2024 ICD-10-CM Diagnosis Code I42.8

Approximate Synonyms

The following clinical terms are approximate synonyms or lay terms that might be used to identify the correct diagnosis code:

• Arrhythmogenic left ventricular cardiomyopathy
• Arrhythmogenic right ventricular dysplasia
• Arrhythmogenic right ventricular dysplasia
• Autosomal recessive familial wooly hair
• Cardiomyopathy
• Cardiomyopathy due to mucopolysaccharidosis
• Coenzyme Q10 deficiency
• Congenital wooly hair
• Disorder of myocardium associated with rejection of cardiac transplant
• Disorder of myocardium due to sickle cell hemoglobinopathy
• Dystrophic cardiomyopathy
• Familial isolated arrhythmogenic right ventricular dysplasia
• Fatal infantile mitochondrial cardiomyopathy
• Histiocytoid mitochondrial cardiomyopathy
• Histiocytoid mitochondrial cardiomyopathy due to cytochrome aa3 deficiency
• Hypertrophic mitochondrial cardiomyopathy
• Hypertrophic mitochondrial cardiomyopathy
• Hypertrophic mitochondrial cardiomyopathy associated with cataracts and lactic acidosis
• Hypertrophy of septomarginal trabeculation
• Infiltrative cardiomyopathy
• Inflammatory cardiomyopathy
• Left ventricular myocardial noncompaction cardiomyopathy
• Left ventricular myocardial noncompaction cardiomyopathy
• Left ventricular myocardial noncompaction cardiomyopathy
• Lethal left ventricular non-compaction, seizures, hypotonia, cataract, developmental delay syndrome
• Macrocephaly, intellectual disability, left ventricular non compaction syndrome
• Maternally inherited mitochondrial cardiomyopathy
• Maternally inherited mitochondrial cardiomyopathy and myopathy
• Maternally inherited mitochondrial deoxyribonucleic acid disease
• Maternally inherited mitochondrial deoxyribonucleic acid disease
• Mitochondrial cardiomyopathy
• Myocardial degeneration
• Myocardial degeneration
• Naxos disease
• Neonatal encephalomyopathy, cardiomyopathy, respiratory distress syndrome
• Nonobstructive cardiomyopathy
• Post-myocarditic cardiomyopathy
• Primary cardiomyopathy
• Right ventricular myocardial noncompaction cardiomyopathy
• TMEM70 related mitochondrial encephalo-cardio-myopathy
• Valvular cardiomyopathy
• Ventricular myocardial noncompaction cardiomyopathy
• Ventricular myocardial noncompaction cardiomyopathy
• Ventricular myocardial noncompaction cardiomyopathy

Clinical Information

• Cardiomyopathies

  a group of diseases in which the dominant feature is the involvement of the cardiac muscle itself. cardiomyopathies are classified according to their predominant pathophysiological features (dilated cardiomyopathy; hypertrophic cardiomyopathy; restrictive cardiomyopathy) or their etiological/pathological factors (cardiomyopathy, alcoholic; endocardial fibroelastosis).

• Cardiomyopathy, Dilated

  a form of cardiac muscle disease that is characterized by ventricular dilation, ventricular dysfunction, and heart failure. risk factors include smoking; alcohol drinking; hypertension; infection; pregnancy; and mutations in the lmna gene encoding lamin type a, a nuclear lamina protein.

• Cardiomyopathy, Hypertrophic

  a form of cardiac muscle disease, characterized by left and/or right ventricular hypertrophy (hypertrophy, left ventricular; hypertrophy, right ventricular), frequent asymmetrical involvement of the heart septum, and normal or reduced left ventricular volume. risk factors include hypertension; aortic stenosis; and gene mutation; (familial hypertrophic cardiomyopathy).

• Cardiomyopathy, Hypertrophic, Familial

  an autosomal dominant inherited form of hypertrophic cardiomyopathy. it results from any of more than 50 mutations involving genes encoding contractile proteins such as ventricular myosins; cardiac troponin t; alpha-tropomyosin.

• Cardiomyopathy, Restrictive

  a form of cardiac muscle disease in which the ventricular walls are excessively rigid, impeding ventricular filling. it is marked by reduced diastolic volume of either or both ventricles but normal or nearly normal systolic function. it may be idiopathic or associated with other diseases (endomyocardial fibrosis or amyloidosis) causing interstitial fibrosis.

• Diabetic Cardiomyopathies

  diabetes complications in which ventricular remodeling in the absence of coronary atherosclerosis and hypertension results in cardiac dysfunctions, typically left ventricular dysfunction. the changes also result in myocardial hypertrophy, myocardial necrosis and fibrosis, and collagen deposition due to impaired glucose tolerance.

