ICD-10-CM Code I42.8

Other cardiomyopathies

Version 2020 Billable Code

Valid for Submission

I42.8 is a billable code used to specify a medical diagnosis of other cardiomyopathies. The code is valid for the year 2020 for the submission of HIPAA-covered transactions. The ICD-10-CM code I42.8 might also be used to specify conditions or terms like arrhythmogenic right ventricular cardiomyopathy, arrhythmogenic right ventricular cardiomyopathy, arrhythmogenic right ventricular dysplasia, cardiomyopathy, congenital woolly hair, disorder of myocardium associated with rejection of cardiac transplant, etc

Short Description:Other cardiomyopathies
Long Description:Other cardiomyopathies

Index to Diseases and Injuries

The Index to Diseases and Injuries is an alphabetical listing of medical terms, with each term mapped to one or more ICD-10 code(s). The following references for the code I42.8 are found in the index:


The following clinical terms are approximate synonyms or lay terms that might be used to identify the correct diagnosis code:

  • Arrhythmogenic right ventricular cardiomyopathy
  • Arrhythmogenic right ventricular cardiomyopathy
  • Arrhythmogenic right ventricular dysplasia
  • Cardiomyopathy
  • Congenital woolly hair
  • Disorder of myocardium associated with rejection of cardiac transplant
  • Disorder of myocardium due to sickle cell hemoglobinopathy
  • Dystrophic cardiomyopathy
  • Familial isolated arrhythmogenic right ventricular dysplasia
  • Fatal infantile mitochondrial cardiomyopathy
  • Histiocytoid mitochondrial cardiomyopathy
  • Histiocytoid mitochondrial cardiomyopathy due to cytochrome aa3 deficiency
  • Hypertrophic mitochondrial cardiomyopathy
  • Hypertrophic mitochondrial cardiomyopathy associated with cataracts and lactic acidosis
  • Hypertrophy of septomarginal trabeculation
  • Inflammatory cardiomyopathy
  • Left ventricular myocardial noncompaction cardiomyopathy
  • Maternally inherited mitochondrial cardiomyopathy and myopathy
  • Mitochondrial cardiomyopathy
  • Mucopolysaccharidosis cardiomyopathy
  • Naxos disease
  • Nonobstructive cardiomyopathy
  • Nutritional and metabolic cardiomyopathies
  • Post-myocarditic cardiomyopathy
  • Primary cardiomyopathy
  • Right ventricular myocardial noncompaction cardiomyopathy
  • TMEM70 related mitochondrial encephalo-cardio-myopathy
  • Valvular cardiomyopathy
  • Ventricular myocardial noncompaction cardiomyopathy
  • Wooly hair

Clinical Information

  • CARDIOMYOPATHY DILATED-. a form of cardiac muscle disease that is characterized by ventricular dilation ventricular dysfunction and heart failure. risk factors include smoking; alcohol drinking; hypertension; infection; pregnancy; and mutations in the lmna gene encoding lamin type a a nuclear lamina protein.
  • CARDIOMYOPATHY HYPERTROPHIC-. a form of cardiac muscle disease characterized by left and/or right ventricular hypertrophy hypertrophy left ventricular; hypertrophy right ventricular frequent asymmetrical involvement of the heart septum and normal or reduced left ventricular volume. risk factors include hypertension; aortic stenosis; and gene mutation; familial hypertrophic cardiomyopathy.
  • CARDIOMYOPATHY RESTRICTIVE-. a form of cardiac muscle disease in which the ventricular walls are excessively rigid impeding ventricular filling. it is marked by reduced diastolic volume of either or both ventricles but normal or nearly normal systolic function. it may be idiopathic or associated with other diseases endomyocardial fibrosis or amyloidosis causing interstitial fibrosis.
  • CARDIOMYOPATHIES-. a group of diseases in which the dominant feature is the involvement of the cardiac muscle itself. cardiomyopathies are classified according to their predominant pathophysiological features dilated cardiomyopathy; hypertrophic cardiomyopathy; restrictive cardiomyopathy or their etiological/pathological factors cardiomyopathy alcoholic; endocardial fibroelastosis.
  • CARDIOMYOPATHY HYPERTROPHIC FAMILIAL-. an autosomal dominant inherited form of hypertrophic cardiomyopathy. it results from any of more than 50 mutations involving genes encoding contractile proteins such as ventricular myosins; cardiac troponin t; alpha tropomyosin.
  • GLYCOGEN STORAGE DISEASE TYPE IIB-. an x linked dominant multisystem disorder resulting in cardiomyopathy myopathy and intellectual disability. it is caused by mutation in the gene encoding lysosomal associated membrane protein 2.
  • DIABETIC CARDIOMYOPATHIES-. diabetes complications in which ventricular remodeling in the absence of coronary atherosclerosis and hypertension results in cardiac dysfunctions typically left ventricular dysfunction. the changes also result in myocardial hypertrophy myocardial necrosis and fibrosis and collagen deposition due to impaired glucose tolerance.

Diagnostic Related Groups

The ICD-10 code I42.8 is grouped in the following groups for version MS-DRG V37.0 What are Diagnostic Related Groups?
The Diagnostic Related Groups (DRGs) are a patient classification scheme which provides a means of relating the type of patients a hospital treats. The DRGs divides all possible principal diagnoses into mutually exclusive principal diagnosis areas referred to as Major Diagnostic Categories (MDC).
applicable from 10/01/2019 through 09/30/2020.


Convert I42.8 to ICD-9

  • 425.2 - Obsc afric cardiomyopath (Approximate Flag)
  • 425.4 - Prim cardiomyopathy NEC (Approximate Flag)

Code Classification

  • Diseases of the circulatory system (I00–I99)
    • Other forms of heart disease (I30-I52)
      • Cardiomyopathy (I42)

Code History

  • FY 2016 - New Code, effective from 10/1/2015 through 9/30/2016
    (First year ICD-10-CM implemented into the HIPAA code set)
  • FY 2017 - No Change, effective from 10/1/2016 through 9/30/2017
  • FY 2018 - No Change, effective from 10/1/2017 through 9/30/2018
  • FY 2019 - No Change, effective from 10/1/2018 through 9/30/2019
  • FY 2020 - No Change, effective from 10/1/2019 through 9/30/2020

Information for Patients


Cardiomyopathy is the name for diseases of the heart muscle. These diseases enlarge your heart muscle or make it thicker and more rigid than normal. In rare cases, scar tissue replaces the muscle tissue.

Some people live long, healthy lives with cardiomyopathy. Some people don't even realize they have it. In others, however, it can make the heart less able to pump blood through the body. This can cause serious complications, including

  • Heart failure
  • Abnormal heart rhythms
  • Heart valve problems
  • Sudden cardiac arrest

Heart attacks, high blood pressure, infections, and other diseases can all cause cardiomyopathy. Some types of cardiomyopathy run in families. In many people, however, the cause is unknown. Treatment might involve medicines, surgery, other medical procedures, and lifestyle changes.

NIH: National Heart, Lung, and Blood Institute

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