2021 ICD-10-CM Codes for Indeterminate sex and pseudohermaphroditism (Q56)

Instructional Notations

Type 1 Excludes Type 1 Excludes
A type 1 excludes note is a pure excludes note. It means "NOT CODED HERE!" An Excludes1 note indicates that the code excluded should never be used at the same time as the code above the Excludes1 note. An Excludes1 is used when two conditions cannot occur together, such as a congenital form versus an acquired form of the same condition.

  • 46,XX true hermaphrodite Q99.1
  • androgen insensitivity syndrome E34.5
  • chimera 46,XX/46,XY true hermaphrodite Q99.0
  • female pseudohermaphroditism with adrenocortical disorder E25
  • pseudohermaphroditism with specified chromosomal anomaly Q96 Q99
  • pure gonadal dysgenesis Q99.1