2026 ICD-10-CM Diagnosis Code K00.4Disturbances in tooth formation
ICD-10-CM Codes›K00–K95›K00-K14›K00
- Billable — Valid for Submission
- Not Chronic
K00.4 is a billable ICD-10-CM diagnosis code for disturbances in tooth formation. It is valid on HIPAA claims for fiscal year 2026 (October 1, 2025 through September 30, 2026) and groups to MS-DRG 157 through 159. In AHRQ's Clinical Classifications Software (CCSR), this diagnosis falls under Any dental condition including traumatic injury, Disorders of teeth and gingiva, and Nontraumatic dental conditions.
Code Identity
Code Classification
Approximate SynonymsGuidance
Alternate terms and clinical phrases that map to this code.
- Agenesis of enamel
- Amelocerebrohypohidrotic syndrome
- Antenatal enamel hypoplasia
- Aplasia of cementum
- Arrest of growth of root of tooth due to and following dental trauma
- Blepharophimosis, intellectual disability syndrome
- Deafness, enamel hypoplasia, nail defect syndrome
- Dental caries associated with enamel hypomineralization
- Dental caries associated with enamel hypoplasia
- Dental caries secondary to developmental defects of tooth structure
- Developmental anomaly of crown and root formation
- Dilaceration of crown of permanent tooth due to and following dental trauma
- Dilaceration of tooth
- Divergence of root of tooth
- Dysplasia of cementum
- Enamel dysplasia
- Enamel hypoplasia
- Generalized enamel hypomineralization
- Generalized enamel hypoplasia associated with ingestion of drugs
- Generalized enamel hypoplasia associated with radiation therapy
- Generalized enamel hypoplasia associated with systemic disease
- Generalized enamel hypoplasia of undetermined etiology
- Hypocalcification of teeth
- Hypohidrosis
- Hypohidrosis, enamel hypoplasia, palmoplantar keratoderma, intellectual disability syndrome
- Hypomineralization of enamel of molar tooth
- Hypomineralization of enamel of second primary molar tooth
- Hypomineralization of enamel of teeth
- Hypomineralization of enamel of tooth
- Hypomineralization of tooth
- Hypoplasia of cementum
- Hypoplasia of enamel due to congenital syphilis
- Hypoplasia of tooth
- Hypoplastic enamel-onycholysis-hypohidrosis syndrome
- Intellectual disability, congenital heart disease, blepharophimosis, blepharoptosis and hypoplastic teeth
- Localized enamel hypomineralization associated with localized infection
- Localized enamel hypomineralization associated with localized trauma
- Localized enamel hypomineralization of undetermined etiology
- Localized enamel hypoplasia
- Localized enamel hypoplasia associated with local infection
- Localized enamel hypoplasia associated with localized trauma
- Localized enamel hypoplasia of undetermined etiology
- Molar incisor hypomineralization
- Neonatal enamel hypoplasia
- Partial arrest of growth of root of tooth due to and following dental trauma
- Regional odontodysplasia
- Root angulation of tooth
- Secondary dental caries associated with local or systemic factors
- Short stature, unique facies, enamel hypoplasia, progressive joint stiffness, high-pitched voice syndrome
- Turner's tooth
- Vestibular root angulation of tooth
- XTE syndrome
Tabular List NotesGuidance
Coding notes and annotation back-references applicable to this code.
Inclusion Terms
- Aplasia and hypoplasia of cementum
- Dilaceration of tooth
- Enamel hypoplasia (neonatal) (postnatal) (prenatal)
- Regional odontodysplasia
- Turner's tooth
Type 1 Excludes
- Hutchinson's teeth and mulberry molars in congenital syphilis A50.5
Type 2 Excludes
- mottled teeth K00.3
These terms are the conditions for which that code is to be used. The terms may be synonyms of the code title, or, in the case of "other specified" codes, the terms are a list of the various conditions assigned to that code. The inclusion terms are not necessarily exhaustive. Additional terms found only in the Alphabetic Index may also be assigned to a code.
A type 1 excludes note is a pure excludes note. It means "NOT CODED HERE!" An Excludes1 note indicates that the code excluded should never be used at the same time as the code above the Excludes1 note. An Excludes1 is used when two conditions cannot occur together, such as a congenital form versus an acquired form of the same condition.
A type 2 excludes note represents "Not included here". An excludes2 note indicates that the condition excluded is not part of the condition represented by the code, but a patient may have both conditions at the same time. When an Excludes2 note appears under a code, it is acceptable to use both the code and the excluded code together, when appropriate.
