2024 ICD-10-CM Diagnosis Code I42.0

Dilated cardiomyopathy

ICD-10-CM Code:
I42.0
ICD-10 Code for:
Dilated cardiomyopathy
Is Billable?
Yes - Valid for Submission
Chronic Condition Indicator: [1]
Chronic
Code Navigator:

Code Classification

  • Diseases of the circulatory system
    (I00–I99)
    • Other forms of heart disease
      (I30-I5A)
      • Cardiomyopathy
        (I42)

I42.0 is a billable diagnosis code used to specify a medical diagnosis of dilated cardiomyopathy. The code is valid during the current fiscal year for the submission of HIPAA-covered transactions from October 01, 2023 through September 30, 2024.

Approximate Synonyms

The following clinical terms are approximate synonyms or lay terms that might be used to identify the correct diagnosis code:

  • Autosomal dominant epidermolysis bullosa simplex
  • Autosomal recessive familial wooly hair
  • Cardiomyopathy caused by drug
  • Cardiomyopathy due to connective tissue disease
  • Cardiomyopathy due to mucopolysaccharidosis
  • Cardiomyopathy due to viral infection
  • Cardiomyopathy in Friedreich's ataxia
  • Cardiomyopathy in myotonic dystrophy
  • Cardiomyopathy with cataract and hip spine disease syndrome
  • Cardiovascular abnormality due to infective myocarditis
  • Cardiovascular abnormality due to infective myocarditis
  • Cardiovascular abnormality due to infective myocarditis
  • Cardiovascular abnormality due to infective myocarditis
  • Cardiovascular abnormality due to infective myocarditis
  • Congenital wooly hair
  • Congestive obstructive cardiomyopathy
  • Dilated cardiomyopathy
  • Dilated cardiomyopathy 3B
  • Dilated cardiomyopathy caused by anthracycline
  • Dilated cardiomyopathy due to amyloidosis
  • Dilated cardiomyopathy due to bacterial myocarditis
  • Dilated cardiomyopathy due to carnitine deficiency
  • Dilated cardiomyopathy due to dermatomyositis
  • Dilated cardiomyopathy due to electrolyte imbalance
  • Dilated cardiomyopathy due to familial storage disease
  • Dilated cardiomyopathy due to Friedreich's ataxia
  • Dilated cardiomyopathy due to fungal myocarditis
  • Dilated cardiomyopathy due to glycogen storage disease
  • Dilated cardiomyopathy due to granuloma
  • Dilated cardiomyopathy due to hemochromatosis
  • Dilated cardiomyopathy due to infectious disease
  • Dilated cardiomyopathy due to infectious disease
  • Dilated cardiomyopathy due to infectious disease
  • Dilated cardiomyopathy due to infectious disease
  • Dilated cardiomyopathy due to infectious disease
  • Dilated cardiomyopathy due to infectious disease
  • Dilated cardiomyopathy due to infiltration
  • Dilated cardiomyopathy due to infiltration
  • Dilated cardiomyopathy due to infiltration
  • Dilated cardiomyopathy due to lysosomal storage disease
  • Dilated cardiomyopathy due to malignancy
  • Dilated cardiomyopathy due to metabolic disorder
  • Dilated cardiomyopathy due to metabolic disorder
  • Dilated cardiomyopathy due to metabolic disorder
  • Dilated cardiomyopathy due to metabolic disorder
  • Dilated cardiomyopathy due to metabolic disorder
  • Dilated cardiomyopathy due to metabolic disorder
  • Dilated cardiomyopathy due to metabolic disorder
  • Dilated cardiomyopathy due to metabolic disorder
  • Dilated cardiomyopathy due to mitochondrial disease
  • Dilated cardiomyopathy due to mucopolysaccharidosis
  • Dilated cardiomyopathy due to muscular dystrophy
  • Dilated cardiomyopathy due to muscular dystrophy
  • Dilated cardiomyopathy due to myotonic dystrophy
  • Dilated cardiomyopathy due to neuromuscular disorder
  • Dilated cardiomyopathy due to nutritional deficiency
  • Dilated cardiomyopathy due to nutritional deficiency
  • Dilated cardiomyopathy due to parasitic myocarditis
  • Dilated cardiomyopathy due to parasitic myocarditis
  • Dilated cardiomyopathy due to phytanic acid storage disease
  • Dilated cardiomyopathy due to polyarteritis nodosa
  • Dilated cardiomyopathy due to protozoan myocarditis
  • Dilated cardiomyopathy due to rheumatoid arthritis
  • Dilated cardiomyopathy due to sarcoidosis
  • Dilated cardiomyopathy due to systemic sclerosis
  • Dilated cardiomyopathy due to taurine deficiency
  • Dilated cardiomyopathy due to viral myocarditis
  • Dilated cardiomyopathy secondary to drug
  • Dilated cardiomyopathy secondary to radiation
  • Dilated cardiomyopathy with connective tissue disorder
  • Dilated cardiomyopathy with genetic marker
  • Dilated cardiomyopathy with hypergonadotropic hypogonadism syndrome
  • Erythrokeratodermia cardiomyopathy syndrome
  • Familial cardiomyopathy
  • Familial cardiomyopathy
  • Familial cardiomyopathy
  • Familial dilated cardiomyopathy with conduction defect due to LMNA mutation
  • Infiltrative cardiomyopathy
  • Infiltrative cardiomyopathy
  • Infiltrative cardiomyopathy
  • Intermediate epidermolysis bullosa simplex with cardiomyopathy
  • Ischemic congestive cardiomyopathy
  • Ischemic congestive cardiomyopathy
  • Ischemic dilated cardiomyopathy due to coronary artery disease
  • Microcephalus cardiomyopathy syndrome
  • Myocardial degeneration
  • Myocardial degeneration
  • Myocardial degeneration
  • Nonischemic congestive cardiomyopathy
  • Nonsenile cataract
  • Primary dilated cardiomyopathy
  • Primary familial dilated cardiomyopathy
  • Primary idiopathic dilated cardiomyopathy
  • Secondary dilated cardiomyopathy
  • Secondary nonischemic congestive cardiomyopathy
  • Sensorineural deafness with dilated cardiomyopathy syndrome
  • Wooly hair and palmoplantar keratoderma with dilated cardiomyopathy syndrome

