Parapsoriasis (L41)

ICD-10 code L41 covers a group of skin conditions collectively known as parapsoriasis, which are chronic inflammatory disorders affecting the skin’s appearance and texture. These codes are used to classify specific types and variations of parapsoriasis for medical diagnosis and billing.

The ICD-10 code for parapsoriasis includes several subtypes, such as L41.0 for pityriasis lichenoides et varioliformis acuta (also known as pityriasis lichenoides or parapsoriasis varioliformis), which is an acute inflammatory skin condition. L41.1 identifies pityriasis lichenoides chronica, a more chronic form. Codes L41.3 and L41.4 specify small and large plaque parapsoriasis, respectively; named for the size of scaly plaques on the skin. L41.5 refers to retiform parapsoriasis, a pattern variant of large plaque parapsoriasis. The code L41.8 addresses other forms such as parapsoriasis atrophicans or herpetiformis. Lastly, L41.9 is used when parapsoriasis is diagnosed but not specified further. Using these specific codes helps healthcare providers accurately document and treat these distinct inflammatory skin disorders.

Instructional Notations

Type 1 Excludes

A type 1 excludes note is a pure excludes note. It means "NOT CODED HERE!" An Excludes1 note indicates that the code excluded should never be used at the same time as the code above the Excludes1 note. An Excludes1 is used when two conditions cannot occur together, such as a congenital form versus an acquired form of the same condition.

  • poikiloderma vasculare atrophicans L94.5

Clinical Terms

The following clinical terms provide additional context, helping users better understand the clinical background and common associations for each diagnosis listed in this section. Including related terms alongside ICD-10-CM codes supports coders, billers, and healthcare professionals in improving accuracy, enhancing documentation, and facilitating research or patient education.

Parapsoriasis

The term applied to a group of relatively uncommon inflammatory, maculopapular, scaly eruptions of unknown etiology and resistant to conventional treatment. Eruptions are both psoriatic and lichenoid in appearance, but the diseases are distinct from psoriasis, lichen planus, or other recognized dermatoses. Proposed nomenclature divides parapsoriasis into two distinct subgroups, PITYRIASIS LICHENOIDES and parapsoriasis en plaques (small- and large-plaque parapsoriasis).

Pityriasis Lichenoides

A subgroup of PARAPSORIASIS itself divided into acute and chronic forms. The acute form is characterized by the abrupt onset of a generalized, reddish-brown, maculopapular eruption. Lesions may be vesicular, hemorrhagic, crusted, or necrotic. Histologically the disease is characterized by epidermal necrolysis. The chronic form shows milder skin changes with necrosis.