2021 ICD-10-CM Code M04.1

Periodic fever syndromes

Version 2021
Billable Code
MS-DRG Mapping

Valid for Submission

M04.1 is a billable diagnosis code used to specify a medical diagnosis of periodic fever syndromes. The code M04.1 is valid during the fiscal year 2021 from October 01, 2020 through September 30, 2021 for the submission of HIPAA-covered transactions.

The ICD-10-CM code M04.1 might also be used to specify conditions or terms like amyloid of familial mediterranean fever, aphthous ulcer of mouth, congenital sideroblastic anemia, b-cell immunodeficiency, periodic fever, developmental delay syndrome, deficiency of mevalonate kinase, familial mediterranean fever , hereditary periodic fever, etc.

ICD-10:M04.1
Short Description:Periodic fever syndromes
Long Description:Periodic fever syndromes

Code Classification

Tabular List of Diseases and Injuries

The Tabular List of Diseases and Injuries is a list of ICD-10 codes, organized "head to toe" into chapters and sections with guidance for inclusions, exclusions, descriptions and more. The following references are applicable to the code M04.1:


Inclusion Terms

Inclusion Terms
These terms are the conditions for which that code is to be used. The terms may be synonyms of the code title, or, in the case of "other specified" codes, the terms are a list of the various conditions assigned to that code. The inclusion terms are not necessarily exhaustive. Additional terms found only in the Alphabetic Index may also be assigned to a code.

Index to Diseases and Injuries

The Index to Diseases and Injuries is an alphabetical listing of medical terms, with each term mapped to one or more ICD-10 code(s). The following references for the code M04.1 are found in the index:

Approximate Synonyms

The following clinical terms are approximate synonyms or lay terms that might be used to identify the correct diagnosis code:

Replacement Code

M041 replaces the following previously assigned ICD-10 code(s):

Convert M04.1 to ICD-9 Code

The General Equivalency Mapping (GEM) crosswalk indicates an approximate mapping between the ICD-10 code M04.1 its ICD-9 equivalent. The approximate mapping means there is not an exact match between the ICD-10 code and the ICD-9 code and the mapped code is not a precise representation of the original code.

Code History

  • FY 2021 - No Change, effective from 10/1/2020 through 9/30/2021
  • FY 2020 - No Change, effective from 10/1/2019 through 9/30/2020
  • FY 2019 - No Change, effective from 10/1/2018 through 9/30/2019
  • FY 2018 - No Change, effective from 10/1/2017 through 9/30/2018