ICD-10 Diagnosis Code M04.1

Diagnostic Related Groups
The diagnosis code M04.1 is grouped in the following Diagnostic Related Group(s) (MS-DRG V35.0)

• 545 - CONNECTIVE TISSUE DISORDERS WITH MCC
• 546 - CONNECTIVE TISSUE DISORDERS WITH CC
• 547 - CONNECTIVE TISSUE DISORDERS WITHOUT CC/MCC

Convert to ICD-9 General Equivalence Map
The ICD-10 and ICD-9 GEMs are used to facilitate linking between the diagnosis codes in ICD-9-CM and the new ICD-10-CM code set. The GEMs are the raw material from which providers, health information vendors and payers can derive specific applied mappings to meet their needs.

• 277.31 - Fam Mediterranean fever (approximate) Approximate Flag
  The approximate flag is on, indicating that the relationship between the code in the source system and the code in the target system is an approximate equivalent.

Synonyms

• Amyloid of familial Mediterranean fever
• Aphthous ulcer of mouth
• Deficiency of mevalonate kinase
• Familial Mediterranean fever
• Hereditary inflammatory disorder involving skin
• Hereditary periodic fever
• Hyper-IgD periodic fever syndrome
• Inflammatory hereditary disorder
• Pericarditis associated with familial Mediterranean fever
• Pericarditis due to metabolic disease
• PFAPA syndrome
• TNF receptor-associated periodic fever syndrome

Index of Diseases and Injuries
References found for the code M04.1 in the Index of Diseases and Injuries:

• Inclusion Terms: Inclusion terms
  List of terms is included under some codes. These terms are the conditions for which that code is to be used. The terms may be synonyms of the code title, or, in the case of "other specified" codes, the terms are a list of the various conditions assigned to that code. The inclusion terms are not necessarily exhaustive. Additional terms found only in the Alphabetic Index may also be assigned to a code.
  • Familial Mediterranean fever
  • Hyperimmunoglobin D syndrome
  • Mevalonate kinase deficiency
  • Tumor NEC NEC "Not elsewhere classifiable"
    This abbreviation in the Alphabetic Index represents "other specified". When a specific code is not available for a condition, the Alphabetic Index directs the coder to the "other specified” code in the Tabular List.rosis factor receptor associated periodic syndrome [TRAPS]

Replacement Code Replacement Code
The National Center for Health Statistics (NCHS) has published an update to the ICD-10-CM diagnosis codes which became effective October 1, 2018. This is a new and revised code for the FY 2019 (October 1, 2018-September 30, 2019).
This code replaces the following previously assigned ICD-10 code(s) listed below:

• E85.0 - Non-neuropathic heredofamilial amyloidosis