ICD-9 Code 277.6

Other deficiencies of circulating enzymes

Not Valid for Submission

277.6 is a legacy non-billable code used to specify a medical diagnosis of other deficiencies of circulating enzymes. This code was replaced on September 30, 2015 by its ICD-10 equivalent.

ICD-9:	277.6
Short Description:	Defic circul enzyme NEC
Long Description:	Other deficiencies of circulating enzymes

Convert 277.6 to ICD-10

The following crosswalk between ICD-9 to ICD-10 is based based on the General Equivalence Mappings (GEMS) information:

D84.1 - Defects in the complement system

Code Classification

Endocrine, nutritional and metabolic diseases, and immunity disorders (240–279)
- Other metabolic disorders and immunity disorders (270-279)
  - 277 Other and unspecified disorders of metabolism

Information for Medical Professionals

Synonyms

6-Pyruvoyl-tetrahydrobiopterin synthase deficiency
Acetyl-CoA: carboxylase deficiency
Acid phosphatase deficiency
Alpha-2-antitrypsin deficiency
Bifunctional peroxisomal enzyme deficiency
Biotinidase deficiency
Clinical manifestation of carnosinase deficiency
Clinical manifestation of enzyme deficiency
Combined deficiency of sialidase AND beta galactosidase
Complex V deficiency
Cytochrome p450 CYP1A2 enzyme deficiency
Cytochrome p450 CYP2C19 enzyme deficiency
Cytochrome p450 CYP2C9 enzyme deficiency
Cytochrome p450 CYP2D6 enzyme deficiency
Cytochrome p450 CYP2E1 enzyme deficiency
Cytochrome p450 CYP3A enzyme deficiency
Cytochrome p450 enzyme deficiency
Deficiency of
Deficiency of
Deficiency of 1,3-beta-glucan synthase
Deficiency of 1,4-alpha-glucan 6alpha-glucosyltransferase
Deficiency of 1,4-alpha-glucan branching enzyme
Deficiency of 2,4-dienoyl-coenzyme A reductase
Deficiency of 2,5-diaminovalerate aminotransferase
Deficiency of 2-hydroxyglutarate dehydrogenase
Deficiency of 2-methylbutyryl-coenzyme A dehydrogenase
Deficiency of 3alpha-hydroxycholanate dehydrogenase
Deficiency of 3alpha-hydroxysteroid dehydrogenase
Deficiency of 3-hydroxyacyl-CoA dehydrogenase
Deficiency of 3-hydroxybutyrate dehydrogenase
Deficiency of 3-hydroxybutyryl-coenzyme A epimerase
Deficiency of 3-hydroxyisobutyrate dehydrogenase
Deficiency of 3-hydroxyisobutyryl coenzyme A hydrolase
Deficiency of 3-mercaptopyruvate sulfurtransferase
Deficiency of 3'-nucleotidase
Deficiency of 3-oxoacid coenzyme A-transferase
Deficiency of 3-oxoadipate coenzyme A-transferase
Deficiency of 4-hydroxy-2-oxoglutarate aldolase
Deficiency of 5'-nucleotidase
Deficiency of 6-phosphofructokinase
Deficiency of A-ase
Deficiency of acetate kinase
Deficiency of acetate-coenzyme A ligase
Deficiency of acetoacetyl-coenzyme A reductase
Deficiency of acetylcholinesterase
Deficiency of acetyl-CoA hydrolase
Deficiency of acetyl-coenzyme A acetyltransferase
Deficiency of acetyl-coenzyme A acylase
Deficiency of acetyl-coenzyme A acyltransferase
Deficiency of acetyl-coenzyme A deacylase
Deficiency of acetylesterase
Deficiency of acetylserotonin methyltransferase
Deficiency of acid-aminoacid ligase
Deficiency of acid-ammonia ligase
Deficiency of aconitate hydratase
Deficiency of acylphosphatase
Deficiency of adenine deaminase
Deficiency of adenine phosphoribosyltransferase
Deficiency of adenosine diphosphate deaminase
Deficiency of adenosine kinase
Deficiency of adenosine monophosphate deaminase
Deficiency of adenosine monophosphate nucleosidase
