Hereditary and idiopathic neuropathy (G60) ICD-10-CM
The G60 code range covers hereditary and idiopathic neuropathy with 7 ICD-10-CM diagnosis codes. 6 of them are billable and valid for claim submission in fiscal year 2026, and the category headers group them but cannot themselves be billed.
Codes in the G60 Range 7 codes · 6 billable
- G60 Hereditary and idiopathic neuropathyNon-billable
- G60.0 Hereditary motor and sensory neuropathy
- G60.1 Refsum's disease
- G60.2 Neuropathy in association with hereditary ataxia
- G60.3 Idiopathic progressive neuropathy
- G60.8 Other hereditary and idiopathic neuropathies
- G60.9 Hereditary and idiopathic neuropathy, unspecified
Clinical Terms in This Code Range
Definitions from the National Library of Medicine for conditions coded in the G60 range.
Giant Axonal Neuropathy
Rare autosomal recessive disorder of INTERMEDIATE FILAMENT PROTEINS. The disease is caused by mutations in the gene that codes gigaxonin protein. The mutations result in disorganization of axonal NEUROFILAMENT PROTEINS, formation of the characteristic giant axons, and progressive neuropathy. The clinical features of the disease include early-onset progressive peripheral motor and sensory neuropathies often associated with central nervous system involvement (INTELLECTUAL DISABILITY, seizures, DYSMETRIA, and CONGENITAL NYSTAGMUS).
Small Fiber Neuropathy
Disorder of the peripheral nerves that primarily impair small nerve fibers. The affected small nerve fibers include myelinated A-delta fibers (see A FIBERS) and unmyelinated C FIBERS. Because these small fibers innervate skin and help control autonomic function, their neuropathy presents with neuropathic pain, reduced thermal and pain sensitivity, and autonomic dysfunction (e.g. abnormal sweating or facial flushing). Small fiber neuropathy can be idiopathic or associated with underlying diseases (e.g., AMYLOIDOSIS; DIABETES MELLITUS; SARCOIDOSIS; or VASCULITIS).
Vocal Cord Paralysis
Congenital or acquired paralysis of one or both VOCAL CORDS. This condition is caused by defects in the CENTRAL NERVOUS SYSTEM, the VAGUS NERVE and branches of LARYNGEAL NERVES. Common symptoms are VOICE DISORDERS including HOARSENESS or APHONIA.
Waardenburg Syndrome
Rare, autosomal dominant disease with variable penetrance and several known clinical types. Characteristics may include depigmentation of the hair and skin, congenital deafness, heterochromia iridis, medial eyebrow hyperplasia, hypertrophy of the nasal root, and especially dystopia canthorum. The underlying cause may be defective development of the neural crest (neurocristopathy). Waardenburg's syndrome may be closely related to piebaldism. Klein-Waardenburg Syndrome refers to a disorder that also includes upper limb abnormalities.
About the G60 Code Range
ICD-10 code G60 covers hereditary and idiopathic neuropathies, which are nerve disorders caused by genetic factors or unknown origins. These codes specifically categorize various inherited and unexplained peripheral neuropathies affecting motor, sensory, and autonomic nerves.
Within this section, G60.0 refers to hereditary motor and sensory neuropathy, commonly known as Charcot-Marie-Tooth disease and its many genetic subtypes. This code includes related conditions like Déjérine-Sottas disease and hereditary liability to pressure palsies, helping coders capture the diverse forms of inherited nerve damage affecting movement and sensation. G60.1 identifies Refsum's disease, a rare metabolic disorder causing neuropathy along with associated symptoms like cardiomyopathy and ophthalmoplegia.
The codes G60.2 and G60.3 pinpoint neuropathies linked to hereditary ataxia and idiopathic progressive neuropathy, respectively, useful for disorders presenting with coordination and nerve function decline of unknown cause. G60.8 includes other hereditary and idiopathic neuropathies such as hereditary sensory and autonomic neuropathies, small fiber neuropathies, and rare syndromes like giant axonal neuropathy. Finally, G60.9 is for hereditary and idiopathic neuropathy when specific details are unavailable, supporting coding in unclear cases. This classification aids healthcare professionals and coders in accurately identifying inherited or unexplained nerve disorders for proper diagnosis and management.
Questions About This Page
How many billable codes are in the G60 range?
Of the 7 codes in this range, 6 are billable and valid for claim submission from October 1, 2025 through September 30, 2026. Category header codes group them but cannot be reported on claims.
What does the G60 range classify?
The range classifies hereditary and idiopathic neuropathy. Each code links to its own reference page with billing status, MS-DRG grouping, coding notes, and clinical information.
Related References
Source: CMS FY 2026 ICD-10-CM Tabular List and order file, effective October 1, 2025 through September 30, 2026.
