Other hereditary hemolytic anemias (D58)
The ICD-10 code section D58 covers other hereditary hemolytic anemias, a group of genetic blood disorders where red blood cells break down prematurely. This section includes various specific conditions distinguished by their unique causes and characteristics.
The code D58.0 represents hereditary spherocytosis, sometimes called "anemia due to membrane defect" or "spherocytosis," characterized by abnormally shaped red blood cells. D58.1 is for hereditary elliptocytosis, also known as "elliptocytosis," involving elliptical-shaped red cells often linked to protein deficiencies. The D58.2 code includes a range of other hemoglobinopathies such as "hemoglobin C disease" or "unstable hemoglobin disease," related to mutations in hemoglobin structure affecting oxygen transport. D58.8 describes other specified hereditary hemolytic anemias like hereditary stomatocytosis and xerocytosis, which have distinct membrane or metabolic defects. Finally, D58.9 is used when the hereditary hemolytic anemia is unspecified, covering cases labeled as "congenital hemolytic anemia" without further detail. These codes assist in accurately classifying inherited hemolytic anemias for diagnosis, treatment, and medical coding purposes.
Instructional Notations
Type 1 Excludes
A type 1 excludes note is a pure excludes note. It means "NOT CODED HERE!" An Excludes1 note indicates that the code excluded should never be used at the same time as the code above the Excludes1 note. An Excludes1 is used when two conditions cannot occur together, such as a congenital form versus an acquired form of the same condition.
- hemolytic anemia of the newborn P55
Clinical Terms
The following clinical terms provide additional context, helping users better understand the clinical background and common associations for each diagnosis listed in this section. Including related terms alongside ICD-10-CM codes supports coders, billers, and healthcare professionals in improving accuracy, enhancing documentation, and facilitating research or patient education.
Hemoglobin C Disease
A disease characterized by compensated hemolysis with a normal hemoglobin level or a mild to moderate anemia. There may be intermittent abdominal discomfort, splenomegaly, and slight jaundice.
Hemoglobinopathies
A group of inherited disorders characterized by structural alterations within the hemoglobin molecule.
Pseudoxanthoma Elasticum
An inherited disorder of connective tissue with extensive degeneration and calcification of ELASTIC TISSUE primarily in the skin, eye, and vasculature. At least two forms exist, autosomal recessive and autosomal dominant. This disorder is caused by mutations of one of the ATP-BINDING CASSETTE TRANSPORTERS. Patients are predisposed to MYOCARDIAL INFARCTION and GASTROINTESTINAL HEMORRHAGE.