Clinical Classification

Clinical Information

  • Intermediate Epidermolysis Bullosa Simplex with Cardiomyopathy

    an autosomal dominant condition caused by mutation(s) in the klhl24 gene, encoding kelch-like protein 24. it is characterized by epidermolysis bullosa and dilated cardiomyopathy.
  • Myocardial Degeneration

    degeneration of myocardial tissue.

Tabular List of Diseases and Injuries

The following annotation back-references are applicable to this diagnosis code. The Tabular List of Diseases and Injuries is a list of ICD-10-CM codes, organized "head to toe" into chapters and sections with coding notes and guidance for inclusions, exclusions, descriptions and more.


Inclusion Terms

Inclusion Terms
These terms are the conditions for which that code is to be used. The terms may be synonyms of the code title, or, in the case of "other specified" codes, the terms are a list of the various conditions assigned to that code. The inclusion terms are not necessarily exhaustive. Additional terms found only in the Alphabetic Index may also be assigned to a code.
  • Congestive cardiomyopathy

Index to Diseases and Injuries References

The following annotation back-references for this diagnosis code are found in the injuries and diseases index. The Index to Diseases and Injuries is an alphabetical listing of medical terms, with each term mapped to one or more ICD-10-CM code(s).

Convert I42.0 to ICD-9-CM

  • ICD-9-CM Code: 425.4 - Prim cardiomyopathy NEC
    Approximate Flag - The approximate mapping means there is not an exact match between the ICD-10 and ICD-9 codes and the mapped code is not a precise representation of the original code.

Patient Education


Cardiomyopathy

Cardiomyopathy is the name for diseases of the heart muscle. These diseases enlarge your heart muscle or make it thicker and more rigid than normal. In rare cases, scar tissue replaces the muscle tissue.

