2021 ICD-10-CM Code L10

Pemphigus

Version 2021

Not Valid for Submission

L10 is a non-specific and non-billable diagnosis code code, consider using a code with a higher level of specificity for a diagnosis of pemphigus. The code is not specific and is NOT valid for the year 2021 for the submission of HIPAA-covered transactions. Category or Header define the heading of a category of codes that may be further subdivided by the use of 4th, 5th, 6th or 7th characters.

ICD-10:L10
Short Description:Pemphigus
Long Description:Pemphigus

Code Classification

Specific Coding for Pemphigus

Non-specific codes like L10 require more digits to indicate the appropriate level of specificity. Consider using any of the following ICD-10 codes with a higher level of specificity when coding for pemphigus:

  • BILLABLE CODE - Use L10.0 for Pemphigus vulgaris
  • BILLABLE CODE - Use L10.1 for Pemphigus vegetans
  • BILLABLE CODE - Use L10.2 for Pemphigus foliaceous
  • BILLABLE CODE - Use L10.3 for Brazilian pemphigus [fogo selvagem]
  • BILLABLE CODE - Use L10.4 for Pemphigus erythematosus
  • BILLABLE CODE - Use L10.5 for Drug-induced pemphigus
  • NON-BILLABLE CODE - L10.8 for Other pemphigus
  • BILLABLE CODE - Use L10.81 for Paraneoplastic pemphigus
  • BILLABLE CODE - Use L10.89 for Other pemphigus
  • BILLABLE CODE - Use L10.9 for Pemphigus, unspecified

Tabular List of Diseases and Injuries

The Tabular List of Diseases and Injuries is a list of ICD-10 codes, organized "head to toe" into chapters and sections with coding notes and guidance for inclusions, exclusions, descriptions and more. The following references are applicable to the code L10:


Type 1 Excludes

Type 1 Excludes
A type 1 excludes note is a pure excludes note. It means "NOT CODED HERE!" An Excludes1 note indicates that the code excluded should never be used at the same time as the code above the Excludes1 note. An Excludes1 is used when two conditions cannot occur together, such as a congenital form versus an acquired form of the same condition.

Clinical Information

Information for Patients


Pemphigus

Pemphigus is an autoimmune disorder. If you have it, your immune system attacks healthy cells in your skin and mouth, causing blisters and sores. No one knows the cause. Pemphigus does not spread from person to person. It does not appear to be inherited. But some people's genes put them more at risk for pemphigus.

Pemphigoid is also an autoimmune skin disease. It leads to deep blisters that do not break easily. Pemphigoid is most common in older adults and may be fatal for older, sick patients.

Doctors diagnose pemphigus with a physical exam, a biopsy, and blood tests. The treatment of pemphigus and pemphigoid is the same: one or more medicines to control symptoms. These may include

NIH: National Institute of Arthritis and Musculoskeletal and Skin Diseases


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Code History

  • FY 2021 - No Change, effective from 10/1/2020 through 9/30/2021
  • FY 2020 - No Change, effective from 10/1/2019 through 9/30/2020
  • FY 2019 - No Change, effective from 10/1/2018 through 9/30/2019
  • FY 2018 - No Change, effective from 10/1/2017 through 9/30/2018
  • FY 2017 - No Change, effective from 10/1/2016 through 9/30/2017
  • FY 2016 - New Code, effective from 10/1/2015 through 9/30/2016 (First year ICD-10-CM implemented into the HIPAA code set)