2022 ICD-10-CM Code M04

Autoinflammatory syndromes

Version 2021

Not Valid for Submission

ICD-10:M04
Short Description:Autoinflammatory syndromes
Long Description:Autoinflammatory syndromes

Code Classification

  • Diseases of the musculoskeletal system and connective tissue (M00–M99)
    • Autoinflammatory syndromes (M04)
      • Autoinflammatory syndromes (M04)

M04 is a non-specific and non-billable diagnosis code code, consider using a code with a higher level of specificity for a diagnosis of autoinflammatory syndromes. The code is not specific and is NOT valid for the year 2022 for the submission of HIPAA-covered transactions. Category or Header define the heading of a category of codes that may be further subdivided by the use of 4th, 5th, 6th or 7th characters.

Specific Coding for Autoinflammatory syndromes

Non-specific codes like M04 require more digits to indicate the appropriate level of specificity. Consider using any of the following ICD-10 codes with a higher level of specificity when coding for autoinflammatory syndromes:

  • BILLABLE CODE - Use M04.1 for Periodic fever syndromes
  • BILLABLE CODE - Use M04.2 for Cryopyrin-associated periodic syndromes
  • BILLABLE CODE - Use M04.8 for Other autoinflammatory syndromes
  • BILLABLE CODE - Use M04.9 for Autoinflammatory syndrome, unspecified

Tabular List of Diseases and Injuries

The Tabular List of Diseases and Injuries is a list of ICD-10 codes, organized "head to toe" into chapters and sections with coding notes and guidance for inclusions, exclusions, descriptions and more. The following references are applicable to the code M04:


Type 2 Excludes

Type 2 Excludes
A type 2 excludes note represents "Not included here". An excludes2 note indicates that the condition excluded is not part of the condition represented by the code, but a patient may have both conditions at the same time. When an Excludes2 note appears under a code, it is acceptable to use both the code and the excluded code together, when appropriate.

Code History

  • FY 2021 - No Change, effective from 10/1/2020 through 9/30/2021
  • FY 2020 - No Change, effective from 10/1/2019 through 9/30/2020
  • FY 2019 - No Change, effective from 10/1/2018 through 9/30/2019
  • FY 2018 - No Change, effective from 10/1/2017 through 9/30/2018