ICD-10-CM Code I42.0

Dilated cardiomyopathy

Version 2020 Billable Code

Valid for Submission

I42.0 is a billable code used to specify a medical diagnosis of dilated cardiomyopathy. The code is valid for the year 2020 for the submission of HIPAA-covered transactions. The ICD-10-CM code I42.0 might also be used to specify conditions or terms like cardiomyopathy in friedreich's ataxia, cardiomyopathy in myotonic dystrophy, cardiomyopathy with cataract and hip spine disease syndrome, congenital woolly hair, congestive obstructive cardiomyopathy, dilated cardiomyopathy, etc

ICD-10:I42.0
Short Description:Dilated cardiomyopathy
Long Description:Dilated cardiomyopathy

Tabular List of Diseases and Injuries

The Tabular List of Diseases and Injuries is a list of ICD-10 codes, organized "head to toe" into chapters and sections with guidance for inclusions, exclusions, descriptions and more. The following references are applicable to the code I42.0:

Inclusion Terms

Inclusion Terms
These terms are the conditions for which that code is to be used. The terms may be synonyms of the code title, or, in the case of "other specified" codes, the terms are a list of the various conditions assigned to that code. The inclusion terms are not necessarily exhaustive. Additional terms found only in the Alphabetic Index may also be assigned to a code.
  • Congestive cardiomyopathy

Index to Diseases and Injuries

The Index to Diseases and Injuries is an alphabetical listing of medical terms, with each term mapped to one or more ICD-10 code(s). The following references for the code I42.0 are found in the index:


Synonyms

The following clinical terms are approximate synonyms or lay terms that might be used to identify the correct diagnosis code:

  • Cardiomyopathy in Friedreich's ataxia
  • Cardiomyopathy in myotonic dystrophy
  • Cardiomyopathy with cataract and hip spine disease syndrome
  • Congenital woolly hair
  • Congestive obstructive cardiomyopathy
  • Dilated cardiomyopathy
  • Dilated cardiomyopathy 3B
  • Dilated cardiomyopathy associated with connective tissue disorder
  • Dilated cardiomyopathy due to systemic sclerosis
  • Dilated cardiomyopathy due to taurine deficiency
  • Dilated cardiomyopathy secondary to amyloidosis
  • Dilated cardiomyopathy secondary to bacterial myocarditis
  • Dilated cardiomyopathy secondary to deficiency
  • Dilated cardiomyopathy secondary to dermatomyositis
  • Dilated cardiomyopathy secondary to electrolyte deficiency
  • Dilated cardiomyopathy secondary to familial storage disease
  • Dilated cardiomyopathy secondary to Friedreich's ataxia
  • Dilated cardiomyopathy secondary to fungal myocarditis
  • Dilated cardiomyopathy secondary to glycogen storage disease
  • Dilated cardiomyopathy secondary to granuloma
  • Dilated cardiomyopathy secondary to hemochromatosis
  • Dilated cardiomyopathy secondary to infection
  • Dilated cardiomyopathy secondary to infection
  • Dilated cardiomyopathy secondary to infection
  • Dilated cardiomyopathy secondary to infiltration
  • Dilated cardiomyopathy secondary to infiltration
  • Dilated cardiomyopathy secondary to infiltration
  • Dilated cardiomyopathy secondary to malignancy
  • Dilated cardiomyopathy secondary to metabolic disorder
  • Dilated cardiomyopathy secondary to metazoal myocarditis
  • Dilated cardiomyopathy secondary to mucopolysaccharidosis
  • Dilated cardiomyopathy secondary to muscular dystrophy
  • Dilated cardiomyopathy secondary to myotonic dystrophy
  • Dilated cardiomyopathy secondary to neuromuscular disorder
  • Dilated cardiomyopathy secondary to nutritive deficiency
  • Dilated cardiomyopathy secondary to phytanic acid storage disease
  • Dilated cardiomyopathy secondary to polyarteritis nodosa
  • Dilated cardiomyopathy secondary to protozoal myocarditis
  • Dilated cardiomyopathy secondary to radiation
  • Dilated cardiomyopathy secondary to rheumatoid arthritis
  • Dilated cardiomyopathy secondary to sarcoidosis
  • Dilated cardiomyopathy secondary to viral myocarditis
  • Dilated cardiomyopathy with genetic marker
  • Dilated cardiomyopathy with hypergonadotropic hypogonadism syndrome
  • Familial cardiomyopathy
  • Familial cardiomyopathy
  • Familial cardiomyopathy
  • Familial dilated cardiomyopathy with conduction defect due to LMNA mutation
  • Heart disease due to ionizing radiation
  • Ischemic congestive cardiomyopathy
  • Ischemic congestive cardiomyopathy
  • Ischemic dilated cardiomyopathy due to coronary artery disease
  • Ischemic myocardial dysfunction
  • Ischemic myocardial dysfunction
  • Microcephalus cardiomyopathy syndrome
  • Nonischemic congestive cardiomyopathy
  • Nonsenile cataract
  • Primary dilated cardiomyopathy
  • Primary familial dilated cardiomyopathy
  • Primary idiopathic dilated cardiomyopathy
  • Secondary dilated cardiomyopathy
  • Secondary nonischemic congestive cardiomyopathy
  • Sensorineural deafness with dilated cardiomyopathy syndrome
  • Wooly hair
  • Wooly hair and palmoplantar keratoderma with dilated cardiomyopathy syndrome

Clinical Information

  • CARDIOMYOPATHY DILATED-. a form of cardiac muscle disease that is characterized by ventricular dilation ventricular dysfunction and heart failure. risk factors include smoking; alcohol drinking; hypertension; infection; pregnancy; and mutations in the lmna gene encoding lamin type a a nuclear lamina protein.