• Glycogen Storage Disease Type IIb

  an x-linked dominant multisystem disorder resulting in cardiomyopathy, myopathy and intellectual disability. it is caused by mutation in the gene encoding lysosomal-associated membrane protein 2.

• Arrhythmogenic Right Ventricular Dysplasia

  a congenital cardiomyopathy that is characterized by infiltration of adipose and fibrous tissue into the right ventricle wall and loss of myocardial cells. primary injuries usually are at the free wall of right ventricular and right atria resulting in ventricular and supraventricular arrhythmias.

• Myocardial Degeneration

  degeneration of myocardial tissue.

• Coenzyme Q10 Deficiency

  a genetically heterogeneous condition, typically inherited in an autosomal recessive fashion, characterized by coenzyme q10 deficiency.

I42.8 is grouped with Diagnostic Related Groups - MS-DRG Mapping

Diagnostic Related Groups (DRGs) are a classification system used to group together diagnosis codes for the purpose of reimbursement and healthcare management. DRGs are used to standardize the way hospitals and other providers are paid for inpatient services. In this system patients are grouped together based on their principal diagnosis in areas referred to as Major Diagnostic Categories (MDC). Once a patient is assigned a particular diagnostic category, providers receive a predetermined payment rate for the services rendered. This reimbursement rate is often fixed and is meant to cover the cost of care for that patient. Reimbursement is also affected by the relative weight of a diagnostic related group based on the severity of a patient's illness and the associated cost of care during hospitalization.

Diagnostic related groups encourage healthcare providers to focus on quality and efficiency in patient care while managing costs effectively. The diagnosis code is present in the following groups for version MS-DRG V41.0 applicable from 10/01/2023 through 09/30/2024.

MS-DRG	MS-DRG Title	MCD	Relative Weight
314	OTHER CIRCULATORY SYSTEM DIAGNOSES WITH MCC	05	2.0935
315	OTHER CIRCULATORY SYSTEM DIAGNOSES WITH CC	05	0.9673
316	OTHER CIRCULATORY SYSTEM DIAGNOSES WITHOUT CC/MCC	05	0.6927

The relative weight of a diagnostic related group determines the reimbursement rate based on the severity of a patient's illness and the associated cost of care during hospitalization.

Convert I42.8 to ICD-9-CM

• ICD-9-CM Code: 425.2 - Obsc afric cardiomyopath
  Approximate Flag - The approximate mapping means there is not an exact match between the ICD-10 and ICD-9 codes and the mapped code is not a precise representation of the original code.
• ICD-9-CM Code: 425.4 - Prim cardiomyopathy NEC
  Approximate Flag - The approximate mapping means there is not an exact match between the ICD-10 and ICD-9 codes and the mapped code is not a precise representation of the original code.

Patient Education

Cardiomyopathy

Cardiomyopathy is the name for diseases of the heart muscle. These diseases enlarge your heart muscle or make it thicker and more rigid than normal. In rare cases, scar tissue replaces the muscle tissue.

Some people live long, healthy lives with cardiomyopathy. Some people don't even realize they have it. In others, however, it can make the heart less able to pump blood through the body. This can cause serious complications, including:

• Heart failure
• Abnormal heart rhythms
• Heart valve problems
• Sudden cardiac arrest (SCA)

Heart attacks, high blood pressure, infections, and other diseases can all cause cardiomyopathy. Some types of cardiomyopathy run in families. In many people, however, the cause is unknown. Treatment might involve medicines, surgery, other medical procedures, and lifestyle changes.

NIH: National Heart, Lung, and Blood Institute

[Learn More in MedlinePlus]

Code History

• FY 2024 - No Change, effective from 10/1/2023 through 9/30/2024
• FY 2023 - No Change, effective from 10/1/2022 through 9/30/2023
• FY 2022 - No Change, effective from 10/1/2021 through 9/30/2022
• FY 2021 - No Change, effective from 10/1/2020 through 9/30/2021
• FY 2020 - No Change, effective from 10/1/2019 through 9/30/2020
• FY 2019 - No Change, effective from 10/1/2018 through 9/30/2019
• FY 2018 - No Change, effective from 10/1/2017 through 9/30/2018
• FY 2017 - No Change, effective from 10/1/2016 through 9/30/2017
• FY 2016 - New Code, effective from 10/1/2015 through 9/30/2016. This was the first year ICD-10-CM was implemented into the HIPAA code set.