2024 ICD-10-CM Diagnosis Code G40.803

Other epilepsy, intractable, with status epilepticus

ICD-10-CM Code:
G40.803
ICD-10 Code for:
Other epilepsy, intractable, with status epilepticus
Is Billable?
Yes - Valid for Submission
Chronic Condition Indicator: [1]
Chronic
Code Navigator:

Code Classification

  • Diseases of the nervous system
    (G00–G99)
    • Episodic and paroxysmal disorders
      (G40-G47)
      • Epilepsy and recurrent seizures
        (G40)

G40.803 is a billable diagnosis code used to specify a medical diagnosis of other epilepsy, intractable, with status epilepticus. The code is valid during the current fiscal year for the submission of HIPAA-covered transactions from October 01, 2023 through September 30, 2024.

Clinical Classification

Clinical Information

  • Drug Resistant Epilepsy

    epileptic condition in which adequate trials of two tolerated and appropriately chosen and used antiepileptic drugs schedules to achieve sustained seizure freedom failed.
  • Epilepsia Partialis Continua

    a variant of epilepsy characterized by continuous focal jerking of a body part over a period of hours, days, or even years without spreading to other body regions. contractions may be aggravated by movement and are reduced, but not abolished during sleep. electroencephalography demonstrates epileptiform (spike and wave) discharges over the hemisphere opposite to the affected limb in most instances. the repetitive movements may originate from the cerebral cortex or from subcortical structures (e.g., brain stem; basal ganglia). this condition is associated with russian spring and summer encephalitis (see encephalitis, tick borne); rasmussen syndrome (see encephalitis); multiple sclerosis; diabetes mellitus; brain neoplasms; and cerebrovascular disorders. (from brain, 1996 april;119(pt2):393-407; epilepsia 1993;34;suppl 1:s29-s36; and adams et al., principles of neurology, 6th ed, p319)
  • Epilepsies, Myoclonic

    a clinically diverse group of epilepsy syndromes characterized either by myoclonic seizures or by myoclonus in association with other seizure types. myoclonic epilepsy syndromes are divided into three subtypes based on etiology: familial, cryptogenic, and symptomatic.
  • Epilepsies, Partial

    conditions characterized by recurrent paroxysmal neuronal discharges which arise from a focal region of the brain. partial seizures are divided into simple and complex, depending on whether consciousness is unaltered (simple partial seizure) or disturbed (complex partial seizure). both types may feature a wide variety of motor, sensory, and autonomic symptoms. partial seizures may be classified by associated clinical features or anatomic location of the seizure focus. a secondary generalized seizure refers to a partial seizure that spreads to involve the brain diffusely. (from adams et al., principles of neurology, 6th ed, pp317)
  • Epilepsy

    a disorder characterized by recurrent episodes of paroxysmal brain dysfunction due to a sudden, disorderly, and excessive neuronal discharge. epilepsy classification systems are generally based upon: (1) clinical features of the seizure episodes (e.g., motor seizure), (2) etiology (e.g., post-traumatic), (3) anatomic site of seizure origin (e.g., frontal lobe seizure), (4) tendency to spread to other structures in the brain, and (5) temporal patterns (e.g., nocturnal epilepsy). (from adams et al., principles of neurology, 6th ed, p313)
  • Epilepsy, Absence

    a seizure disorder usually occurring in childhood characterized by rhythmic electrical brain discharges of generalized onset. clinical features include a sudden cessation of ongoing activity usually without loss of postural tone. rhythmic blinking of the eyelids or lip smacking frequently accompanies the seizures. the usual duration is 5-10 seconds, and multiple episodes may occur daily. juvenile absence epilepsy is characterized by the juvenile onset of absence seizures and an increased incidence of myoclonus and tonic-clonic seizures. (menkes, textbook of child neurology, 5th ed, p736)
  • Epilepsy, Benign Neonatal

    a condition marked by recurrent seizures that occur during the first 4-6 weeks of life despite an otherwise benign neonatal course. autosomal dominant familial and sporadic forms have been identified. seizures generally consist of brief episodes of tonic posturing and other movements, apnea, eye deviations, and blood pressure fluctuations. these tend to remit after the 6th week of life. the risk of developing epilepsy at an older age is moderately increased in the familial form of this disorder. (neurologia 1996 feb;11(2):51-5)
  • Epilepsy, Complex Partial

