ICD-10-CM Code I42.5

Other restrictive cardiomyopathy

Version 2021 Billable Code

Valid for Submission

I42.5 is a billable code used to specify a medical diagnosis of other restrictive cardiomyopathy. The code is valid for the fiscal year 2021 for the submission of HIPAA-covered transactions. The ICD-10-CM code I42.5 might also be used to specify conditions or terms like acquired subpulmonary stenosis associated with functionally univentricular heart, acquired subpulmonary stenosis due to restrictive ventricular defect associated with functionally univentricular heart, familial cardiomyopathy, familial restrictive cardiomyopathy, primary idiopathic restrictive cardiomyopathy, primary restrictive cardiomyopathy, etc

ICD-10:I42.5
Short Description:Other restrictive cardiomyopathy
Long Description:Other restrictive cardiomyopathy

Tabular List of Diseases and Injuries

The Tabular List of Diseases and Injuries is a list of ICD-10 codes, organized "head to toe" into chapters and sections with guidance for inclusions, exclusions, descriptions and more. The following references are applicable to the code I42.5:

Inclusion Terms

Inclusion Terms
These terms are the conditions for which that code is to be used. The terms may be synonyms of the code title, or, in the case of "other specified" codes, the terms are a list of the various conditions assigned to that code. The inclusion terms are not necessarily exhaustive. Additional terms found only in the Alphabetic Index may also be assigned to a code.
  • Constrictive cardiomyopathy NOS

Index to Diseases and Injuries

The Index to Diseases and Injuries is an alphabetical listing of medical terms, with each term mapped to one or more ICD-10 code(s). The following references for the code I42.5 are found in the index:


Synonyms

The following clinical terms are approximate synonyms or lay terms that might be used to identify the correct diagnosis code:

  • Acquired subpulmonary stenosis associated with functionally univentricular heart
  • Acquired subpulmonary stenosis due to restrictive ventricular defect associated with functionally univentricular heart
  • Familial cardiomyopathy
  • Familial restrictive cardiomyopathy
  • Primary idiopathic restrictive cardiomyopathy
  • Primary restrictive cardiomyopathy
  • Restrictive cardiomyopathy
  • Restrictive cardiomyopathy secondary to amyloidosis
  • Restrictive cardiomyopathy secondary to endocardial fibroelastosis
  • Restrictive cardiomyopathy secondary to glycogen storage disease
  • Restrictive cardiomyopathy secondary to granulomas
  • Restrictive cardiomyopathy secondary to hemochromatosis
  • Restrictive cardiomyopathy secondary to infiltrations
  • Restrictive cardiomyopathy secondary to malignancy
  • Restrictive cardiomyopathy secondary to mucopolysaccharidosis
  • Restrictive cardiomyopathy secondary to sarcoidosis
  • Restrictive cardiomyopathy without endomyocardial fibrosis
  • Secondary restrictive cardiomyopathy
  • Secondary restrictive cardiomyopathy
  • Secondary restrictive cardiomyopathy
  • Secondary restrictive cardiomyopathy
  • Secondary restrictive cardiomyopathy
  • Secondary restrictive cardiomyopathy
  • Subpulmonary stenosis

Clinical Information

  • CARDIOMYOPATHY RESTRICTIVE-. a form of cardiac muscle disease in which the ventricular walls are excessively rigid impeding ventricular filling. it is marked by reduced diastolic volume of either or both ventricles but normal or nearly normal systolic function. it may be idiopathic or associated with other diseases endomyocardial fibrosis or amyloidosis causing interstitial fibrosis.

Diagnostic Related Groups

The ICD-10 code I42.5 is grouped in the following groups for version MS-DRG V38.0 What are Diagnostic Related Groups?
The Diagnostic Related Groups (DRGs) are a patient classification scheme which provides a means of relating the type of patients a hospital treats. The DRGs divides all possible principal diagnoses into mutually exclusive principal diagnosis areas referred to as Major Diagnostic Categories (MDC).
applicable from 10/01/2020 through 09/30/2021.

