Respiratory disorders in diseases classified elsewhere (J99)

Instructional Notations

Code First Code First
Certain conditions have both an underlying etiology and multiple body system manifestations due to the underlying etiology. For such conditions, the ICD-10-CM has a coding convention that requires the underlying condition be sequenced first followed by the manifestation. Wherever such a combination exists, there is a "use additional code" note at the etiology code, and a "code first" note at the manifestation code. These instructional notes indicate the proper sequencing order of the codes, etiology followed by manifestation.

  • underlying disease, such as:
  • amyloidosis E85
  • ankylosing spondylitis M45
  • congenital syphilis A50.5
  • cryoglobulinemia D89.1
  • early congenital syphilis A50.0
  • plasminogen deficiency E88.02
  • schistosomiasis B65.0 B65.9

Type 1 Excludes Type 1 Excludes
A type 1 excludes note is a pure excludes note. It means "NOT CODED HERE!" An Excludes1 note indicates that the code excluded should never be used at the same time as the code above the Excludes1 note. An Excludes1 is used when two conditions cannot occur together, such as a congenital form versus an acquired form of the same condition.