ICD-9 Code 446.1
Acute febrile mucocutaneous lymph node syndrome [MCLS]
Not Valid for Submission
446.1 is a legacy non-billable code used to specify a medical diagnosis of acute febrile mucocutaneous lymph node syndrome [mcls]. This code was replaced on September 30, 2015 by its ICD-10 equivalent.
| ICD-9: | 446.1 |
| Short Description: | Mucocutan lymph node syn |
| Long Description: | Acute febrile mucocutaneous lymph node syndrome [MCLS] |
Convert 446.1 to ICD-10
The following crosswalk between ICD-9 to ICD-10 is based based on the General Equivalence Mappings (GEMS) information:
- M30.3 - Mucocutaneous lymph node syndrome [Kawasaki]
Code Classification
-
Diseases of the circulatory system (390–459)
-
Diseases of arteries, arterioles, and capillaries (440-449)
- 446 Polyarteritis nodosa and allied conditions
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Diseases of arteries, arterioles, and capillaries (440-449)
Information for Medical Professionals
Index to Diseases and Injuries
References found for the code 446.1 in the Index of Diseases and Injuries:
- Disease diseased SEE ALSO
See Also
A “see also” instruction following a main term in the index instructs that there is another main term that may also be referenced that may provide additional index entries that may be useful. It is not necessary to follow the “see also” note when the original main term provides the necessary code. Syndrome- Kawasaki 446.1
- Kawasaki disease 446.1
- MCLS mucocutaneous lymph node syndrome 446.1
- Mucocutaneous lymph node syndrome acute febrile infantile 446.1
- Syndrome SEE ALSO See Also
A “see also” instruction following a main term in the index instructs that there is another main term that may also be referenced that may provide additional index entries that may be useful. It is not necessary to follow the “see also” note when the original main term provides the necessary code. Disease- mucocutaneous lymph node acute febrile infantile MCLS 446.1
Information for Patients
Kawasaki Disease
What is Kawasaki disease?
Kawasaki disease is a rare illness that usually affects small children. Other names for it are Kawasaki syndrome and mucocutaneous lymph node syndrome. It is a type of vasculitis, which is inflammation of the blood vessels. Kawasaki disease is serious, but most children can fully recover if they are treated right away.
What causes Kawasaki disease?
Kawasaki disease happens when the immune system injures the blood vessels by mistake. Researchers do not fully know why this happens. But when it does, the blood vessels become inflamed and can narrow or close off.
Genetics may play a role in Kawasaki disease. There may also be environmental factors, such as infections. It does not seem to be contagious. This means that it cannot be passed from one child to another.
Who is at risk for Kawasaki disease?
Kawasaki disease usually affects children under the age of 5. But older children and adults can sometimes get it. It is more common in boys than girls. It can affect children of any race, but those with Asian or Pacific Islander descent are more likely to get it.
What are the symptoms of Kawasaki disease?
The symptoms of Kawasaki disease may include:
- High fever lasting at least five days
- A rash, often on the back, chest, and groin
- Swollen hands and feet
- Redness of the lips, lining of the mouth, tongue, palms of the hand, and soles of the feet
- Pink eye
- Swollen lymph nodes
What other problems can Kawasaki disease cause?
Sometimes Kawasaki disease can affect the walls of the coronary arteries. These arteries bring supply blood and oxygen to your heart. This can lead to:
- An aneurysm (bulging and thinning of the walls of the arteries). This can raise the risk of blood clotss in the arteries. If the blood clots are not treated, they could lead to a heart attack or internal bleeding.
- Inflammation in the heart
- Heart valve problems
Kawasaki disease can also affect other parts of the body, including the brain and nervous system, the immune system, and the digestive system.
How is Kawasaki disease diagnosed?
There is no specific test for Kawasaki disease. To make a diagnosis, your child's health care provider may use many tools:
- A physical exam, which includes looking at the signs and symptoms
- Blood and urine tests to rule out other diseases and check for signs of inflammation
- Tests to check for damage to the heart, such as an echocardiogram and electrocardiogram (EKG)
What are the treatments for Kawasaki disease?
