2024 ICD-10-CM Diagnosis Code I42.5

Other restrictive cardiomyopathy

ICD-10-CM Code:
I42.5
ICD-10 Code for:
Other restrictive cardiomyopathy
Is Billable?
Yes - Valid for Submission
Chronic Condition Indicator: [1]
Chronic
Code Navigator:

Code Classification

  • Diseases of the circulatory system
    (I00–I99)
    • Other forms of heart disease
      (I30-I5A)
      • Cardiomyopathy
        (I42)

I42.5 is a billable diagnosis code used to specify a medical diagnosis of other restrictive cardiomyopathy. The code is valid during the current fiscal year for the submission of HIPAA-covered transactions from October 01, 2023 through September 30, 2024.

Approximate Synonyms

The following clinical terms are approximate synonyms or lay terms that might be used to identify the correct diagnosis code:

  • Acquired abnormality of right cardiac ventricle
  • Acquired stenosis of subpulmonary area
  • Acquired subpulmonary stenosis associated with functionally univentricular heart
  • Acquired subpulmonary stenosis due to restrictive ventricular defect associated with functionally univentricular heart
  • Cardiomyopathy due to mucopolysaccharidosis
  • Familial cardiomyopathy
  • Familial restrictive cardiomyopathy
  • Functionally univentricular heart
  • Primary idiopathic restrictive cardiomyopathy
  • Primary restrictive cardiomyopathy
  • Restrictive cardiomyopathy
  • Restrictive cardiomyopathy due to mucopolysaccharidosis
  • Restrictive cardiomyopathy secondary to amyloidosis
  • Restrictive cardiomyopathy secondary to endocardial fibroelastosis
  • Restrictive cardiomyopathy secondary to glycogen storage disease
  • Restrictive cardiomyopathy secondary to granulomas
  • Restrictive cardiomyopathy secondary to hemochromatosis
  • Restrictive cardiomyopathy secondary to infiltrations
  • Restrictive cardiomyopathy secondary to malignancy
  • Restrictive cardiomyopathy secondary to sarcoidosis
  • Restrictive cardiomyopathy without endomyocardial fibrosis
  • Secondary restrictive cardiomyopathy
  • Secondary restrictive cardiomyopathy
  • Secondary restrictive cardiomyopathy
  • Secondary restrictive cardiomyopathy
  • Secondary restrictive cardiomyopathy
  • Secondary restrictive cardiomyopathy
  • Secondary restrictive cardiomyopathy
  • Secondary restrictive cardiomyopathy
  • Secondary restrictive cardiomyopathy
  • Subpulmonary stenosis

Clinical Classification

Tabular List of Diseases and Injuries

The following annotation back-references are applicable to this diagnosis code. The Tabular List of Diseases and Injuries is a list of ICD-10-CM codes, organized "head to toe" into chapters and sections with coding notes and guidance for inclusions, exclusions, descriptions and more.


Inclusion Terms

Inclusion Terms
These terms are the conditions for which that code is to be used. The terms may be synonyms of the code title, or, in the case of "other specified" codes, the terms are a list of the various conditions assigned to that code. The inclusion terms are not necessarily exhaustive. Additional terms found only in the Alphabetic Index may also be assigned to a code.
  • Constrictive cardiomyopathy NOS

Index to Diseases and Injuries References

The following annotation back-references for this diagnosis code are found in the injuries and diseases index. The Index to Diseases and Injuries is an alphabetical listing of medical terms, with each term mapped to one or more ICD-10-CM code(s).

Convert I42.5 to ICD-9-CM

  • ICD-9-CM Code: 425.4 - Prim cardiomyopathy NEC
    Approximate Flag - The approximate mapping means there is not an exact match between the ICD-10 and ICD-9 codes and the mapped code is not a precise representation of the original code.

Patient Education


Cardiomyopathy

Cardiomyopathy is the name for diseases of the heart muscle. These diseases enlarge your heart muscle or make it thicker and more rigid than normal. In rare cases, scar tissue replaces the muscle tissue.

Some people live long, healthy lives with cardiomyopathy. Some people don't even realize they have it. In others, however, it can make the heart less able to pump blood through the body. This can cause serious complications, including:

  • Heart failure
  • Abnormal heart rhythms
  • Heart valve problems
  • Sudden cardiac arrest (SCA)

Heart attacks, high blood pressure, infections, and other diseases can all cause cardiomyopathy. Some types of cardiomyopathy run in families. In many people, however, the cause is unknown. Treatment might involve medicines, surgery, other medical procedures, and lifestyle changes.

NIH: National Heart, Lung, and Blood Institute


[Learn More in MedlinePlus]

Familial restrictive cardiomyopathy

Familial restrictive cardiomyopathy is a genetic form of heart disease. For the heart to beat normally, the heart (cardiac) muscle must contract and relax in a coordinated way. Oxygen-rich blood from the lungs travels first through the upper chambers of the heart (the atria), and then to the lower chambers of the heart (the ventricles).

In people with familial restrictive cardiomyopathy, the heart muscle is stiff and cannot fully relax after each contraction. Impaired muscle relaxation causes blood to back up in the atria and lungs, which reduces the amount of blood in the ventricles.

Familial restrictive cardiomyopathy can appear anytime from childhood to adulthood. The first signs and symptoms of this condition in children are failure to gain weight and grow at the expected rate (failure to thrive), extreme tiredness (fatigue), and fainting. Children who are severely affected may also have abnormal swelling or puffiness (edema), increased blood pressure, an enlarged liver, an abnormal buildup of fluid in the abdominal cavity (ascites), and lung congestion. Some children with familial restrictive cardiomyopathy do not have any obvious signs or symptoms, but they may die suddenly due to heart failure. Without treatment, the majority of affected children survive only a few years after they are diagnosed.

Adults with familial restrictive cardiomyopathy typically first develop shortness of breath, fatigue, and a reduced ability to exercise. Some individuals have an irregular heart beat (arrhythmia) and may also experience a sensation of fluttering or pounding in the chest (palpitations) and dizziness. Abnormal blood clots are commonly seen in adults with this condition. Without treatment, approximately one-third of adults with familial restrictive cardiomyopathy do not survive more than five years after diagnosis.


[Learn More in MedlinePlus]

Code History

  • FY 2024 - No Change, effective from 10/1/2023 through 9/30/2024
  • FY 2023 - No Change, effective from 10/1/2022 through 9/30/2023
  • FY 2022 - No Change, effective from 10/1/2021 through 9/30/2022
  • FY 2021 - No Change, effective from 10/1/2020 through 9/30/2021
  • FY 2020 - No Change, effective from 10/1/2019 through 9/30/2020
  • FY 2019 - No Change, effective from 10/1/2018 through 9/30/2019
  • FY 2018 - No Change, effective from 10/1/2017 through 9/30/2018
  • FY 2017 - No Change, effective from 10/1/2016 through 9/30/2017
  • FY 2016 - New Code, effective from 10/1/2015 through 9/30/2016. This was the first year ICD-10-CM was implemented into the HIPAA code set.

Footnotes

[1] Chronic - a chronic condition code indicates a condition lasting 12 months or longer and its effect on the patient based on one or both of the following criteria:

  • The condition results in the need for ongoing intervention with medical products,treatment, services, and special equipment
  • The condition places limitations on self-care, independent living, and social interactions.