Deficiency of adenosine triphosphate pyrophosphatase
Deficiency of adenosinetriphosphatase
Deficiency of adenosylhomocysteinase
Deficiency of adenylate kinase
Deficiency of adenylylsulfate kinase
Deficiency of alanine aminotransferase
Deficiency of alanine dehydrogenase
Deficiency of alanine-oxo-acid aminotransferase
Deficiency of alanine-transfer ribonucleic acid ligase
Deficiency of alcohol sulfotransferase
Deficiency of aldehyde dehydrogenase
Deficiency of aldehyde oxidase
Deficiency of aldehyde reductase
Deficiency of aldehyde-lyase
Deficiency of aldonolactonase
Deficiency of aldose 1-epimerase
Deficiency of alkaline phosphatase
Deficiency of alkaline phosphomonoesterase
Deficiency of alkylhalidase
Deficiency of allantoicase
Deficiency of allantoinase
Deficiency of alpha- and beta-trypsin
Deficiency of alpha-1,4-glucan-protein synthase
Deficiency of alpha-aminoacylpeptide hydrolase
Deficiency of alpha-amylase
Deficiency of alpha-galactosidase
Deficiency of alpha-glucosidase
Deficiency of amidase
Deficiency of amidinotransferase
Deficiency of amidophosphoribosyltransferase
Deficiency of amine oxidase
Deficiency of amine oxidase
Deficiency of aminoacyl-histidine dipeptidase
Deficiency of aminoacyltransferase
Deficiency of aminopeptidase
Deficiency of aminotransferase
Deficiency of ammonia-lyase
Deficiency of amylase
Deficiency of amylo-1,6-glucosidase
Deficiency of arginine deiminase
Deficiency of aromatic-L-amino-acid decarboxylase
Deficiency of aryl sulfotransferase
Deficiency of arylamine acetyltransferase
Deficiency of arylesterase
Deficiency of arylsulfatase
Deficiency of asparagine-oxo-acid aminotransferase
Deficiency of aspartate 4-decarboxylase
Deficiency of aspartate aminotransferase
Deficiency of aspartate carbamoyltransferase
Deficiency of aspartate kinase
Deficiency of aspartic proteinase
Deficiency of azobenzene reductase
Deficiency of benzaldehyde dehydrogenase
Deficiency of benzoylcholinesterase
Deficiency of beta-amylase
Deficiency of beta-fructofuranosidase
Deficiency of beta-galactosidase
Deficiency of beta-glucosidase
Deficiency of beta-glucuronidase
Deficiency of betaine-aldehyde dehydrogenase
Deficiency of betaine-homocysteine methyltransferase
Deficiency of beta-ureidopropionase
Deficiency of bisphosphoglycerate mutase
Deficiency of bisphosphoglycerate phosphatase
Deficiency of butyrate-acetoacetate coenzyme A-transferase
Deficiency of butyrylcholine esterase
Deficiency of carbamate kinase
Deficiency of carbonate dehydratase
Deficiency of carbon-carbon lyase
Deficiency of carbon-halide lyase
Deficiency of carbon-nitrogen lyase
Deficiency of carbon-oxygen lyase
Deficiency of carbon-sulfur lyase
Deficiency of carboxylesterase
Deficiency of carboxylic ester hydrolase
Deficiency of carboxy-lyase
Deficiency of carboxypeptidase A
Deficiency of carboxypeptidase B
Deficiency of carnitine acetyltransferase
Deficiency of carnosinase
Deficiency of catalase
Deficiency of catechol oxidase
Deficiency of cathepsin C
Deficiency of cellulase
Deficiency of chlorophyllase
Deficiency of cholate-CoA ligase
Deficiency of cholesterol esterase
Deficiency of cholesterol oxidase
Deficiency of choline acetyltransferase
Deficiency of choline dehydrogenase
Deficiency of choline esterase I
Deficiency of choline esterase II
Deficiency of choline kinase
Deficiency of choline-phosphate cytidylyltransferase
Deficiency of cholinephosphotransferase
