Cardiomyopathy in diseases classified elsewhere (I43)

The ICD-10 code I43 is used to identify cardiomyopathy that arises specifically as a result of other underlying diseases rather than as a primary heart condition. This includes heart muscle disorders linked to systemic illnesses like thyrotoxicosis, systemic lupus erythematosus, or viral infections.

Cardiomyopathy in diseases classified elsewhere (I43) covers a diverse group of heart muscle diseases caused by various systemic or inherited conditions. Commonly called names such as thyrotoxic cardiomyopathy, diabetic cardiomyopathy, or familial restrictive cardiomyopathy, these reflect heart problems secondary to diseases including endocrine disorders, autoimmune diseases, metabolic storage diseases, infections like COVID-19, and genetic abnormalities such as muscular dystrophies or amyloidosis. Using this ICD-10 code allows healthcare professionals and coders to classify cardiomyopathy precisely when it is linked to another disorder, clarifying the connection between the heart condition and its systemic cause. This specificity improves accuracy when documenting complex cases where the heart disease is one aspect of a broader illness, thus ensuring that the right ICD-10 code for cardiomyopathy due to systemic or hereditary disease is applied.

Instructional Notations

Code First

Certain conditions have both an underlying etiology and multiple body system manifestations due to the underlying etiology. For such conditions, the ICD-10-CM has a coding convention that requires the underlying condition be sequenced first followed by the manifestation. Wherever such a combination exists, there is a "use additional code" note at the etiology code, and a "code first" note at the manifestation code. These instructional notes indicate the proper sequencing order of the codes, etiology followed by manifestation.

Type 1 Excludes

A type 1 excludes note is a pure excludes note. It means "NOT CODED HERE!" An Excludes1 note indicates that the code excluded should never be used at the same time as the code above the Excludes1 note. An Excludes1 is used when two conditions cannot occur together, such as a congenital form versus an acquired form of the same condition.

Clinical Terms

The following clinical terms provide additional context, helping users better understand the clinical background and common associations for each diagnosis listed in this section. Including related terms alongside ICD-10-CM codes supports coders, billers, and healthcare professionals in improving accuracy, enhancing documentation, and facilitating research or patient education.

Endomyocardial Fibrosis

A condition characterized by the thickening of the ventricular ENDOCARDIUM and subendocardium (MYOCARDIUM), seen mostly in children and young adults in the TROPICAL CLIMATE. The fibrous tissue extends from the apex toward and often involves the HEART VALVES causing restrictive blood flow into the respective ventricles (CARDIOMYOPATHY, RESTRICTIVE).