Anemia (essential) (general) (hemoglobin deficiency) (infantile) (primary) (profound) - in the ICD-10-CM Index
Annotation Back-References in the 2025 ICD-10-CM Index to Diseases and Injuries
Browse the ICD-10-CM codes with references applicable to the clinical term "anemia (essential) (general) (hemoglobin deficiency) (infantile) (primary) (profound)"
Anemia (essential) (general) (hemoglobin deficiency) (infantile) (primary) (profound) - D64.9 Anemia, unspecified
achlorhydric - D50.8 Other iron deficiency anemias
achrestic - D53.1 Other megaloblastic anemias, not elsewhere classified
Addison (-Biermer) (pernicious) - D51.0 Vitamin B12 deficiency anemia due to intrinsic factor deficiency
agranulocytic - See: Agranulocytosis;
amino-acid-deficiency - D53.0 Protein deficiency anemia
aplastic - D61.9 Aplastic anemia, unspecified
congenital - D61.09 Other constitutional aplastic anemia
drug-induced - D61.1 Drug-induced aplastic anemia
due to
idiopathic - D61.3 Idiopathic aplastic anemia
red cell (pure) - D60.9 Acquired pure red cell aplasia, unspecified
specified type NEC - D61.89 Other specified aplastic anemias and other bone marrow failure syndromes
toxic - D61.2 Aplastic anemia due to other external agents
aregenerative
congenital - D61.09 Other constitutional aplastic anemia
asiderotic - D50.9 Iron deficiency anemia, unspecified
atypical (primary) - D64.9 Anemia, unspecified
Baghdad spring - D55.0 Anemia due to glucose-6-phosphate dehydrogenase [G6PD] deficiency
Balantidium coli - A07.0 Balantidiasis
Biermer's (pernicious) - D51.0 Vitamin B12 deficiency anemia due to intrinsic factor deficiency
blood loss (chronic) - D50.0 Iron deficiency anemia secondary to blood loss (chronic)
acute - D62 Acute posthemorrhagic anemia
bothriocephalus - B70.0 Diphyllobothriasis
brickmaker's - B76.9 Hookworm disease, unspecified
cerebral - I67.89 Other cerebrovascular disease
childhood - D58.9 Hereditary hemolytic anemia, unspecified
chlorotic - D50.8 Other iron deficiency anemias
chronic
chronica congenita aregenerativa - D61.09 Other constitutional aplastic anemia
combined system disease NEC - D51.0 Vitamin B12 deficiency anemia due to intrinsic factor deficiency
due to dietary vitamin B12 deficiency - D51.3 Other dietary vitamin B12 deficiency anemia
complicating pregnancy, childbirth or puerperium - See: Pregnancy, complicated by (management affected by), anemia;
congenital - P61.4 Other congenital anemias, not elsewhere classified
aplastic - D61.09 Other constitutional aplastic anemia
due to isoimmunization NOS - P55.9 Hemolytic disease of newborn, unspecified
dyserythropoietic, dyshematopoietic - D64.4 Congenital dyserythropoietic anemia
following fetal blood loss - P61.3 Congenital anemia from fetal blood loss
Heinz body - D58.2 Other hemoglobinopathies
hereditary hemolytic NOS - D58.9 Hereditary hemolytic anemia, unspecified
pernicious - D51.0 Vitamin B12 deficiency anemia due to intrinsic factor deficiency
spherocytic - D58.0 Hereditary spherocytosis
Cooley's (erythroblastic) - D56.1 Beta thalassemia
cytogenic - D51.0 Vitamin B12 deficiency anemia due to intrinsic factor deficiency
deficiency - D53.9 Nutritional anemia, unspecified
2, 3 diphosphoglycurate mutase - D55.29 Anemia due to other disorders of glycolytic enzymes
2, 3 PG - D55.29 Anemia due to other disorders of glycolytic enzymes
6 phosphogluconate dehydrogenase - D55.1 Anemia due to other disorders of glutathione metabolism
6-PGD - D55.1 Anemia due to other disorders of glutathione metabolism
amino-acid - D53.0 Protein deficiency anemia
combined B12 and folate - D53.1 Other megaloblastic anemias, not elsewhere classified
enzyme - D55.9 Anemia due to enzyme disorder, unspecified
drug-induced (hemolytic) - D59.2 Drug-induced nonautoimmune hemolytic anemia
glucose-6-phosphate dehydrogenase (G6PD) - D55.0 Anemia due to glucose-6-phosphate dehydrogenase [G6PD] deficiency
glycolytic - D55.29 Anemia due to other disorders of glycolytic enzymes