Deficiency of cholinesterase
Deficiency of chymosin
Deficiency of chymotrypsin
Deficiency of chymotrypsin A and B
Deficiency of citrate
Deficiency of coenzyme-A transferase
Deficiency of creatine kinase
Deficiency of cysteamine dioxygenase
Deficiency of cysteine aminotransferase
Deficiency of cysteine carboxypeptidase
Deficiency of cysteine proteinase
Deficiency of cysteinyl-glycine dipeptidase
Deficiency of cystine reductase
Deficiency of cytidine deaminase
Deficiency of cytochrome-b>5< reductase
Deficiency of cytochrome-c peroxidase
Deficiency of cytosol aminopeptidase
Deficiency of D-2-hydroxy-acid dehydrogenase
Deficiency of D-amino-acid oxidase
Deficiency of D-aspartate oxidase
Deficiency of dehydrogenase
Deficiency of dehydrogluconate dehydrogenase
Deficiency of dehydrogluconokinase
Deficiency of deoxyribonuclease I
Deficiency of deoxyribonuclease II
Deficiency of deoxyribonucleic acid nucleotidylexotransferase
Deficiency of deoxyribonucleic acid-directed deoxyribonucleic acid polymerase
Deficiency of deoxyribonucleic acid-directed ribonucleic acid polymerase
Deficiency of dephospho-coenzyme A kinase
Deficiency of dextranase
Deficiency of dihydrolipoamide acetyltransferase
Deficiency of dihydroorotase
Deficiency of dihydrouracil dehydrogenase
Deficiency of diisopropyl-fluorophosphatase
Deficiency of dimethylallyltranstransferase
Deficiency of dioxygenase
Deficiency of dipeptidase
Deficiency of dipeptide hydrolase
Deficiency of dipeptidyl peptidase I
Deficiency of dipeptidyl-amino-peptidase I
Deficiency of dipeptidylpeptide hydrolase
Deficiency of diphosphomevalonate decarboxylase
Deficiency of diphosphoric monoester hydrolase
Deficiency of D-lactate dehydrogenase
Deficiency of endo-1,3
Deficiency of endopeptidase
Deficiency of endoribonuclease
Deficiency of enolase
Deficiency of enoyl-coenzyme A hydratase
Deficiency of enteropeptidase
Deficiency of epimerase
Deficiency of erythritol kinase
Deficiency of estradiol 6beta-monooxygenase
Deficiency of ethanolamine-phosphate cytidylyltransferase
Deficiency of ethanolaminephosphotransferase
Deficiency of ether hydrolase
Deficiency of exoribonuclease
Deficiency of ferroxidase
Deficiency of formaldehyde dehydrogenase
Deficiency of formamidase
Deficiency of formate dehydrogenase
Deficiency of formate-tetrahydrofolate ligase
Deficiency of formiminotetrahydrofolate cyclodeaminase
Deficiency of formyltetrahydrofolate deformylase
Deficiency of fructose-bisphosphatase
Deficiency of fructose-bisphosphate aldolase
Deficiency of fumarate hydratase
Deficiency of fumarylacetoacetase
Deficiency of galactonolactone dehydrogenase
Deficiency of galactose dehydrogenase
Deficiency of gentisate l,2-dioxygenase
Deficiency of glucan 1,3-alpha-glucosidase
Deficiency of glucan 1,4-alpha-glucosidase
Deficiency of glucokinase
Deficiency of gluconate 2-dehydrogenase
Deficiency of gluconokinase
Deficiency of gluconolactonase
Deficiency of glucosamine acetyltransferase
Deficiency of glucosamine kinase
Deficiency of glucosamine-6-phosphate isomerase
Deficiency of glucosamine-phosphate acetyltransferase
Deficiency of glucose dehydrogenase
Deficiency of glucose oxidase
Deficiency of glucose-1-phosphatase
Deficiency of glucose-1-phosphate phosphodismutase
Deficiency of glucose-6-phosphate dehydrogenase
Deficiency of glutamate decarboxylase
Deficiency of glutamate dehydrogenase
Deficiency of glutamate-ammonia ligase