Some people live long, healthy lives with cardiomyopathy. Some people don't even realize they have it. In others, however, it can make the heart less able to pump blood through the body. This can cause serious complications, including:

  • Heart failure
  • Abnormal heart rhythms
  • Heart valve problems
  • Sudden cardiac arrest (SCA)

Heart attacks, high blood pressure, infections, and other diseases can all cause cardiomyopathy. Some types of cardiomyopathy run in families. In many people, however, the cause is unknown. Treatment might involve medicines, surgery, other medical procedures, and lifestyle changes.

NIH: National Heart, Lung, and Blood Institute


[Learn More in MedlinePlus]

Familial dilated cardiomyopathy

Familial dilated cardiomyopathy is a genetic form of heart disease. It occurs when heart (cardiac) muscle becomes thin and weakened in at least one chamber of the heart, causing the open area of the chamber to become enlarged (dilated). As a result, the heart is unable to pump blood as efficiently as usual. To compensate, the heart attempts to increase the amount of blood being pumped through the heart, leading to further thinning and weakening of the cardiac muscle. Over time, this condition results in heart failure.

It usually takes many years for symptoms of familial dilated cardiomyopathy to cause health problems. They typically begin in mid-adulthood, but can occur at any time from infancy to late adulthood. Signs and symptoms of familial dilated cardiomyopathy can include an irregular heartbeat (arrhythmia), shortness of breath (dyspnea), extreme tiredness (fatigue), fainting episodes (syncope), and swelling of the legs and feet. In some cases, the first sign of the disorder is sudden cardiac death. The severity of the condition varies among affected individuals, even in members of the same family.


[Learn More in MedlinePlus]

X-linked dilated cardiomyopathy

X-linked dilated cardiomyopathy is a form of heart disease. Dilated cardiomyopathy enlarges and weakens the heart (cardiac) muscle, preventing the heart from pumping blood efficiently. Signs and symptoms of this condition can include an irregular heartbeat (arrhythmia), shortness of breath, extreme tiredness (fatigue), and swelling of the legs and feet. In males with X-linked dilated cardiomyopathy, heart problems usually develop early in life and worsen quickly, leading to heart failure in adolescence or early adulthood. In affected females, the condition appears later in life and worsens more slowly.

X-linked dilated cardiomyopathy is part of a spectrum of related conditions caused by mutations in the DMD gene. The other conditions in the spectrum, Duchenne and Becker muscular dystrophy, are characterized by progressive weakness and wasting of muscles used for movement (skeletal muscles) in addition to heart disease. People with X-linked dilated cardiomyopathy typically do not have any skeletal muscle weakness or wasting, although they may have subtle changes in their skeletal muscle cells that are detectable through laboratory testing. Based on these skeletal muscle changes, X-linked dilated cardiomyopathy is sometimes classified as subclinical Becker muscular dystrophy.


[Learn More in MedlinePlus]

Code History

  • FY 2024 - No Change, effective from 10/1/2023 through 9/30/2024
  • FY 2023 - No Change, effective from 10/1/2022 through 9/30/2023
  • FY 2022 - No Change, effective from 10/1/2021 through 9/30/2022
  • FY 2021 - No Change, effective from 10/1/2020 through 9/30/2021
  • FY 2020 - No Change, effective from 10/1/2019 through 9/30/2020
  • FY 2019 - No Change, effective from 10/1/2018 through 9/30/2019
  • FY 2018 - No Change, effective from 10/1/2017 through 9/30/2018
  • FY 2017 - No Change, effective from 10/1/2016 through 9/30/2017
  • FY 2016 - New Code, effective from 10/1/2015 through 9/30/2016. This was the first year ICD-10-CM was implemented into the HIPAA code set.

Footnotes

[1] Chronic - a chronic condition code indicates a condition lasting 12 months or longer and its effect on the patient based on one or both of the following criteria:

  • The condition results in the need for ongoing intervention with medical products,treatment, services, and special equipment
  • The condition places limitations on self-care, independent living, and social interactions.