Use Additional Code Notes in Chapter 17: Congenital malformations, deformations and chromosomal abnormalities ICD-10-CM
A Use Additional Code note means a second code should be added, after this one, to fully describe the condition. In Chapter 17 (Q00-QA1), notes printed in the chapter name other codes 21 times, and Use Additional Code Notes anywhere in the Tabular List name the chapter’s codes 3 times, covering 3 distinct codes, categories and ranges. Switch views to read the list either way.
Use Additional Code Notes by the code that carries the note
- code for any associated paraplegia (paraparesis) (G82.2-)
- Q13.1 Absence of iris
- code for associated glaucoma (H42)
- Q13.81 Rieger anomaly
- code for associated glaucoma (H42)
- code to identify associated malformation of the nose (Q30.2)
- Q87.81 Alport syndrome
- Q87.87 Hao-Fountain Syndrome
- Q87.88 CTNNB1 syndrome
- Q93.52 Phelan-McDermid syndrome
- Q02 Microcephaly
- Q87.88 CTNNB1 syndrome: microcephaly (Q02)
- Q87.88 CTNNB1 syndrome: congenital heart malformations (Q20.0-Q24.9)
- Q30.2 Fissured, notched and cleft nose
- Block Q35-Q37 Cleft lip and cleft palate: code to identify associated malformation of the nose (Q30.2)
The first view lists notes printed in this chapter (a note on a category or block applies to every code beneath it). The second lists codes of this chapter named by Use Additional Code Notes anywhere in the Tabular List, including notes in other chapters.
Questions About Use Additional Code Notes
What does a Use Additional Code note mean?
A Use Additional Code note tells you to add a second code, reported after the code that carries the note, to describe the condition completely. In an etiology/manifestation pair it sits at the etiology code and points to the manifestation (Section I.A.13). The FY 2027 Tabular List has 1,491 of them; 1,174 name other codes, with 1,438 references to 389 distinct codes, categories and ranges.
Where does the additional code go?
After the code carrying the note. For etiology/manifestation pairs the Guidelines are explicit: the etiology is sequenced first, followed by the manifestation code.
Related References
Source: FY 2027 ICD-10-CM Tabular List (CMS and NCHS) and the ICD-10-CM Official Guidelines for Coding and Reporting FY 2027, Section I.A. ICD List is not affiliated with CMS or NCHS.
