ICD-9 Code 742.4

Other specified congenital anomalies of brain

Not Valid for Submission

742.4 is a legacy non-billable code used to specify a medical diagnosis of other specified congenital anomalies of brain. This code was replaced on September 30, 2015 by its ICD-10 equivalent.

ICD-9: 742.4
Short Description:Brain anomaly NEC
Long Description:Other specified congenital anomalies of brain

Convert 742.4 to ICD-10

The following crosswalk between ICD-9 to ICD-10 is based based on the General Equivalence Mappings (GEMS) information:

  • Q04.5 - Megalencephaly
  • Q04.6 - Congenital cerebral cysts
  • Q04.8 - Other specified congenital malformations of brain

Code Classification

  • Congenital anomalies (740–759)
    • Congenital anomalies (740-759)
      • 742 Other congenital anomalies of nervous system

Information for Medical Professionals

Synonyms

  • Absence of septum pellucidum
  • Aprosencephaly
  • Arnold Chiari type 2 without hydrocephalus
  • Atrophy of corpus callosum
  • Calcium/calmodulin-dependent serine protein kinase related intellectual disability
  • Cerebellar cortical dysplasia
  • Cerebral cortical dysgenesis
  • Chiari malformation type III
  • Colloid cyst of third ventricle
  • Congenital abnormal shape of cerebellum
  • Congenital adhesions of cerebral meninges
  • Congenital cerebellar cortical atrophy
  • Congenital cerebral cyst
  • Congenital choroid plexus cyst
  • Congenital malformation of corpus callosum
  • Congenital malformation of dural sinus
  • Congenital porencephaly
  • Congenital pseudoporencephaly
  • Cortical dysplasia
  • Cortical dysplasia with hemimegalencephaly
  • Cystic malformation of posterior fossa
  • Defect of telencephalic division
  • Derodidymis
  • Dural arteriovenous malformation
  • Dyke-Davidoff-Masson syndrome
  • Ecchordosis physaliphora
  • Ectopic glial tissue
  • Ectopic gray matter in centrum ovale
  • Encephalo-ophthalmic dysplasia
  • Familial aplasia of the vermis
  • Familial megalencephaly
  • Fetal choroid plexus cyst
  • Fetal macrocephaly
  • Granular cell hypoplasia
  • Hemimegalencephaly
  • Localized cortical dysplasia
  • Macroencephaly
  • Macrogyria
  • Marinesco-Sjögren syndrome
  • Multiple brain anomalies
  • Multiple congenital cerebral cysts
  • Muscle eye brain disease
  • Nodular heterotopia
  • Olivary heterotopia
  • Olive dysplasia
  • Partial absence of septum pellucidum
  • Persistent Blake's pouch cyst
  • Posterior fossa arachnoid cyst
  • Prion disease
  • Rhombencephalosynapsis
  • Schizencephaly
  • Single congenital cerebral cyst
  • Sporadic megalencephaly
  • Status marmoratus
  • Subependymal nodular heterotopia
  • Ulegyria
  • X-linked periventricular heterotopia

Index to Diseases and Injuries

References found for the code 742.4 in the Index of Diseases and Injuries:


Information for Patients


Brain Malformations

Most brain malformations begin long before a baby is born. Something damages the developing nervous system or causes it to develop abnormally. Sometimes it's a genetic problem. In other cases, exposure to certain medicines, infections, or radiation during pregnancy interferes with brain development. Parts of the brain may be missing, abnormally small or large, or not fully developed.

Treatment depends upon the problem. In many cases, treatment only helps with symptoms. It may include antiseizure medicines, shunts to drain fluid from the brain, and physical therapy.

There are head malformations that do not involve the brain. Craniofacial disorders are the result of abnormal growth of soft tissue and bones in the face and head. It's common for new babies to have slightly uneven heads, but parents should watch the shape of their baby's head for possible problems.

NIH: National Institute of Neurological Disorders and Stroke


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ICD-9 Footnotes

General Equivalence Map Definitions
The ICD-9 and ICD-10 GEMs are used to facilitate linking between the diagnosis codes in ICD-9-CM and the new ICD-10-CM code set. The GEMs are the raw material from which providers, health information vendors and payers can derive specific applied mappings to meet their needs.

  • Approximate Flag - The approximate flag is on, indicating that the relationship between the code in the source system and the code in the target system is an approximate equivalent.
  • No Map Flag - The no map flag indicates that a code in the source system is not linked to any code in the target system.
  • Combination Flag - The combination flag indicates that more than one code in the target system is required to satisfy the full equivalent meaning of a code in the source system.

Index of Diseases and Injuries Definitions

  • And - The word "and" should be interpreted to mean either "and" or "or" when it appears in a title.
  • Code also note - A "code also" note instructs that two codes may be required to fully describe a condition, but this note does not provide sequencing direction.
  • Code first - Certain conditions have both an underlying etiology and multiple body system manifestations due to the underlying etiology. For such conditions, the ICD-10-CM has a coding convention that requires the underlying condition be sequenced first followed by the manifestation. Wherever such a combination exists, there is a "use additional code" note at the etiology code, and a "code first" note at the manifestation code. These instructional notes indicate the proper sequencing order of the codes, etiology followed by manifestation.
  • Type 1 Excludes Notes - A type 1 Excludes note is a pure excludes note. It means "NOT CODED HERE!" An Excludes1 note indicates that the code excluded should never be used at the same time as the code above the Excludes1 note. An Excludes1 is used when two conditions cannot occur together, such as a congenital form versus an acquired form of the same condition.
  • Type 2 Excludes Notes - A type 2 Excludes note represents "Not included here". An excludes2 note indicates that the condition excluded is not part of the condition represented by the code, but a patient may have both conditions at the same time. When an Excludes2 note appears under a code, it is acceptable to use both the code and the excluded code together, when appropriate.
  • Includes Notes - This note appears immediately under a three character code title to further define, or give examples of, the content of the category.
  • Inclusion terms - List of terms is included under some codes. These terms are the conditions for which that code is to be used. The terms may be synonyms of the code title, or, in the case of "other specified" codes, the terms are a list of the various conditions assigned to that code. The inclusion terms are not necessarily exhaustive. Additional terms found only in the Alphabetic Index may also be assigned to a code.
  • NEC "Not elsewhere classifiable" - This abbreviation in the Alphabetic Index represents "other specified". When a specific code is not available for a condition, the Alphabetic Index directs the coder to the "other specified” code in the Tabular List.
  • NOS "Not otherwise specified" - This abbreviation is the equivalent of unspecified.
  • See - The "see" instruction following a main term in the Alphabetic Index indicates that another term should be referenced. It is necessary to go to the main term referenced with the "see" note to locate the correct code.
  • See Also - A "see also" instruction following a main term in the Alphabetic Index instructs that there is another main term that may also be referenced that may provide additional Alphabetic Index entries that may be useful. It is not necessary to follow the "see also" note when the original main term provides the necessary code.
  • 7th Characters - Certain ICD-10-CM categories have applicable 7th characters. The applicable 7th character is required for all codes within the category, or as the notes in the Tabular List instruct. The 7th character must always be the 7th character in the data field. If a code that requires a 7th character is not 6 characters, a placeholder X must be used to fill in the empty characters.
  • With - The word "with" should be interpreted to mean "associated with" or "due to" when it appears in a code title, the Alphabetic Index, or an instructional note in the Tabular List. The word "with" in the Alphabetic Index is sequenced immediately following the main term, not in alphabetical order.