Kawasaki disease is usually treated in the hospital with an intravenous (IV) dose of immunoglobulin (IVIG). Aspirin may also be part of the treatment. But do not give your child aspirin unless the health care provider tells you to. Aspirin can cause Reye syndrome in children. This is a rare, serious illness that can affect the brain and liver.
Usually treatment works. But if it is not working well enough, the provider may also give your child other medicines to fight the inflammation. If the disease affects your child's heart, he or she might need additional medicines, surgery, or other medical procedures.
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ICD-9 Footnotes
General Equivalence Map Definitions
The ICD-9 and ICD-10 GEMs are used to facilitate linking between the diagnosis codes in ICD-9-CM and the new ICD-10-CM code set. The GEMs are the raw material from which providers, health information vendors and payers can derive specific applied mappings to meet their needs.
- Approximate Flag - The approximate flag is on, indicating that the relationship between the code in the source system and the code in the target system is an approximate equivalent.
- No Map Flag - The no map flag indicates that a code in the source system is not linked to any code in the target system.
- Combination Flag - The combination flag indicates that more than one code in the target system is required to satisfy the full equivalent meaning of a code in the source system.
Index of Diseases and Injuries Definitions
- And - The word "and" should be interpreted to mean either "and" or "or" when it appears in a title.
- Code also note - A "code also" note instructs that two codes may be required to fully describe a condition, but this note does not provide sequencing direction.
- Code first - Certain conditions have both an underlying etiology and multiple body system manifestations due to the underlying etiology. For such conditions, the ICD-10-CM has a coding convention that requires the underlying condition be sequenced first followed by the manifestation. Wherever such a combination exists, there is a "use additional code" note at the etiology code, and a "code first" note at the manifestation code. These instructional notes indicate the proper sequencing order of the codes, etiology followed by manifestation.
- Type 1 Excludes Notes - A type 1 Excludes note is a pure excludes note. It means "NOT CODED HERE!" An Excludes1 note indicates that the code excluded should never be used at the same time as the code above the Excludes1 note. An Excludes1 is used when two conditions cannot occur together, such as a congenital form versus an acquired form of the same condition.
- Type 2 Excludes Notes - A type 2 Excludes note represents "Not included here". An excludes2 note indicates that the condition excluded is not part of the condition represented by the code, but a patient may have both conditions at the same time. When an Excludes2 note appears under a code, it is acceptable to use both the code and the excluded code together, when appropriate.
- Includes Notes - This note appears immediately under a three character code title to further define, or give examples of, the content of the category.
- Inclusion terms - List of terms is included under some codes. These terms are the conditions for which that code is to be used. The terms may be synonyms of the code title, or, in the case of "other specified" codes, the terms are a list of the various conditions assigned to that code. The inclusion terms are not necessarily exhaustive. Additional terms found only in the Alphabetic Index may also be assigned to a code.
- NEC "Not elsewhere classifiable" - This abbreviation in the Alphabetic Index represents "other specified". When a specific code is not available for a condition, the Alphabetic Index directs the coder to the "other specified” code in the Tabular List.
- NOS "Not otherwise specified" - This abbreviation is the equivalent of unspecified.
- See - The "see" instruction following a main term in the Alphabetic Index indicates that another term should be referenced. It is necessary to go to the main term referenced with the "see" note to locate the correct code.
- See Also - A "see also" instruction following a main term in the Alphabetic Index instructs that there is another main term that may also be referenced that may provide additional Alphabetic Index entries that may be useful. It is not necessary to follow the "see also" note when the original main term provides the necessary code.
- 7th Characters - Certain ICD-10-CM categories have applicable 7th characters. The applicable 7th character is required for all codes within the category, or as the notes in the Tabular List instruct. The 7th character must always be the 7th character in the data field. If a code that requires a 7th character is not 6 characters, a placeholder X must be used to fill in the empty characters.
- With - The word "with" should be interpreted to mean "associated with" or "due to" when it appears in a code title, the Alphabetic Index, or an instructional note in the Tabular List. The word "with" in the Alphabetic Index is sequenced immediately following the main term, not in alphabetical order.