

  • Use I27.24 for Chronic thromboembolic pulmonary hypertension - BILLABLE CODE

  • Use I27.29 for Other secondary pulmonary hypertension - BILLABLE CODE

Code Classification

  • Diseases of the circulatory system
    I00–I99
    • Pulmonary heart disease and diseases of pulmonary circulation
      I26-I28
      • Other pulmonary heart diseases
        I27

Clinical Classification

Clinical Classifications group individual ICD-10-CM diagnosis codes into broader, clinically meaningful categories. These categories help simplify complex data by organizing related conditions under common clinical themes.

They are especially useful for data analysis, reporting, and clinical decision-making. Even when diagnosis codes differ, similar conditions can be grouped together based on their clinical relevance. Each category is assigned a unique CCSR code that represents a specific clinical concept, often tied to a body system or medical specialty.

Pulmonary heart disease

CCSR Code: CIR014

Inpatient Default: Y - Yes, default inpatient assignment for principal diagnosis or first-listed diagnosis.

Outpatient Default: Y - Yes, default outpatient assignment for principal diagnosis or first-listed diagnosis.

Tabular List of Diseases and Injuries

The following annotation back-references are applicable to this diagnosis code. The Tabular List of Diseases and Injuries is a list of ICD-10-CM codes, organized "head to toe" into chapters and sections with coding notes and guidance for inclusions, exclusions, descriptions and more.


Code Also

Code Also
A "code also" note instructs that two codes may be required to fully describe a condition, but this note does not provide sequencing direction.
  • associated underlying condition

Type 1 Excludes

Type 1 Excludes
A type 1 excludes note is a pure excludes note. It means "NOT CODED HERE!" An Excludes1 note indicates that the code excluded should never be used at the same time as the code above the Excludes1 note. An Excludes1 is used when two conditions cannot occur together, such as a congenital form versus an acquired form of the same condition.
  • Eisenmenger's syndrome I27.83

Patient Education


Pulmonary Hypertension

What is pulmonary hypertension?

Pulmonary hypertension, sometimes called PH, is a serious condition that affects the blood vessels in the lungs. It develops when the blood pressure in your lungs is higher than normal.

Your heart pumps blood to your lungs so they can add oxygen to the blood. The blood goes back to your heart. From there, it travels to the rest of your body so that your tissues can get the oxygen that they need.

The blood moves from your heart to your lungs through blood vessels called pulmonary arteries. If the pulmonary arteries become damaged, narrowed, or blocked, the blood does not flow through them as well. This can increase the blood pressure in the arteries and cause pulmonary hypertension.

There are different types of pulmonary hypertension, including pulmonary arterial hypertension (PAH). The different types are based on what caused the disease.

What causes pulmonary hypertension?

Pulmonary hypertension can develop on its own or be caused by another condition. Sometimes the cause is unknown or is not clear.

Some of the possible causes include:

  • Heart diseases, including left-sided heart failure and congenital heart disease
  • Lung diseases such as COPD (chronic obstructive pulmonary disease), interstitial lung disease, emphysema, and sleep apnea
  • Other medical conditions such as:
    • Liver diseases
    • Sickle cell disease
    • Pulmonary embolism (blood clots in the lungs)
    • Connective tissue disorders like scleroderma

Who is more likely to develop pulmonary hypertension?

Certain factors can make you more likely to develop pulmonary hypertension, such as:

  • Your age. The risk increases as you get older. The condition is usually diagnosed between ages 30 and 60.
  • Your environment. Being exposed to asbestos or having certain infections caused by parasites can raise your risk.
  • Your family history and genetics. Certain genetic disorders, such as Down syndrome, congenital heart disease, and Gaucher disease, can raise your risk of pulmonary hypertension. So can a family history of blood clots.
  • Your lifestyle habits. Smoking and illegal drug use can raise your risk of developing pulmonary hypertension.
  • Certain medicines. For example, some medicines used to treat cancer and depression can make you more likely to develop pulmonary hypertension.
  • Your sex. Pulmonary hypertension is more common in women than in men.

What are the symptoms of pulmonary hypertension?

The symptoms of pulmonary hypertension are sometimes hard to recognize and are similar to the symptoms of other medical conditions. So sometimes it can take years for someone to get diagnosed with pulmonary hypertension.

The symptoms of pulmonary hypertension may include:

  • Shortness of breath
  • Chest pain or pressure
  • Dizziness that may lead to fainting
  • Fatigue
  • Swelling of the abdomen, legs, or feet
  • Heart palpitations (the feeling that your heart is pounding or beating too fast)

What other problems can pulmonary hypertension cause?

Pulmonary hypertension can get worse over time and lead to serious problems, including:

  • Anemia, which can cause your body to not get enough oxygen-rich blood
  • Arrhythmias, problems with the rate or rhythm of your heartbeat
  • Blood clots in the pulmonary arteries
  • Bleeding in the lungs
  • Heart failure
  • Liver damage
  • Pericardial effusion, a collection of fluid around the heart
  • Serious pregnancy complications

How is pulmonary hypertension diagnosed?

To find out if you have pulmonary hypertension, your health care provider:

  • Will ask about your medical history and symptoms
  • Will do a physical exam, which may include checking your blood oxygen, listening to your heart and lungs, and checking your blood pressure
  • Will likely order some tests, such as:
    • Blood tests to look for blood clots, stress on the heart, or anemia
    • Heart imaging tests, such as a cardiac MRI
    • Lung imaging tests, such as chest x-ray
    • An electrocardiogram (ECG or EKG)

What are the treatments for pulmonary hypertension?

Often there is no cure for pulmonary hypertension, but treatments can help manage your symptoms. Your provider will work with you to come up with a treatment plan. It will be based on your needs and the cause of the pulmonary hypertension. The plan may include:

  • Healthy lifestyle changes, such as:
    • Healthy eating, which includes eating less salt
    • Regular physical activity, which may be done through pulmonary rehabilitation
  • Medicines, such as:
    • Blood thinners
    • Medicines to control the rate blood is pumped throughout the body
    • Medicines to relax blood vessels and allow the blood to flow better
    • Medicine to reduce swelling (diuretics)
  • Oxygen therapy
  • Procedures to reduce pressure in the heart or pulmonary artery
  • In some severe cases, a lung transplant

NIH: National Heart, Lung, and Blood Institute


[Learn More in MedlinePlus]

Code History

  • FY 2026 - No Change, effective from 10/1/2025 through 9/30/2026
  • FY 2025 - No Change, effective from 10/1/2024 through 9/30/2025
  • FY 2024 - No Change, effective from 10/1/2023 through 9/30/2024
  • FY 2023 - No Change, effective from 10/1/2022 through 9/30/2023
  • FY 2022 - No Change, effective from 10/1/2021 through 9/30/2022
  • FY 2021 - No Change, effective from 10/1/2020 through 9/30/2021
  • FY 2020 - No Change, effective from 10/1/2019 through 9/30/2020
  • FY 2019 - No Change, effective from 10/1/2018 through 9/30/2019
  • FY 2018 - No Change, effective from 10/1/2017 through 9/30/2018
  • FY 2017 - No Change, effective from 10/1/2016 through 9/30/2017
  • FY 2016 - New Code, effective from 10/1/2015 through 9/30/2016. This was the first year ICD-10-CM was implemented into the HIPAA code set.

Footnotes

[1] Chronic - a chronic condition code indicates a condition lasting 12 months or longer and its effect on the patient based on one or both of the following criteria:

  • The condition results in the need for ongoing intervention with medical products,treatment, services, and special equipment
  • The condition places limitations on self-care, independent living, and social interactions.