nucleotide metabolism - D55.3 Anemia due to disorders of nucleotide metabolism
specified type NEC - D55.8 Other anemias due to enzyme disorders
erythrocytic glutathione - D55.1 Anemia due to other disorders of glutathione metabolism
folate - D52.9 Folate deficiency anemia, unspecified
folic acid - D52.9 Folate deficiency anemia, unspecified
G SH - D55.1 Anemia due to other disorders of glutathione metabolism
G6PD - D55.0 Anemia due to glucose-6-phosphate dehydrogenase [G6PD] deficiency
GGS-R - D55.1 Anemia due to other disorders of glutathione metabolism
glucose-6-phosphate dehydrogenase - D55.0 Anemia due to glucose-6-phosphate dehydrogenase [G6PD] deficiency
glutathione reductase - D55.1 Anemia due to other disorders of glutathione metabolism
glyceraldehyde phosphate dehydrogenase - D55.29 Anemia due to other disorders of glycolytic enzymes
hexokinase - D55.29 Anemia due to other disorders of glycolytic enzymes
iron - D50.9 Iron deficiency anemia, unspecified
secondary to blood loss (chronic) - D50.0 Iron deficiency anemia secondary to blood loss (chronic)
nutritional - D53.9 Nutritional anemia, unspecified
phosphofructo-aldolase - D55.29 Anemia due to other disorders of glycolytic enzymes
phosphoglycerate kinase - D55.29 Anemia due to other disorders of glycolytic enzymes
PK - D55.21 Anemia due to pyruvate kinase deficiency
protein - D53.0 Protein deficiency anemia
pyruvate kinase - D55.21 Anemia due to pyruvate kinase deficiency
transcobalamin II - D51.2 Transcobalamin II deficiency
triose-phosphate isomerase - D55.29 Anemia due to other disorders of glycolytic enzymes
vitamin B12 NOS - D51.9 Vitamin B12 deficiency anemia, unspecified
Diamond-Blackfan (congenital hypoplastic) - D61.01 Constitutional (pure) red blood cell aplasia
dibothriocephalus - B70.0 Diphyllobothriasis
dimorphic - D53.1 Other megaloblastic anemias, not elsewhere classified
diphasic - D53.1 Other megaloblastic anemias, not elsewhere classified
Diphyllobothrium (Dibothriocephalus) - B70.0 Diphyllobothriasis
due to (in) (with)
antineoplastic chemotherapy - D64.81 Anemia due to antineoplastic chemotherapy
blood loss (chronic) - D50.0 Iron deficiency anemia secondary to blood loss (chronic)
acute - D62 Acute posthemorrhagic anemia
chemotherapy, antineoplastic - D64.81 Anemia due to antineoplastic chemotherapy
chronic disease classified elsewhere NEC - D63.8 Anemia in other chronic diseases classified elsewhere
chronic kidney disease - D63.1 Anemia in chronic kidney disease
deficiency
amino-acid - D53.0 Protein deficiency anemia
copper - D53.8 Other specified nutritional anemias
folate (folic acid) - D52.9 Folate deficiency anemia, unspecified
molybdenum - D53.8 Other specified nutritional anemias
protein - D53.0 Protein deficiency anemia
zinc - D53.8 Other specified nutritional anemias
dietary vitamin B12 deficiency - D51.3 Other dietary vitamin B12 deficiency anemia
disorder of
drug - See Also: Table of Drugs and Chemicals; See: Anemia, by type;
end stage renal disease - D63.1 Anemia in chronic kidney disease
enzyme disorder - D55.9 Anemia due to enzyme disorder, unspecified
fetal blood loss - P61.3 Congenital anemia from fetal blood loss
fish tapeworm (D.latum) infestation - B70.0 Diphyllobothriasis
hemorrhage (chronic) - D50.0 Iron deficiency anemia secondary to blood loss (chronic)
acute - D62 Acute posthemorrhagic anemia
impaired absorption - D50.9 Iron deficiency anemia, unspecified
loss of blood (chronic) - D50.0 Iron deficiency anemia secondary to blood loss (chronic)
acute - D62 Acute posthemorrhagic anemia
myxedema - E03.9 Hypothyroidism, unspecified
Necator americanus - B76.1 Necatoriasis
prematurity - P61.2 Anemia of prematurity
selective vitamin B12 malabsorption with proteinuria - D51.1 Vitamin B12 deficiency anemia due to selective vitamin B12 malabsorption with proteinuria
transcobalamin II deficiency - D51.2 Transcobalamin II deficiency
Dyke-Young type (secondary) (symptomatic) - D59.19 Other autoimmune hemolytic anemia
