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  6. 2024 ICD-10-CM Code G40.C09
Version 2024
Billable Code
New Code

2024 ICD-10-CM Diagnosis Code G40.C09

Lafora progressive myoclonus epilepsy, not intractable, without status epilepticus

ICD-10-CM Code:
G40.C09
ICD-10 Code for:
Lafora progr myoclonus epilepsy, not ntrct, without stat epi
Is Billable?
Yes - Valid for Submission
Code Navigator:

Code Classification

  • Diseases of the nervous system
    (G00–G99)
    • Episodic and paroxysmal disorders
      (G40-G47)
      • Epilepsy and recurrent seizures
        (G40)

G40.C09 is a billable diagnosis code used to specify a medical diagnosis of lafora progressive myoclonus epilepsy, not intractable, without status epilepticus. The code is valid during the current fiscal year for the submission of HIPAA-covered transactions from October 01, 2023 through September 30, 2024.

Approximate Synonyms

The following clinical terms are approximate synonyms or lay terms that might be used to identify the correct diagnosis code:

  • Lafora disease

Clinical Information

  • Lafora Disease

    a form of stimulus sensitive myoclonic epilepsy inherited as an autosomal recessive condition. the most common presenting feature is a single seizure in the second decade of life. this is followed by progressive myoclonus, myoclonic seizures, tonic-clonic seizures, focal occipital seizures, intellectual decline, and severe motor and coordination impairments. most affected individuals do not live past the age of 25 years. concentric amyloid (lafora) bodies are found in neurons, liver, skin, bone, and muscle (from menkes, textbook of childhood neurology, 5th ed, pp111-110).

  • Lafora Disease

    a rare, fatal autosomal recessive inherited disorder caused by mutations in the genes epm2a and epm2b. it is characterized by the presence of cytoplasmic inclusion bodies called lafora bodies in many cells of the body including neurons, muscle cells, and liver cells. the lafora bodies contain mucopolysaccharides. signs and symptoms include seizures, myoclonus, ataxia, and dementia.

New 2024 ICD-10-CM Code

G40.C09 is new to ICD-10-CM code set for the FY 2024, effective October 1, 2023. The National Center for Health Statistics (NCHS) has published an update to the ICD-10-CM diagnosis codes which became effective October 1, 2023. This is a new and revised code for the FY 2024 (October 1, 2023 - September 30, 2024).

Tabular List of Diseases and Injuries

The following annotation back-references are applicable to this diagnosis code. The Tabular List of Diseases and Injuries is a list of ICD-10-CM codes, organized "head to toe" into chapters and sections with coding notes and guidance for inclusions, exclusions, descriptions and more.


Inclusion Terms

Inclusion Terms
These terms are the conditions for which that code is to be used. The terms may be synonyms of the code title, or, in the case of "other specified" codes, the terms are a list of the various conditions assigned to that code. The inclusion terms are not necessarily exhaustive. Additional terms found only in the Alphabetic Index may also be assigned to a code.
  • Lafora progressive myoclonus epilepsy NOS

Index to Diseases and Injuries References

The following annotation back-references for this diagnosis code are found in the injuries and diseases index. The Index to Diseases and Injuries is an alphabetical listing of medical terms, with each term mapped to one or more ICD-10-CM code(s).

  • - Lafora disease - See Also: Epilepsy, progressive, Lafora; - G40.C09

Replacement Code

G40C09 replaces the following previously assigned ICD-10-CM code(s):

  • G40.309 - Gen idiopathic epilepsy, not intractable, w/o stat epi

Code History

  • FY 2024 - Code Added, effective from 10/1/2023 through 9/30/2024