  • 314 - OTHER CIRCULATORY SYSTEM DIAGNOSES WITH MCC
  • 315 - OTHER CIRCULATORY SYSTEM DIAGNOSES WITH CC
  • 316 - OTHER CIRCULATORY SYSTEM DIAGNOSES WITHOUT CC/MCC

Convert I42.5 to ICD-9

  • 425.4 - Prim cardiomyopathy NEC (Approximate Flag)

Code Classification

  • Diseases of the circulatory system (I00–I99)
    • Other forms of heart disease (I30-I52)
      • Cardiomyopathy (I42)

Code History

  • FY 2016 - New Code, effective from 10/1/2015 through 9/30/2016
    (First year ICD-10-CM implemented into the HIPAA code set)
  • FY 2017 - No Change, effective from 10/1/2016 through 9/30/2017
  • FY 2018 - No Change, effective from 10/1/2017 through 9/30/2018
  • FY 2019 - No Change, effective from 10/1/2018 through 9/30/2019
  • FY 2020 - No Change, effective from 10/1/2019 through 9/30/2020
  • FY 2021 - No Change, effective from 10/1/2020 through 9/30/2021

Information for Patients


Cardiomyopathy

Also called: Dilated cardiomyopathy, Hypertrophic cardiomyopathy, Myocardiopathy, Restrictive cardiomyopathy

Cardiomyopathy is the name for diseases of the heart muscle. These diseases enlarge your heart muscle or make it thicker and more rigid than normal. In rare cases, scar tissue replaces the muscle tissue.

Some people live long, healthy lives with cardiomyopathy. Some people don't even realize they have it. In others, however, it can make the heart less able to pump blood through the body. This can cause serious complications, including

  • Heart failure
  • Abnormal heart rhythms
  • Heart valve problems
  • Sudden cardiac arrest

Heart attacks, high blood pressure, infections, and other diseases can all cause cardiomyopathy. Some types of cardiomyopathy run in families. In many people, however, the cause is unknown. Treatment might involve medicines, surgery, other medical procedures, and lifestyle changes.

NIH: National Heart, Lung, and Blood Institute

  • Cardiomyopathy (Medical Encyclopedia)
  • Dilated cardiomyopathy (Medical Encyclopedia)
  • Electrocardiogram (Medical Encyclopedia)
  • Hypertrophic cardiomyopathy (Medical Encyclopedia)

[Learn More]

Familial restrictive cardiomyopathy Familial restrictive cardiomyopathy is a genetic form of heart disease. For the heart to beat normally, the heart (cardiac) muscle must contract and relax in a coordinated way. Oxygen-rich blood from the lungs travels first through the upper chambers of the heart (the atria), and then to the lower chambers of the heart (the ventricles).In people with familial restrictive cardiomyopathy, the heart muscle is stiff and cannot fully relax after each contraction. Impaired muscle relaxation causes blood to back up in the atria and lungs, which reduces the amount of blood in the ventricles.Familial restrictive cardiomyopathy can appear anytime from childhood to adulthood. The first signs and symptoms of this condition in children are failure to gain weight and grow at the expected rate (failure to thrive), extreme tiredness (fatigue), and fainting. Children who are severely affected may also have abnormal swelling or puffiness (edema), increased blood pressure, an enlarged liver, an abnormal buildup of fluid in the abdominal cavity (ascites), and lung congestion. Some children with familial restrictive cardiomyopathy do not have any obvious signs or symptoms, but they may die suddenly due to heart failure. Without treatment, the majority of affected children survive only a few years after they are diagnosed.Adults with familial restrictive cardiomyopathy typically first develop shortness of breath, fatigue, and a reduced ability to exercise. Some individuals have an irregular heart beat (arrhythmia) and may also experience a sensation of fluttering or pounding in the chest (palpitations) and dizziness. Abnormal blood clots are commonly seen in adults with this condition. Without treatment, approximately one-third of adults with familial restrictive cardiomyopathy do not survive more than five years after diagnosis.
[Learn More]