ICD-10 Diagnosis Code L40.1

Generalized pustular psoriasis

Diagnosis Code L40.1

ICD-10: L40.1
Short Description: Generalized pustular psoriasis
Long Description: Generalized pustular psoriasis
This is the 2017 version of the ICD-10-CM diagnosis code L40.1

Valid for Submission
The code L40.1 is valid for submission for HIPAA-covered transactions.

Code Classification
  • Diseases of the skin and subcutaneous tissue (L00–L99)
    • Papulosquamous disorders (L40-L45)
      • Psoriasis (L40)

Information for Medical Professionals

Diagnostic Related Groups
The diagnosis code L40.1 is grouped in the following Diagnostic Related Group(s) (MS-DRG V34.0)


Convert to ICD-9 Additional informationCallout TooltipGeneral Equivalence Map
The ICD-10 and ICD-9 GEMs are used to facilitate linking between the diagnosis codes in ICD-9-CM and the new ICD-10-CM code set. The GEMs are the raw material from which providers, health information vendors and payers can derive specific applied mappings to meet their needs.

  • Acute generalized pustular flare of preexisting plaque psoriasis
  • Acute generalized pustular psoriasis de novo
  • Childhood pustular psoriasis
  • Circinate and annular pustular psoriasis
  • Exanthematous disorder
  • Generalized pustular psoriasis
  • Generalized pustular psoriasis
  • Generalized pustular psoriasis of pregnancy
  • Generalized pustular psoriasis of von Zumbush
  • Generalized pustular psoriasis, exanthematous type
  • Impetigo herpetiformis
  • Infantile pustular psoriasis
  • Localized pustular psoriasis
  • Pustular psoriasis
  • Pustular psoriasis in children

Index of Diseases and Injuries
References found for the code L40.1 in the Index of Diseases and Injuries:

Information for Patients


Psoriasis is a skin disease that causes itchy or sore patches of thick, red skin with silvery scales. You usually get the patches on your elbows, knees, scalp, back, face, palms and feet, but they can show up on other parts of your body. Some people who have psoriasis also get a form of arthritis called psoriatic arthritis.

A problem with your immune system causes psoriasis. In a process called cell turnover, skin cells that grow deep in your skin rise to the surface. Normally, this takes a month. In psoriasis, it happens in just days because your cells rise too fast.

Psoriasis can be hard to diagnose because it can look like other skin diseases. Your doctor might need to look at a small skin sample under a microscope.

Psoriasis can last a long time, even a lifetime. Symptoms come and go. Things that make them worse include

  • Infections
  • Stress
  • Dry skin
  • Certain medicines

Psoriasis usually occurs in adults. It sometimes runs in families. Treatments include creams, medicines, and light therapy.

NIH: National Institute of Arthritis and Musculoskeletal and Skin Diseases

  • Psoriasis
  • Psoriasis - guttate

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