    a disorder characterized by recurrent partial seizures marked by impairment of cognition. during the seizure the individual may experience a wide variety of psychic phenomenon including formed hallucinations, illusions, deja vu, intense emotional feelings, confusion, and spatial disorientation. focal motor activity, sensory alterations and automatism may also occur. complex partial seizures often originate from foci in one or both temporal lobes. the etiology may be idiopathic (cryptogenic partial complex epilepsy) or occur as a secondary manifestation of a focal cortical lesion (symptomatic partial complex epilepsy). (from adams et al., principles of neurology, 6th ed, pp317-8)
  • Epilepsy, Frontal Lobe

    a localization-related (focal) form of epilepsy characterized by seizures which arise in the frontal lobe.
  • Epilepsy, Generalized

    recurrent conditions characterized by epileptic seizures which arise diffusely and simultaneously from both hemispheres of the brain. classification is generally based upon motor manifestations of the seizure (e.g., convulsive, nonconvulsive, akinetic, atonic, etc.) or etiology (e.g., idiopathic, cryptogenic, and symptomatic). (from mayo clin proc, 1996 apr;71(4):405-14)
  • Epilepsy, Partial, Motor

    a disorder characterized by recurrent localized paroxysmal discharges of cerebral neurons that give rise to seizures that have motor manifestations. the majority of partial motor seizures originate in the frontal lobe (see also epilepsy, frontal lobe). motor seizures may manifest as tonic or clonic movements involving the face, one limb or one side of the body. a variety of more complex patterns of movement, including abnormal posturing of extremities, may also occur.
  • Epilepsy, Partial, Sensory

    a disorder characterized by recurrent focal onset seizures which have sensory (i.e., olfactory, visual, tactile, gustatory, or auditory) manifestations. partial seizures that feature alterations of consciousness are referred to as complex partial seizures (epilepsy, complex partial).
  • Epilepsy, Post-Traumatic

    recurrent seizures causally related to craniocerebral trauma. seizure onset may be immediate but is typically delayed for several days after the injury and may not occur for up to two years. the majority of seizures have a focal onset that correlates clinically with the site of brain injury. cerebral cortex injuries caused by a penetrating foreign object (craniocerebral trauma, penetrating) are more likely than closed head injuries (head injuries, closed) to be associated with epilepsy. concussive convulsions are nonepileptic phenomena that occur immediately after head injury and are characterized by tonic and clonic movements. (from rev neurol 1998 feb;26(150):256-261; sports med 1998 feb;25(2):131-6)
  • Epilepsy, Reflex

    a subtype of epilepsy characterized by seizures that are consistently provoked by a certain specific stimulus. auditory, visual, and somatosensory stimuli as well as the acts of writing, reading, eating, and decision making are examples of events or activities that may induce seizure activity in affected individuals. (from neurol clin 1994 feb;12(1):57-8)
  • Epilepsy, Rolandic

    an autosomal dominant inherited partial epilepsy syndrome with onset between age 3 and 13 years. seizures are characterized by paresthesia and tonic or clonic activity of the lower face associated with drooling and dysarthria. in most cases, affected children are neurologically and developmentally normal. (from epilepsia 1998 39;suppl 4:s32-s41)
  • Epilepsy, Temporal Lobe

    a localization-related (focal) form of epilepsy characterized by recurrent seizures that arise from foci within the temporal lobe, most commonly from its mesial aspect. a wide variety of psychic phenomena may be associated, including illusions, hallucinations, dyscognitive states, and affective experiences. the majority of complex partial seizures (see epilepsy, complex partial) originate from the temporal lobes. temporal lobe seizures may be classified by etiology as cryptogenic, familial, or symptomatic. (from adams et al., principles of neurology, 6th ed, p321).
  • Epilepsy, Tonic-Clonic

    a generalized seizure disorder characterized by recurrent major motor seizures. the initial brief tonic phase is marked by trunk flexion followed by diffuse extension of the trunk and extremities. the clonic phase features rhythmic flexor contractions of the trunk and limbs, pupillary dilation, elevations of blood pressure and pulse, urinary incontinence, and tongue biting. this is followed by a profound state of depressed consciousness (post-ictal state) which gradually improves over minutes to hours. the disorder may be cryptogenic, familial, or symptomatic (caused by an identified disease process). (from adams et al., principles of neurology, 6th ed, p329)
  • Epileptic Syndromes

    epileptic seizures that are of similar type and age of onset and have other similar features (e.g., clinical course, eeg findings, genetic association and neuropathology).
  • Lafora Disease

