2021 ICD-10-CM Code M04.1

Tabular List of Diseases and Injuries

The Tabular List of Diseases and Injuries is a list of ICD-10 codes, organized "head to toe" into chapters and sections with guidance for inclusions, exclusions, descriptions and more. The following references are applicable to the code M04.1:

Inclusion Terms

• Familial Mediterranean fever
• Hyperimmunoglobin D syndrome
• Mevalonate kinase deficiency
• Tumor necrosis factor receptor associated periodic syndrome TRAPS

Index to Diseases and Injuries

The Index to Diseases and Injuries is an alphabetical listing of medical terms, with each term mapped to one or more ICD-10 code(s). The following references for the code M04.1 are found in the index:

• - Arthritis, arthritic (acute) (chronic) (nonpyogenic) (subacute) - M19.90
  • - in (due to)
    • - Mediterranean fever, familial - See Also: subcategory M14.8-; - M04.1

• - Deficiency, deficient
  • - mevalonate kinase - M04.1

• - Fever (inanition) (of unknown origin) (persistent) (with chills) (with rigor) - R50.9
  • - Mediterranean - See Also: Brucellosis; - A23.9
    • - familial - M04.1
  • - periodic (Mediterranean) - M04.1

• - Mediterranean
  • - fever - See: Brucellosis;
    • - familial - M04.1

• - Syndrome - See Also: Disease;
  • - hyperimmunoglobulin D - M04.1
  • - periodic fever - M04.1
  • - tumor necrosis factor receptor associated periodic (TRAPS) - M04.1

• - TRAPS (tumor necrosis factor receptor associated periodic syndrome) - M04.1

Approximate Synonyms

The following clinical terms are approximate synonyms or lay terms that might be used to identify the correct diagnosis code:

• Amyloid of familial Mediterranean fever
• Aphthous ulcer of mouth
• Congenital sideroblastic anemia, B-cell immunodeficiency, periodic fever, developmental delay syndrome
• Deficiency of mevalonate kinase
• Familial Mediterranean fever
• Hereditary periodic fever
• Hyper-IgD periodic fever syndrome
• NLRP12-associated hereditary periodic fever syndrome
• Pericarditis due to familial Mediterranean fever
• PFAPA syndrome
• Recurrent aphthous ulcer
• Recurrent ulcer of mouth
• TNF receptor-associated periodic fever syndrome