dyserythropoietic (congenital) - D64.4 Congenital dyserythropoietic anemia
dyshematopoietic (congenital) - D64.4 Congenital dyserythropoietic anemia
Egyptian - B76.9 Hookworm disease, unspecified
elliptocytosis - See: Elliptocytosis;
enzyme-deficiency, drug-induced - D59.2 Drug-induced nonautoimmune hemolytic anemia
epidemic - See Also: Ancylostomiasis; - B76.9 Hookworm disease, unspecified
erythroblastic
erythrocytic glutathione deficiency - D55.1 Anemia due to other disorders of glutathione metabolism
erythropoietin-resistant anemia (EPO resistant anemia) - D63.1 Anemia in chronic kidney disease
Faber's (achlorhydric anemia) - D50.9 Iron deficiency anemia, unspecified
factitious (self-induced blood letting) - D50.0 Iron deficiency anemia secondary to blood loss (chronic)
familial erythroblastic - D56.1 Beta thalassemia
Fanconi ('s) - D61.03 Fanconi anemia
favism - D55.0 Anemia due to glucose-6-phosphate dehydrogenase [G6PD] deficiency
fish tapeworm (D. latum) infestation - B70.0 Diphyllobothriasis
folate (folic acid) deficiency - D52.9 Folate deficiency anemia, unspecified
glucose-6-phosphate dehydrogenase (G6PD) deficiency - D55.0 Anemia due to glucose-6-phosphate dehydrogenase [G6PD] deficiency
glutathione-reductase deficiency - D55.1 Anemia due to other disorders of glutathione metabolism
goat's milk - D52.0 Dietary folate deficiency anemia
granulocytic - See: Agranulocytosis;
Heinz body, congenital - D58.2 Other hemoglobinopathies
hemolytic - D58.9 Hereditary hemolytic anemia, unspecified
acquired - D59.9 Acquired hemolytic anemia, unspecified
autoimmune NEC - D59.19 Other autoimmune hemolytic anemia
infectious - D59.4 Other nonautoimmune hemolytic anemias
specified type NEC - D59.8 Other acquired hemolytic anemias
toxic - D59.4 Other nonautoimmune hemolytic anemias
with hemoglobinuria NEC - D59.6 Hemoglobinuria due to hemolysis from other external causes
acute - D59.9 Acquired hemolytic anemia, unspecified
autoimmune - D59.10 Autoimmune hemolytic anemia, unspecified
chronic - D58.9 Hereditary hemolytic anemia, unspecified
idiopathic - D59.9 Acquired hemolytic anemia, unspecified
cold type (primary) (secondary) (symptomatic) - D59.12 Cold autoimmune hemolytic anemia
congenital (spherocytic) - See: Spherocytosis;
due to
cardiac conditions - D59.4 Other nonautoimmune hemolytic anemias
drugs (nonautoimmune) - D59.2 Drug-induced nonautoimmune hemolytic anemia
autoimmune - D59.0 Drug-induced autoimmune hemolytic anemia
enzyme disorder - D55.9 Anemia due to enzyme disorder, unspecified
drug-induced - D59.2 Drug-induced nonautoimmune hemolytic anemia
presence of shunt or other internal prosthetic device - D59.4 Other nonautoimmune hemolytic anemias
familial - D58.9 Hereditary hemolytic anemia, unspecified
hereditary - D58.9 Hereditary hemolytic anemia, unspecified
idiopathic (chronic) - D59.9 Acquired hemolytic anemia, unspecified
mechanical - D59.4 Other nonautoimmune hemolytic anemias
microangiopathic - D59.4 Other nonautoimmune hemolytic anemias
mixed type (primary) (secondary) (symptomatic) - D59.13 Mixed type autoimmune hemolytic anemia
nonautoimmune - D59.4 Other nonautoimmune hemolytic anemias
drug-induced - D59.2 Drug-induced nonautoimmune hemolytic anemia
nonspherocytic
primary
secondary - D59.4 Other nonautoimmune hemolytic anemias
specified (hereditary) type NEC - D58.8 Other specified hereditary hemolytic anemias
Stransky-Regala type - See Also: Hemoglobinopathy; - D58.8 Other specified hereditary hemolytic anemias
symptomatic - D59.4 Other nonautoimmune hemolytic anemias
toxic - D59.4 Other nonautoimmune hemolytic anemias
warm type (primary) (secondary) (symptomatic) - D59.11 Warm autoimmune hemolytic anemia
hemorrhagic (chronic) - D50.0 Iron deficiency anemia secondary to blood loss (chronic)
acute - D62 Acute posthemorrhagic anemia
Herrick's - D57.1 Sickle-cell disease without crisis
hexokinase deficiency - D55.29 Anemia due to other disorders of glycolytic enzymes