Deficiency of glutaminase
Deficiency of glutamine phenylacetyltransferase
Deficiency of glutamine-fructose-6-phosphate aminotransferase
Deficiency of glutamine-pyruvate aminotransferase
Deficiency of glutarate-CoA ligase
Deficiency of glutathione reductase
Deficiency of glutathione synthase
Deficiency of glutathione thiolesterase
Deficiency of glutathione-homocystine transhydrogenase
Deficiency of glyceraldehyde-3-phosphate dehydrogenase
Deficiency of glycerate kinase
Deficiency of glycerol kinase
Deficiency of glycerol-3-phosphate acyltransferase
Deficiency of glycerophosphatase
Deficiency of glycerophosphocholine phosphodiesterase
Deficiency of glycine acyltransferase
Deficiency of glycine amidinotransferase
Deficiency of glycine formiminotransferase
Deficiency of glycine hydroxymethyltransferase
Deficiency of glycosulfatase
Deficiency of glycosyltransferase
Deficiency of guanidinoacetate kinase
Deficiency of guanidinoacetate methyltransferase
Deficiency of guanine deaminase
Deficiency of guanosine monophosphate synthase
Deficiency of heparin lyase
Deficiency of hexokinase
Deficiency of hexose oxidase
Deficiency of hexosyltransferase
Deficiency of histidine ammonia-lyase
Deficiency of histidine decarboxylase
Deficiency of histidinol dehydrogenase
Deficiency of homocysteine desulfhydrase
Deficiency of homoserine kinase
Deficiency of hyaluronate lyase
Deficiency of hyaluronoglucosaminidase
Deficiency of hydrogen-sulfide acetyltransferase
Deficiency of hydrolase
Deficiency of hydrolyase
Deficiency of hydroxyacylglutathione hydrolase
Deficiency of hydroxyalkyl-protein kinase
Deficiency of hydroxymethylglutaryl-CoA hydrolase
Deficiency of hydroxymethylglutaryl-CoA lyase
Deficiency of hydroxymethylglutaryl-coenzyme A reductase
Deficiency of hydroxymethylglutaryl-coenzyme A synthase
Deficiency of hypoxanthine phosphoribosyltransferase
Deficiency of imidodipeptidase
Deficiency of iminodipeptidase
Deficiency of inorganic pyrophosphatase
Deficiency of inosinase
Deficiency of inosine monophosphate cyclohydrolase
Deficiency of inosine monophosphate dehydrogenase
Deficiency of inosine nucleosidase
Deficiency of iodide peroxidase
Deficiency of isocitrate dehydrogenase
Deficiency of isocitrate lyase
Deficiency of isoleucine-transfer ribonucleic acid ligase
Deficiency of isomerase
Deficiency of isopentenyl-diphosphate delta-isomerase
Deficiency of ketohexokinase
Deficiency of ketotetrose-phosphate aldolase
Deficiency of kynurenine 3-monooxygenase
Deficiency of kynurenine-oxoglutarate aminotransferase
Deficiency of lactate racemase
Deficiency of lactonase
Deficiency of lactoylglutathione lyase
Deficiency of L-amino-acid oxidase
Deficiency of L-arabinose dehydrogenase
Deficiency of L-asparagine amidohydrolase
Deficiency of lecithinase D
Deficiency of leucine aminopeptidase
Deficiency of leucine aminotransferase
Deficiency of leucine-transfer ribonucleic acid ligase
Deficiency of L-gulonate dehydrogenase
Deficiency of lichenase
Deficiency of ligase
Deficiency of lipophosphodiesterase II
Deficiency of L-lactate dehydrogenase
Deficiency of L-lactate dehydrogenase
Deficiency of long-chain fatty-acyl-coenzyme A hydrolase
Deficiency of long-chain-fatty-acid-CoA ligase
Deficiency of L-prolylglycine dipeptidase
Deficiency of L-serine dehydratase
Deficiency of lyase
Deficiency of lysine racemase
Deficiency of lysine-transfer ribonucleic acid ligase
