2026 ICD-10-CM Diagnosis Code K22.0Achalasia of cardia
ICD-10-CM Codes›K00–K95›K20-K31›K22
- Billable — Valid for Submission
- Chronic Condition
K22.0 is a billable ICD-10-CM diagnosis code for achalasia of cardia. It is valid on HIPAA claims for fiscal year 2026 (October 1, 2025 through September 30, 2026) and groups to MS-DRG 391 through 392. In AHRQ's Clinical Classifications Software (CCSR), this diagnosis falls under Esophageal disorders.
Code Identity
Code Classification
Approximate SynonymsGuidance
Alternate terms and clinical phrases that map to this code.
- Absent peristalsis
- Achalasia
- Achalasia due to Chagas disease
- Achalasia of esophagus
- Acquired achalasia of esophagus
- Adrenocorticotropic hormone resistance syndrome
- Aperistalsis of esophagus
- Congenital achalasia of esophagus
- Dilatation of esophagus
- Disorder of esophageal peristalsis
- Glucocorticoid deficiency with achalasia
- Hypertensive spasm of cardiac sphincter
- Idiopathic achalasia of esophagus
- Idiopathic megaesophagus
- Megaesophagus
- Moyamoya disease
- Moyamoya disease with early onset achalasia
- Pituitary thyroid hormone resistance
- Primary adrenocortical insufficiency
- Resistance to thyroid hormone syndrome
Tabular List NotesGuidance
Coding notes and annotation back-references applicable to this code.
Inclusion Terms
- Achalasia NOS
- Cardiospasm
Type 1 Excludes
- congenital cardiospasm Q39.5
These terms are the conditions for which that code is to be used. The terms may be synonyms of the code title, or, in the case of "other specified" codes, the terms are a list of the various conditions assigned to that code. The inclusion terms are not necessarily exhaustive. Additional terms found only in the Alphabetic Index may also be assigned to a code.
A type 1 excludes note is a pure excludes note. It means "NOT CODED HERE!" An Excludes1 note indicates that the code excluded should never be used at the same time as the code above the Excludes1 note. An Excludes1 is used when two conditions cannot occur together, such as a congenital form versus an acquired form of the same condition.
Index to Diseases and InjuriesGuidance
Alphabetical index entries that point to this code.
- Achalasia (cardia) (esophagus) - K22.0
- Aperistalsis, esophagus - K22.0
- due to achalasia - K22.0
- Megaesophagus (functional) - K22.0
- Megaloesophagus (functional) - K22.0
- Spasm (s), spastic, spasticity - See Also: condition; - R25.2
- cardia - K22.0
External Cause of Injuries IndexGuidance
References for this code in the External Cause of Injuries Index.
- Achalasia(cardia) (esophagus)
- Aperistalsis, esophagus
- Cardiospasm(esophagus) (reflex) (stomach)
- Dilatation
- esophagus
- due to achalasia
- Incompetency, incompetent, incompetence
- esophagogastric (junction) (sphincter)
- Megaesophagus(functional)
- Megaloesophagus(functional)
- Spasm(s), spastic, spasticity
- cardia
- Syndrome
- gastroesophageal
- junction
Clinical ClassificationClinical
AHRQ’s CCSR groups this code into broader clinical categories.
