| E88.0 | Disorders of plasma-protein metabolism, not elsewhere classified | NON-BILLABLE CODE |
| E88.01 | Alpha-1-antitrypsin deficiency | BILLABLE CODE |
| E88.02 | Plasminogen deficiency | BILLABLE CODE |
| E88.09 | Other disorders of plasma-protein metabolism, not elsewhere classified | BILLABLE CODE |
| E88.1 | Lipodystrophy, not elsewhere classified | BILLABLE CODE |
| E88.2 | Lipomatosis, not elsewhere classified | BILLABLE CODE |
| E88.3 | Tumor lysis syndrome | BILLABLE CODE |
| E88.4 | Mitochondrial metabolism disorders | NON-BILLABLE CODE |
| E88.40 | Mitochondrial metabolism disorder, unspecified | BILLABLE CODE |
| E88.41 | MELAS syndrome | BILLABLE CODE |
| E88.42 | MERRF syndrome | BILLABLE CODE |
| E88.43 | Disorders of mitochondrial tRNA synthetases | BILLABLE CODE |
| E88.49 | Other mitochondrial metabolism disorders | BILLABLE CODE |
| E88.8 | Other specified metabolic disorders | NON-BILLABLE CODE |
| E88.81 | Metabolic syndrome and other insulin resistance | NON-BILLABLE CODE |
| E88.810 | Metabolic syndrome | BILLABLE CODE |
| E88.811 | Insulin resistance syndrome, Type A | BILLABLE CODE |
| E88.818 | Other insulin resistance | BILLABLE CODE |
| E88.819 | Insulin resistance, unspecified | BILLABLE CODE |
| E88.89 | Other specified metabolic disorders | BILLABLE CODE |
| E88.9 | Metabolic disorder, unspecified | BILLABLE CODE |
| E88.A | Wasting disease (syndrome) due to underlying condition | BILLABLE CODE |
