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  2. ICD-10-CM Codes List
  3. J00–J99
  4. J96-J99
  5. Respiratory disorders in diseases classified elsewhere (J99)

Respiratory disorders in diseases classified elsewhere (J99)

The ICD-10 code J99 covers respiratory disorders that occur as a result of other diseases classified elsewhere in the medical system. This code is essential for documenting lung and respiratory system problems linked directly to underlying conditions rather than primary lung diseases.

J99 is used for a wide variety of respiratory complications including restrictive lung diseases caused by neuromuscular conditions like amyotrophic lateral sclerosis and Parkinson disease, as well as pulmonary involvement in systemic diseases such as connective tissue disorders and vasculitis. It also applies to infections like pulmonary histoplasmosis; often referred to as African histoplasmosis or pneumonia caused by Histoplasma capsulatum; and respiratory issues occurring with HIV/AIDS. By associating these respiratory disorders with their root causes, the ICD-10 code for respiratory disorders in diseases classified elsewhere aids medical coders and clinicians in capturing complex cases where lung problems are secondary to other illnesses. This distinction is crucial for precise diagnosis, treatment planning, and health data accuracy.

Instructional Notations

Code First

Certain conditions have both an underlying etiology and multiple body system manifestations due to the underlying etiology. For such conditions, the ICD-10-CM has a coding convention that requires the underlying condition be sequenced first followed by the manifestation. Wherever such a combination exists, there is a "use additional code" note at the etiology code, and a "code first" note at the manifestation code. These instructional notes indicate the proper sequencing order of the codes, etiology followed by manifestation.

  • underlying disease, such as:
  • amyloidosis E85
  • ankylosing spondylitis M45
  • congenital syphilis A50
  • cryoglobulinemia D89.1
  • early congenital syphilis A50.0
  • plasminogen deficiency E88.02
  • schistosomiasis B65.0 B65.9

Type 1 Excludes

A type 1 excludes note is a pure excludes note. It means "NOT CODED HERE!" An Excludes1 note indicates that the code excluded should never be used at the same time as the code above the Excludes1 note. An Excludes1 is used when two conditions cannot occur together, such as a congenital form versus an acquired form of the same condition.