Index to Diseases and InjuriesGuidance
Alphabetical index entries that point to this code.
- Amelogenesis imperfecta - K00.5
- nonhereditaria (segmentalis) - K00.4
- dentinal papilla - K00.4
- Dilaceration, tooth - K00.4
- Disturbance (s) - See Also: Disease;
- Odontodysplasia, regional - K00.4
- Turner's
- hypoplasia (tooth) - K00.4
- tooth - K00.4
External Cause of Injuries IndexGuidance
References for this code in the External Cause of Injuries Index.
- Amelogenesis imperfecta
- nonhereditaria (segmentalis)
- Aplasia
- cementum
- Calcification
- dentinal papilla
- Dilaceration, tooth
- Disturbance(s)
- tooth
- formation
- Ghost
- teeth
- Hypoplasia, hypoplastic
- cementum
- Hypoplasia, hypoplastic
- enamel of teeth (neonatal) (postnatal) (prenatal)
- Hypoplasia, hypoplastic
- Turner's
- Odontodysplasia, regional
- Pitting
- teeth
- Turner's
- hypoplasia (tooth)
- Turner's
- tooth
Clinical ClassificationClinical
AHRQ’s CCSR groups this code into broader clinical categories.
Clinical InformationClinical
Hypohidrosis
abnormally diminished or absent perspiration. both generalized and segmented (reduced or absent sweating in circumscribed locations) forms of the disease are usually associated with other underlying conditions.Grade 2 Hypohidrosis, CTCAE|Grade 2 Hypohidrosis
symptomatic; limiting instrumental adl or mild/moderate impact on age-appropriate normal daily activity (pediatric)Grade 3 Hypohidrosis, CTCAE|Grade 3 Hypohidrosis
increase in body temperature; limiting self-care adl or severe impact on age-appropriate normal daily activity (pediatric)Grade 4 Hypohidrosis, CTCAE|Grade 4 Hypohidrosis
life-threatening consequences; urgent intervention indicatedEnamel Hypoplasia
deficiency in the enamel tissue that results in the formation of grooves, pits, or dents on the surface of the affected teeth.Grade 2 Hypohidrosis, CTCAE|Grade 2 Hypohidrosis
symptomatic; limiting instrumental adlGrade 3 Hypohidrosis, CTCAE|Grade 3 Hypohidrosis
increase in body temperature; limiting self care adlGrade 4 Hypohidrosis, CTCAE|Grade 4 Hypohidrosis
heat strokeGrade 5 Hypohidrosis, CTCAE|Grade 5 Hypohidrosis
deathHypohidrosis
reduced sweating. causes include burns, dehydration, radiation, and leprosy.Hypohidrosis, CTCAE|Hypohidrosis|Hypohidrosis
a disorder characterized by reduced sweating.
Patient EducationClinical
Tooth Disorders
Your teeth are made of a hard, bonelike material. There are four parts:
The full article covers:
- What are teeth?
- What are tooth disorders?
- What causes tooth disorders?
- What are the symptoms of tooth disorders?
- How are tooth disorders diagnosed?
- What are the treatments for tooth disorders?
- Can tooth disorders be prevented?
Read the full article at MedlinePlus
Courtesy of MedlinePlus, a service of the U.S. National Library of Medicine.
Convert K00.4 to ICD-9-CMHistory
The closest ICD-9-CM equivalents under the General Equivalence Mappings.
Code HistoryHistory
Questions About K00.4Overview
Is K00.4 (Disorders of tooth development and eruption) a billable code?
Yes. This is a billable ICD-10-CM code, specific enough to report disturbances in tooth formation on HIPAA-covered claims from October 1, 2025 through September 30, 2026.
What MS-DRG does K00.4 group to?
When disturbances in tooth formation is the principal diagnosis on an inpatient stay, it groups to MS-DRG 157, 158, 159, with relative weights from 0.7085 to 1.7168 depending on complications. Higher weights mean higher Medicare reimbursement.
What is the ICD-9 equivalent of K00.4?
Under the General Equivalence Mappings, disturbances in tooth formation converts to ICD-9-CM 520.4 (tooth formation disturb). The mapping is a direct match.
Footnotes
[1] Not chronic - A diagnosis code that does not fit the criteria for chronic condition (duration, ongoing medical treatment, and limitations) is considered not chronic. Some codes designated as not chronic are acute conditions. Other diagnosis codes that indicate a possible chronic condition, but for which the duration of the illness is not specified in the code description (i.e., we do not know the condition has lasted 12 months or longer) also are considered not chronic.