    a form of stimulus sensitive myoclonic epilepsy inherited as an autosomal recessive condition. the most common presenting feature is a single seizure in the second decade of life. this is followed by progressive myoclonus, myoclonic seizures, tonic-clonic seizures, focal occipital seizures, intellectual decline, and severe motor and coordination impairments. most affected individuals do not live past the age of 25 years. concentric amyloid (lafora) bodies are found in neurons, liver, skin, bone, and muscle (from menkes, textbook of childhood neurology, 5th ed, pp111-110).
  • Myoclonic Epilepsies, Progressive

    a heterogeneous group of primarily familial epilepsy disorders characterized by myoclonic seizures, tonic-clonic seizures, ataxia, progressive intellectual deterioration, and neuronal degeneration. these include lafora disease; merrf syndrome; neuronal ceroid-lipofuscinosis; sialidosis (see mucolipidoses), and unverricht-lundborg syndrome.
  • Myoclonic Epilepsy, Juvenile

    a disorder characterized by the onset of myoclonus in adolescence, a marked increase in the incidence of absence seizures (see epilepsy, absence), and generalized major motor seizures (see epilepsy, tonic-clonic). the myoclonic episodes tend to occur shortly after awakening. seizures tend to be aggravated by sleep deprivation and alcohol consumption. hereditary and sporadic forms have been identified. (from adams et al., principles of neurology, 6th ed, p323)
  • Unverricht-Lundborg Syndrome

    an autosomal recessive condition characterized by recurrent myoclonic and generalized seizures, ataxia, slowly progressive intellectual deterioration, dysarthria, and intention tremor. myoclonic seizures are severe and continuous, and tend to be triggered by movement, stress, and sensory stimuli. the age of onset is between 8 and 13 years, and the condition is relatively frequent in the baltic region, especially finland. (from menkes, textbook of child neurology, 5th ed, pp109-110)
  • Seizures

    clinical or subclinical disturbances of cortical function due to a sudden, abnormal, excessive, and disorganized discharge of brain cells. clinical manifestations include abnormal motor, sensory and psychic phenomena. recurrent seizures are usually referred to as epilepsy or "seizure disorder."
  • Automatism

    automatic, mechanical, and apparently undirected behavior which is outside of conscious control.
  • Frontal Lobe

    the part of the cerebral hemisphere anterior to the central sulcus, and anterior and superior to the lateral sulcus.

Index to Diseases and Injuries References

The following annotation back-references for this diagnosis code are found in the injuries and diseases index. The Index to Diseases and Injuries is an alphabetical listing of medical terms, with each term mapped to one or more ICD-10-CM code(s).

Convert G40.803 to ICD-9-CM

  • ICD-9-CM Code: 345.81 - Epilepsy NEC w intr epil
    Approximate Flag - The approximate mapping means there is not an exact match between the ICD-10 and ICD-9 codes and the mapped code is not a precise representation of the original code.

Patient Education


Epilepsy

Epilepsy is a brain disorder that causes people to have recurring seizures. The seizures happen when clusters of nerve cells, or neurons, in the brain send out the wrong signals. People may have strange sensations and emotions or behave strangely. They may have violent muscle spasms or lose consciousness.

Epilepsy has many possible causes, including illness, brain injury, and abnormal brain development. In many cases, the cause is unknown.

Doctors use brain scans and other tests to diagnose epilepsy. It is important to start treatment right away. There is no cure for epilepsy, but medicines can control seizures for most people. When medicines are not working well, surgery or implanted devices such as vagus nerve stimulators may help. Special diets can help some children with epilepsy.

NIH: National Institute of Neurological Disorders and Stroke


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Code History

  • FY 2024 - No Change, effective from 10/1/2023 through 9/30/2024
  • FY 2023 - No Change, effective from 10/1/2022 through 9/30/2023
  • FY 2022 - No Change, effective from 10/1/2021 through 9/30/2022
  • FY 2021 - No Change, effective from 10/1/2020 through 9/30/2021
  • FY 2020 - No Change, effective from 10/1/2019 through 9/30/2020
  • FY 2019 - No Change, effective from 10/1/2018 through 9/30/2019
  • FY 2018 - No Change, effective from 10/1/2017 through 9/30/2018
  • FY 2017 - No Change, effective from 10/1/2016 through 9/30/2017
  • FY 2016 - New Code, effective from 10/1/2015 through 9/30/2016. This was the first year ICD-10-CM was implemented into the HIPAA code set.

Footnotes

[1] Chronic - a chronic condition code indicates a condition lasting 12 months or longer and its effect on the patient based on one or both of the following criteria:

  • The condition results in the need for ongoing intervention with medical products,treatment, services, and special equipment
  • The condition places limitations on self-care, independent living, and social interactions.