Clinical InformationClinical
Moyamoya Disease
a noninflammatory, progressive occlusion of the intracranial carotid arteries and the formation of netlike collateral arteries arising from the circle of willis. cerebral angiogram shows the puff-of-smoke (moyamoya) collaterals at the base of the brain. it is characterized by endothelial hyperplasia and fibrosis with thickening of arterial walls. this disease primarily affects children but can also occur in adults.AAAS wt Allele|AAA|AAASb|ADRACALA|ADRACALIN|ALADIN|Achalasia, Adrenocortical Insufficiency, Alacrimia (Allgrove, Triple-A) Gene|Achalasia, Adrenocortical Insufficiency, Alacrimia Gene|Aladin WD Repeat Nucleoporin wt Allele|Allgrove, Triple-A Gene|GL003
human aaas wild-type allele is located in the vicinity of 12q13.13 and is approximately 17 kb in length. this allele, which encodes aladin protein, is involved in peripheral and central nervous system development and mitotic spindle formation. mutations in the gene are associated with achalasia-addisonianism-alacrima syndrome (allgrove or triple-a syndrome).Achalasia
failure of the smooth muscle fibers of the gastrointestinal tract to relax at any one point of junction of one part with another.Esophageal Achalasia|Achalasia Cardia|Achalasia of Cardia
a finding indicating the lack of adequate relaxation of the lower esophageal sphincter resulting in difficulty swallowing food.Triple A Syndrome|3A syndrome|Achalasia-Addisonianism-Alacrima Syndrome|Allgrove Syndrome|Allgrove Syndrome|Triple-A syndrome
an autosomal recessive condition caused by mutation(s) in the aaas gene encoding the protein aladin, and characterized by primary adrenal insufficiency, esophageal dysmotility, and absence of tear production.Moyamoya Disease
a rare inherited vascular disorder characterized by constriction of arteries at the base of the brain, resulting in the formation of collateral circulation in order to compensate for the constriction. the name "moyamoya" in japanese means "puff of smoke" and derives from the characteristic radiographic appearance of the collateral vessels.Moyamoya Disease 2|MYMY2
an autosomally inherited subtype of moyamoya disease often presenting in childhood caused by mutation(s) in the rnf213 gene, encoding e3 ubiquitin-protein ligase rnf213.RNF213 wt Allele|ALK Lymphoma Oligomerization Partner on Chromosome 17 Gene|ALO17|C17orf27|Chromosome 17 Open Reading Frame 27 Gene|DKFZp762N1115|FLJ13051|KIAA1554|KIAA1618|MGC46622|MGC9929|MYMY2|MYSTR|Moyamoya Disease 2 Gene|NET57|Ring Finger Protein 213 wt Allele|hCG_1812857
human rnf213 wild-type allele is located in the vicinity of 17q25.3 and is approximately 135 kb in length. this allele, which encodes e3 ubiquitin-protein ligase rnf213 protein, may play a role in the regulation of protein ubiquitination. a chromosomal translocation t(2;17)(p23;q25) of this gene with the alk gene is associated with anaplastic large cell lymphoma.Megaesophagus
an abnormal dilation of the esophagus not due to obstruction.Alacrima, Achalasia, and Impaired Intellectual Development Syndrome|AAMR
an autosomal recessive condition caused by mutation(s) in the gmppa gene, encoding mannose-1-phosphate guanyltransferase alpha. it is characterized by alacrima, achalasia, and impaired intellectual development.
Patient EducationClinical
Esophagus Disorders
The esophagus is the muscular tube that carries food and liquids from your mouth to the stomach. You may not be aware of your esophagus until you swallow something too large, too hot, or too cold. You may also notice it when something is wrong. You may feel pain or have trouble swallowing.
Read the full article at MedlinePlus
Courtesy of MedlinePlus, a service of the U.S. National Library of Medicine.
Convert K22.0 to ICD-9-CMHistory
The closest ICD-9-CM equivalents under the General Equivalence Mappings.
Code HistoryHistory
Questions About K22.0Overview
Is K22.0 (Other diseases of esophagus) a billable code?
Yes. This is a billable ICD-10-CM code, specific enough to report achalasia of cardia on HIPAA-covered claims from October 1, 2025 through September 30, 2026.
What MS-DRG does K22.0 group to?
When achalasia of cardia is the principal diagnosis on an inpatient stay, it groups to MS-DRG 391, 392, with relative weights from 0.7796 to 1.2683 depending on complications. Higher weights mean higher Medicare reimbursement.
What is the ICD-9 equivalent of K22.0?
Under the General Equivalence Mappings, achalasia of cardia converts to ICD-9-CM 530.0 (achalasia & cardiospasm). The mapping is approximate, so confirm the match fits the documentation.
Footnotes
[1] Chronic - a chronic condition code indicates a condition lasting 12 months or longer and its effect on the patient based on one or both of the following criteria:
- The condition results in the need for ongoing intervention with medical products,treatment, services, and special equipment
- The condition places limitations on self-care, independent living, and social interactions.