hookworm - B76.9 Hookworm disease, unspecified
hypochromic (idiopathic) (microcytic) (normoblastic) - D50.9 Iron deficiency anemia, unspecified
due to blood loss (chronic) - D50.0 Iron deficiency anemia secondary to blood loss (chronic)
acute - D62 Acute posthemorrhagic anemia
familial sex-linked - D64.0 Hereditary sideroblastic anemia
pyridoxine-responsive - D64.3 Other sideroblastic anemias
sideroblastic, sex-linked - D64.0 Hereditary sideroblastic anemia
hypoplasia, red blood cells - D61.9 Aplastic anemia, unspecified
congenital or familial - D61.01 Constitutional (pure) red blood cell aplasia
hypoplastic (idiopathic) - D61.9 Aplastic anemia, unspecified
congenital or familial (of childhood) - D61.01 Constitutional (pure) red blood cell aplasia
hypoproliferative (refractive) - D61.9 Aplastic anemia, unspecified
idiopathic - D64.9 Anemia, unspecified
in (due to) (with)
intertropical - See Also: Ancylostomiasis; - D63.8 Anemia in other chronic diseases classified elsewhere
iron deficiency - D50.9 Iron deficiency anemia, unspecified
Joseph-Diamond-Blackfan (congenital hypoplastic) - D61.01 Constitutional (pure) red blood cell aplasia
Lederer's (hemolytic) - D59.19 Other autoimmune hemolytic anemia
leukoerythroblastic - D61.82 Myelophthisis
macrocytic - D53.9 Nutritional anemia, unspecified
malarial - See Also: Malaria; - B54 Unspecified malaria
malignant (progressive) - D51.0 Vitamin B12 deficiency anemia due to intrinsic factor deficiency
malnutrition - D53.9 Nutritional anemia, unspecified
marsh - See Also: Malaria; - B54 Unspecified malaria
Mediterranean (with other hemoglobinopathy) - D56.9 Thalassemia, unspecified
megaloblastic - D53.1 Other megaloblastic anemias, not elsewhere classified
combined B12 and folate deficiency - D53.1 Other megaloblastic anemias, not elsewhere classified
hereditary - D51.1 Vitamin B12 deficiency anemia due to selective vitamin B12 malabsorption with proteinuria
nutritional - D52.0 Dietary folate deficiency anemia
orotic aciduria - D53.0 Protein deficiency anemia
refractory - D53.1 Other megaloblastic anemias, not elsewhere classified
specified type NEC - D53.1 Other megaloblastic anemias, not elsewhere classified
megalocytic - D53.1 Other megaloblastic anemias, not elsewhere classified
microcytic (hypochromic) - D50.9 Iron deficiency anemia, unspecified
microdrepanocytosis - D57.40 Sickle-cell thalassemia without crisis
microelliptopoikilocytic (Rietti-Greppi- Micheli) - D56.9 Thalassemia, unspecified
miner's - B76.9 Hookworm disease, unspecified
myelodysplastic - D46.9 Myelodysplastic syndrome, unspecified
myelofibrosis - D75.81 Myelofibrosis
myelogenous - D64.89 Other specified anemias
myelopathic - D64.89 Other specified anemias
myelophthisic - D61.82 Myelophthisis
myeloproliferative - D47.Z9 Other specified neoplasms of uncertain behavior of lymphoid, hematopoietic and related tissue
newborn - P61.4 Other congenital anemias, not elsewhere classified
nonspherocytic hemolytic - See: Anemia, hemolytic, nonspherocytic;
normocytic (infectional) - D64.9 Anemia, unspecified
nutritional (deficiency) - D53.9 Nutritional anemia, unspecified
of prematurity - P61.2 Anemia of prematurity
orotaciduric (congenital) (hereditary) - D53.0 Protein deficiency anemia
osteosclerotic - D64.89 Other specified anemias
ovalocytosis (hereditary) - See: Elliptocytosis;
paludal - See Also: Malaria; - B54 Unspecified malaria
pernicious (congenital) (malignant) (progressive) - D51.0 Vitamin B12 deficiency anemia due to intrinsic factor deficiency
pleochromic - D64.89 Other specified anemias
of sprue - D52.8 Other folate deficiency anemias
posthemorrhagic (chronic) - D50.0 Iron deficiency anemia secondary to blood loss (chronic)
postoperative (postprocedural)
postpartum - O90.81 Anemia of the puerperium
pressure - D64.89 Other specified anemias
progressive - D64.9 Anemia, unspecified
protein-deficiency - D53.0 Protein deficiency anemia
pseudoleukemica infantum - D64.89 Other specified anemias
