ICD-10 Diagnosis Code I27.0

Primary pulmonary hypertension

Diagnosis Code I27.0

ICD-10: I27.0
Short Description: Primary pulmonary hypertension
Long Description: Primary pulmonary hypertension
This is the 2018 version of the ICD-10-CM diagnosis code I27.0

Valid for Submission
The code I27.0 is valid for submission for HIPAA-covered transactions.

Code Classification
  • Diseases of the circulatory system (I00–I99)
    • Pulmonary heart disease and diseases of pulmonary circulation (I26-I28)
      • Other pulmonary heart diseases (I27)

Information for Medical Professionals

Diagnostic Related Groups
The diagnosis code I27.0 is grouped in the following Diagnostic Related Group(s) (MS-DRG V35.0)


Convert to ICD-9 Additional informationCallout TooltipGeneral Equivalence Map
The ICD-10 and ICD-9 GEMs are used to facilitate linking between the diagnosis codes in ICD-9-CM and the new ICD-10-CM code set. The GEMs are the raw material from which providers, health information vendors and payers can derive specific applied mappings to meet their needs.
  • 416.0 - Prim pulm hypertension

  • Ayerza's syndrome
  • Cor pulmonale
  • Familial primary pulmonary hypertension
  • Heritable pulmonary arterial hypertension
  • Heritable pulmonary arterial hypertension due to activin A receptor type II-like kinase 1 or endoglin mutation
  • Heritable pulmonary arterial hypertension due to bone morphogenetic protein receptor type II mutation
  • Idiopathic pulmonary arterial hypertension
  • Idiopathic pulmonary arteriosclerosis
  • Precapillary pulmonary hypertension
  • Sporadic primary pulmonary hypertension

Index of Diseases and Injuries
References found for the code I27.0 in the Index of Diseases and Injuries:

Information for Patients

Pulmonary Hypertension

Also called: Pulmonary arterial hypertension

Pulmonary hypertension (PH) is high blood pressure in the arteries to your lungs. It is a serious condition. If you have it, the blood vessels that carry blood from your heart to your lungs become hard and narrow. Your heart has to work harder to pump the blood through. Over time, your heart weakens and cannot do its job and you can develop heart failure.

Symptoms of PH include

  • Shortness of breath during routine activity, such as climbing two flights of stairs
  • Tiredness
  • Chest pain
  • A racing heartbeat
  • Pain on the upper right side of the abdomen
  • Decreased appetite

As PH worsens, you may find it hard to do any physical activities.

There are two main kinds of PH. One runs in families or appears for no known reason. The other kind is related to another condition, usually heart or lung disease.

There is no cure for PH. Treatments can control symptoms. They involve treating the heart or lung disease, medicines, oxygen, and sometimes lung transplantation.

NIH: National Heart, Lung, and Blood Institute

  • Cor pulmonale (Medical Encyclopedia)
  • Lung diffusion testing (Medical Encyclopedia)
  • Pulmonary angiography (Medical Encyclopedia)
  • Pulmonary hypertension (Medical Encyclopedia)

[Read More]

Pulmonary arterial hypertension Pulmonary arterial hypertension is a progressive disorder characterized by abnormally high blood pressure (hypertension) in the pulmonary artery, the blood vessel that carries blood from the heart to the lungs. Pulmonary arterial hypertension is one form of a broader condition known as pulmonary hypertension. Pulmonary hypertension occurs when most of the very small arteries throughout the lungs narrow in diameter, which increases the resistance to blood flow through the lungs. To overcome the increased resistance, blood pressure increases in the pulmonary artery and in the right ventricle of the heart, which is the chamber that pumps blood into the pulmonary artery. Ultimately, the increased blood pressure can damage the right ventricle of the heart.Signs and symptoms of pulmonary arterial hypertension occur when increased blood pressure cannot fully overcome the elevated resistance. As a result, the flow of oxygenated blood from the lungs to the rest of the body is insufficient. Shortness of breath (dyspnea) during exertion and fainting spells are the most common symptoms of pulmonary arterial hypertension. People with this disorder may experience additional symptoms, particularly as the condition worsens. Other symptoms include dizziness, swelling (edema) of the ankles or legs, chest pain, and a rapid heart rate.
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