M04.1 - Periodic fever syndromes
| ICD-10: | M04.1 |
| Short Description: | Periodic fever syndromes |
| Long Description: | Periodic fever syndromes |
| Status: | Valid for Submission |
| Version: | ICD-10-CM 2023 |
| Code Classification: |
M04.1 is a billable ICD-10 code used to specify a medical diagnosis of periodic fever syndromes. The code is valid during the fiscal year 2023 from October 01, 2022 through September 30, 2023 for the submission of HIPAA-covered transactions.
Approximate Synonyms
The following clinical terms are approximate synonyms or lay terms that might be used to identify the correct diagnosis code:
- Amyloid of familial Mediterranean fever
- Aphthous ulcer of mouth
- Congenital sideroblastic anemia, B-cell immunodeficiency, periodic fever, developmental delay syndrome
- Deficiency of mevalonate kinase
- Familial Mediterranean fever
- Hereditary periodic fever
- Hyper-IgD periodic fever syndrome
- Menstrual cycle dependent periodic fever
- NLRP12-associated hereditary periodic fever syndrome
- Pericarditis due to familial Mediterranean fever
- PFAPA syndrome
- Recurrent aphthous ulcer
- Recurrent ulcer of mouth
- Secondary systemic amyloidosis
- TNF receptor-associated periodic fever syndrome
Clinical Information
- Familial Mediterranean Fever-. a group of hereditary autoinflammation diseases, characterized by recurrent fever, abdominal pain, headache, rash, pleurisy; and arthritis. orchitis; benign meningitis; and amyloidosis may also occur. homozygous or compound heterozygous mutations in marenostrin gene encoding pyrin result in autosomal recessive transmission; simple heterozygous, autosomal dominant form of the disease also exists with mutations in the same gene.
Tabular List of Diseases and Injuries
The Tabular List of Diseases and Injuries is a list of ICD-10 codes, organized "head to toe" into chapters and sections with coding notes and guidance for inclusions, exclusions, descriptions and more. The following references are applicable to this diagnosis code:
Inclusion Terms
Inclusion TermsThese terms are the conditions for which that code is to be used. The terms may be synonyms of the code title, or, in the case of "other specified" codes, the terms are a list of the various conditions assigned to that code. The inclusion terms are not necessarily exhaustive. Additional terms found only in the Alphabetic Index may also be assigned to a code.
- Familial Mediterranean fever
- Hyperimmunoglobin D syndrome
- Mevalonate kinase deficiency
- Tumor necrosis factor receptor associated periodic syndrome TRAPS
Index to Diseases and Injuries References
The Index to Diseases and Injuries is an alphabetical listing of medical terms, with each term mapped to one or more ICD-10 code(s). The following references for this diagnosis code are found in the injuries and diseases index:
- - Arthritis, arthritic (acute) (chronic) (nonpyogenic) (subacute) - M19.90
- - in (due to)
- - Mediterranean fever, familial - See Also: subcategory M14.8-; - M04.1
- - in (due to)
- - Deficiency, deficient
- - mevalonate kinase - M04.1
- - Fever (inanition) (of unknown origin) (persistent) (with chills) (with rigor) - R50.9
- - Mediterranean - See Also: Brucellosis; - A23.9
- - familial - M04.1
- - periodic (Mediterranean) - M04.1
- - Mediterranean - See Also: Brucellosis; - A23.9
- - Syndrome - See Also: Disease;
- - hyperimmunoglobulin D - M04.1
- - periodic fever - M04.1
- - tumor necrosis factor receptor associated periodic (TRAPS) - M04.1
Replacement Code
M041 replaces the following previously assigned ICD-10 code(s):
- E85.0 - Non-neuropathic heredofamilial amyloidosis
Convert to ICD-9 Code
| Source ICD-10 Code | Target ICD-9 Code | |
|---|---|---|
| M04.1 | 277.31 - Fam Mediterranean fever | |
| Approximate Flag - The approximate mapping means there is not an exact match between the ICD-10 and ICD-9 codes and the mapped code is not a precise representation of the original code. | ||
Code History
- FY 2023 - No Change, effective from 10/1/2022 through 9/30/2023
- FY 2022 - No Change, effective from 10/1/2021 through 9/30/2022
- FY 2021 - No Change, effective from 10/1/2020 through 9/30/2021
- FY 2020 - No Change, effective from 10/1/2019 through 9/30/2020
- FY 2019 - No Change, effective from 10/1/2018 through 9/30/2019
- FY 2018 - No Change, effective from 10/1/2017 through 9/30/2018