pure red cell - D60.9 Acquired pure red cell aplasia, unspecified
congenital - D61.01 Constitutional (pure) red blood cell aplasia
pyridoxine-responsive - D64.3 Other sideroblastic anemias
pyruvate kinase deficiency - D55.21 Anemia due to pyruvate kinase deficiency
refractory - D46.4 Refractory anemia, unspecified
megaloblastic - D53.1 Other megaloblastic anemias, not elsewhere classified
sideroblastic - D46.1 Refractory anemia with ring sideroblasts
sideropenic - D50.9 Iron deficiency anemia, unspecified
with
without ring sideroblasts, so stated - D46.0 Refractory anemia without ring sideroblasts, so stated
without sideroblasts without excess of blasts - D46.0 Refractory anemia without ring sideroblasts, so stated
Rietti-Greppi-Micheli - D56.9 Thalassemia, unspecified
scorbutic - D53.2 Scorbutic anemia
secondary to
semiplastic - D61.89 Other specified aplastic anemias and other bone marrow failure syndromes
sickle-cell - See: Disease, sickle-cell;
sideroblastic - D64.3 Other sideroblastic anemias
hereditary - D64.0 Hereditary sideroblastic anemia
hypochromic, sex-linked - D64.0 Hereditary sideroblastic anemia
pyridoxine-responsive NEC - D64.3 Other sideroblastic anemias
refractory - D46.1 Refractory anemia with ring sideroblasts
secondary (due to)
specified type NEC - D64.3 Other sideroblastic anemias
sideropenic (refractory) - D50.9 Iron deficiency anemia, unspecified
simple chronic - D53.9 Nutritional anemia, unspecified
specified type NEC - D64.89 Other specified anemias
spherocytic (hereditary) - See: Spherocytosis;
splenic - D64.89 Other specified anemias
splenomegalic - D64.89 Other specified anemias
stomatocytosis - D58.8 Other specified hereditary hemolytic anemias
syphilitic (acquired) (late) - A52.79 Other symptomatic late syphilis
target cell - D64.89 Other specified anemias
thalassemia - D56.9 Thalassemia, unspecified
thrombocytopenic - See: Thrombocytopenia;
toxic - D61.2 Aplastic anemia due to other external agents
tropical - B76.9 Hookworm disease, unspecified
macrocytic - D52.8 Other folate deficiency anemias
tuberculous - A18.89 Tuberculosis of other sites
vegan - D51.3 Other dietary vitamin B12 deficiency anemia
vitamin
von Jaksch's - D64.89 Other specified anemias
with (due to) (in)
Witts' (achlorhydric anemia) - D50.8 Other iron deficiency anemias
Applicable Clinical Terms Definitions
Favism: Hemolytic anemia due to the ingestion of fava beans or after inhalation of pollen from the Vicia fava plant by persons with glucose-6-phosphate dehydrogenase deficient erythrocytes.
Ancylostomatoidea: A superfamily of nematode parasitic hookworms consisting of four genera: ANCYLOSTOMA; NECATOR; Bunostomum; and Uncinaria. ANCYLOSTOMA and NECATOR occur in humans and other mammals. Bunostomum is common in ruminants and Uncinaria in wolves, foxes, and dogs.
Malnutrition: An imbalanced nutritional status resulting from insufficient intake of nutrients to meet normal physiological requirement.
Primary Myelofibrosis: A de novo myeloproliferation arising from an abnormal stem cell. It is characterized by the replacement of bone marrow by fibrous tissue, a process that is mediated by CYTOKINES arising from the abnormal clone.
Infant, Newborn: An infant during the first 28 days after birth.
Postpartum Period: In females, the period that is shortly after giving birth (PARTURITION).
Pressure: A type of stress exerted uniformly in all directions. Its measure is the force exerted per unit area. (McGraw-Hill Dictionary of Scientific and Technical Terms, 6th ed)
Thalassemia: A group of hereditary hemolytic anemias in which there is decreased synthesis of one or more hemoglobin polypeptide chains. There are several genetic types with clinical pictures ranging from barely detectable hematologic abnormality to severe and fatal anemia.
Vitamins: Organic substances that are required in small amounts for maintenance and growth, but which cannot be manufactured by the human body.