Diagnostic Related Groups

The ICD-10 code I42.0 is grouped in the following groups for version MS-DRG V37.0 What are Diagnostic Related Groups?
The Diagnostic Related Groups (DRGs) are a patient classification scheme which provides a means of relating the type of patients a hospital treats. The DRGs divides all possible principal diagnoses into mutually exclusive principal diagnosis areas referred to as Major Diagnostic Categories (MDC).
applicable from 10/01/2019 through 09/30/2020.

  • 314 - OTHER CIRCULATORY SYSTEM DIAGNOSES WITH MCC
  • 315 - OTHER CIRCULATORY SYSTEM DIAGNOSES WITH CC
  • 316 - OTHER CIRCULATORY SYSTEM DIAGNOSES WITHOUT CC/MCC

Convert I42.0 to ICD-9

  • 425.4 - Prim cardiomyopathy NEC (Approximate Flag)

Code Classification

  • Diseases of the circulatory system (I00–I99)
    • Other forms of heart disease (I30-I52)
      • Cardiomyopathy (I42)

Code History

  • FY 2016 - New Code, effective from 10/1/2015 through 9/30/2016
    (First year ICD-10-CM implemented into the HIPAA code set)
  • FY 2017 - No Change, effective from 10/1/2016 through 9/30/2017
  • FY 2018 - No Change, effective from 10/1/2017 through 9/30/2018
  • FY 2019 - No Change, effective from 10/1/2018 through 9/30/2019
  • FY 2020 - No Change, effective from 10/1/2019 through 9/30/2020

Information for Patients


Cardiomyopathy

Cardiomyopathy is the name for diseases of the heart muscle. These diseases enlarge your heart muscle or make it thicker and more rigid than normal. In rare cases, scar tissue replaces the muscle tissue.

Some people live long, healthy lives with cardiomyopathy. Some people don't even realize they have it. In others, however, it can make the heart less able to pump blood through the body. This can cause serious complications, including

  • Heart failure
  • Abnormal heart rhythms
  • Heart valve problems
  • Sudden cardiac arrest

Heart attacks, high blood pressure, infections, and other diseases can all cause cardiomyopathy. Some types of cardiomyopathy run in families. In many people, however, the cause is unknown. Treatment might involve medicines, surgery, other medical procedures, and lifestyle changes.

NIH: National Heart, Lung, and Blood Institute


[Learn More]

Familial dilated cardiomyopathy Familial dilated cardiomyopathy is a genetic form of heart disease. It occurs when heart (cardiac) muscle becomes thin and weakened in at least one chamber of the heart, causing the open area of the chamber to become enlarged (dilated). As a result, the heart is unable to pump blood as efficiently as usual. To compensate, the heart attempts to increase the amount of blood being pumped through the heart, leading to further thinning and weakening of the cardiac muscle. Over time, this condition results in heart failure.It usually takes many years for symptoms of familial dilated cardiomyopathy to cause health problems. They typically begin in mid-adulthood, but can occur at any time from infancy to late adulthood. Signs and symptoms of familial dilated cardiomyopathy can include an irregular heartbeat (arrhythmia), shortness of breath (dyspnea), extreme tiredness (fatigue), fainting episodes (syncope), and swelling of the legs and feet. In some cases, the first sign of the disorder is sudden cardiac death. The severity of the condition varies among affected individuals, even in members of the same family.
[Learn More]

X-linked dilated cardiomyopathy X-linked dilated cardiomyopathy is a form of heart disease. Dilated cardiomyopathy enlarges and weakens the heart (cardiac) muscle, preventing the heart from pumping blood efficiently. Signs and symptoms of this condition can include an irregular heartbeat (arrhythmia), shortness of breath, extreme tiredness (fatigue), and swelling of the legs and feet. In males with X-linked dilated cardiomyopathy, heart problems usually develop early in life and worsen quickly, leading to heart failure in adolescence or early adulthood. In affected females, the condition appears later in life and worsens more slowly.X-linked dilated cardiomyopathy is part of a spectrum of related conditions caused by mutations in the DMD gene. The other conditions in the spectrum, Duchenne and Becker muscular dystrophy, are characterized by progressive weakness and wasting of muscles used for movement (skeletal muscles) in addition to heart disease. People with X-linked dilated cardiomyopathy typically do not have any skeletal muscle weakness or wasting, although they may have subtle changes in their skeletal muscle cells that are detectable through laboratory testing. Based on these skeletal muscle changes, X-linked dilated cardiomyopathy is sometimes classified as subclinical Becker muscular dystrophy.
[Learn More]