2021 ICD-10-CM Code M04.1
Periodic fever syndromes
Valid for Submission
M04.1 is a billable diagnosis code used to specify a medical diagnosis of periodic fever syndromes. The code M04.1 is valid during the fiscal year 2021 from October 01, 2020 through September 30, 2021 for the submission of HIPAA-covered transactions.
The ICD-10-CM code M04.1 might also be used to specify conditions or terms like amyloid of familial mediterranean fever, aphthous ulcer of mouth, congenital sideroblastic anemia, b-cell immunodeficiency, periodic fever, developmental delay syndrome, deficiency of mevalonate kinase, familial mediterranean fever , hereditary periodic fever, etc.
Code Classification
Tabular List of Diseases and Injuries
The Tabular List of Diseases and Injuries is a list of ICD-10 codes, organized "head to toe" into chapters and sections with guidance for inclusions, exclusions, descriptions and more. The following references are applicable to the code M04.1:
Inclusion Terms
Inclusion TermsThese terms are the conditions for which that code is to be used. The terms may be synonyms of the code title, or, in the case of "other specified" codes, the terms are a list of the various conditions assigned to that code. The inclusion terms are not necessarily exhaustive. Additional terms found only in the Alphabetic Index may also be assigned to a code.
- Familial Mediterranean fever
- Hyperimmunoglobin D syndrome
- Mevalonate kinase deficiency
- Tumor necrosis factor receptor associated periodic syndrome TRAPS
Index to Diseases and Injuries
The Index to Diseases and Injuries is an alphabetical listing of medical terms, with each term mapped to one or more ICD-10 code(s). The following references for the code M04.1 are found in the index:
- - Arthritis, arthritic (acute) (chronic) (nonpyogenic) (subacute) - M19.90
- - in (due to)
- - Mediterranean fever, familial - See Also: subcategory M14.8-; - M04.1
- - in (due to)
- - Deficiency, deficient
- - mevalonate kinase - M04.1
- - Fever (inanition) (of unknown origin) (persistent) (with chills) (with rigor) - R50.9
- - Mediterranean - See Also: Brucellosis; - A23.9
- - familial - M04.1
- - periodic (Mediterranean) - M04.1
- - Mediterranean - See Also: Brucellosis; - A23.9
- - Syndrome - See Also: Disease;
- - hyperimmunoglobulin D - M04.1
- - periodic fever - M04.1
- - tumor necrosis factor receptor associated periodic (TRAPS) - M04.1
Approximate Synonyms
The following clinical terms are approximate synonyms or lay terms that might be used to identify the correct diagnosis code:
- Amyloid of familial Mediterranean fever
- Aphthous ulcer of mouth
- Congenital sideroblastic anemia, B-cell immunodeficiency, periodic fever, developmental delay syndrome
- Deficiency of mevalonate kinase
- Familial Mediterranean fever
- Hereditary periodic fever
- Hyper-IgD periodic fever syndrome
- NLRP12-associated hereditary periodic fever syndrome
- Pericarditis due to familial Mediterranean fever
- PFAPA syndrome
- Recurrent aphthous ulcer
- Recurrent ulcer of mouth
- TNF receptor-associated periodic fever syndrome
Diagnostic Related Groups - MS-DRG Mapping
The ICD-10 code M04.1 is grouped in the following groups for version MS-DRG V38.0 What are Diagnostic Related Groups?
The Diagnostic Related Groups (DRGs) are a patient classification scheme which provides a means of relating the type of patients a hospital treats. The DRGs divides all possible principal diagnoses into mutually exclusive principal diagnosis areas referred to as Major Diagnostic Categories (MDC). applicable from 10/01/2020 through 09/30/2021.
Replacement Code
M041 replaces the following previously assigned ICD-10 code(s):
- E85.0 - Non-neuropathic heredofamilial amyloidosis
Convert M04.1 to ICD-9 Code
The General Equivalency Mapping (GEM) crosswalk indicates an approximate mapping between the ICD-10 code M04.1 its ICD-9 equivalent. The approximate mapping means there is not an exact match between the ICD-10 code and the ICD-9 code and the mapped code is not a precise representation of the original code.
- 277.31 - Fam Mediterranean fever (Approximate Flag)
Code History
- FY 2021 - No Change, effective from 10/1/2020 through 9/30/2021
- FY 2020 - No Change, effective from 10/1/2019 through 9/30/2020
- FY 2019 - No Change, effective from 10/1/2018 through 9/30/2019
- FY 2018 - No Change, effective from 10/1/2017 through 9/30/2018