ICD-9 Diagnosis Code 277.1

Dis porphyrin metabolism

Diagnosis Code 277.1

ICD-9: 277.1
Short Description: Dis porphyrin metabolism
Long Description: Disorders of porphyrin metabolism
This is the 2014 version of the ICD-9-CM diagnosis code 277.1

Code Classification
  • Endocrine, nutritional and metabolic diseases, and immunity disorders
    • Other metabolic disorders and immunity disorders (270-279)
      • 277 Other and unspecified disorders of metabolism

Information for Medical Professionals

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Index of Diseases and Injuries
References found for the code 277.1 in the Index of Diseases and Injuries:

Information for Patients


Porphyrias are a group of genetic disorders caused by problems with how your body makes a substance called heme. Heme is found throughout the body, especially in your blood and bone marrow, where it carries oxygen.

There are two main types of porphyrias. One affects the skin and the other affects the nervous system. People with the skin type develop blisters, itching, and swelling of their skin when it is exposed to sunlight. The nervous system type is called acute porphyria. Symptoms include pain in the chest, abdomen, limbs, or back; muscle numbness, tingling, paralysis, or cramping; vomiting; constipation; and personality changes or mental disorders. These symptoms come and go.

Certain triggers can cause an attack, including some medicines, smoking, drinking alcohol, infections, stress, and sun exposure. Attacks develop over hours or days. They can last for days or weeks.

Porphyria can be hard to diagnose. It requires blood, urine, and stool tests. Each type of porphyria is treated differently. Treatment may involve avoiding triggers, receiving heme through a vein, taking medicines to relieve symptoms, or having blood drawn to reduce iron in the body. People who have severe attacks may need to be hospitalized.

NIH: National Institute of Diabetes and Digestive and Kidney Diseases

  • Delta-ALA
  • PBG test
  • Porphyria - NIH
  • Porphyria
  • Porphyrins - blood
  • Porphyrins - urine

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