Deficiency of lysolecithin acylmutase
Deficiency of lysophospholipase
Deficiency of lysozyme
Deficiency of malate dehydrogenase
Deficiency of malate dehydrogenase
Deficiency of malate dehydrogenase
Deficiency of malate oxidase
Deficiency of maleylacetoacetate isomerase
Deficiency of malonate CoA-transferase
Deficiency of malonyl-coenzyme A decarboxylase
Deficiency of maltose phosphorylase
Deficiency of mannitol dehydrogenase
Deficiency of mannokinase
Deficiency of mannose-6-phosphate isomerase
Deficiency of metallocarboxypeptidase
Deficiency of metalloproteinase
Deficiency of methenyltetrahydrofolate cyclohydrolase
Deficiency of methionine adenosyltransferase
Deficiency of methionine-transfer ribonucleic acid ligase
Deficiency of methylaspartate mutase
Deficiency of methylcrotonoyl-coenzyme A carboxylase
Deficiency of methylenetetrahydrofolate dehydrogenase
Deficiency of methylglutaconyl-coenzyme A hydratase
Deficiency of methylmalonyl-coenzyme A mutase
Deficiency of methyltransferase
Deficiency of mevaldate reductase
Deficiency of mevalonate kinase
Deficiency of monodehydroascorbate reductase
Deficiency of monooxygenase
Deficiency of mutase
Deficiency of myo-inositol oxygenase
Deficiency of N-acetyl-beta-glucosaminidase
Deficiency of N-acetylneuraminate lyase
Deficiency of NAPH cytochrome-c>2< reductase
Deficiency of nicotinamide adenine dinucleotidase
Deficiency of nicotinamide adenine dinucleotide ^+^ kinase
Deficiency of nicotinamide adenine dinucleotide ^+^ nucleosidase
Deficiency of nicotinamide adenine dinucleotide ^+^ synthase
Deficiency of nicotinamide adenine dinucleotide phosphate ^+^ nucleosidase
Deficiency of nicotinamide adenine dinucleotide phosphate ^+^ transhydrogenase
Deficiency of nicotinamide methyltransferase
Deficiency of nicotinamide phosphoribosyltransferase
Deficiency of nicotinamide-nucleotide adenylyltransferase
Deficiency of nicotinate dehydrogenase
Deficiency of nicotinate phosphoribosyltransferase
Deficiency of nitrate reductase
Deficiency of N-methyl-L-amino-acid oxidase
Deficiency of non-specific cholinesterase
Deficiency of nucleosidase
Deficiency of nucleoside-diphosphatase
Deficiency of nucleoside-diphosphate kinase
Deficiency of nucleoside-phosphate kinase
Deficiency of nucleotidase
Deficiency of nucleotide pyrophosphatase
Deficiency of nucleotidyltransferase
Deficiency of O-acetylserine
Deficiency of omega peptidase
Deficiency of orotate phosphoribosyltransferase
Deficiency of oxalate coenzyme A-transferase
Deficiency of oxidase
Deficiency of oximinotransferase
Deficiency of oxo-acid-lyase
Deficiency of oxoglutarate dehydrogenase
Deficiency of oxygenase
Deficiency of palmitoyl-coenzyme A hydrolase
Deficiency of pancreatic elastase
Deficiency of pantetheine kinase
Deficiency of pantetheine-phosphate adenylyltransferase
Deficiency of pantothenoylcysteine decarboxylase
Deficiency of pectin methoxylase
Deficiency of pectin methylesterase
Deficiency of pectinesterase
Deficiency of pentosyltransferase
Deficiency of pepsin A
Deficiency of pepsin B
Deficiency of peptidase a
Deficiency of peptide hydrolase
Deficiency of peptidoglycan endopeptidase
Deficiency of peroxidase
Deficiency of phenylalanine 4-monooxygenase
Deficiency of phenylpyruvate tautomerase
Deficiency of phosphatase
Deficiency of phosphatidate phosphatase
Deficiency of phosphoacetylglucosamine mutase
Deficiency of phosphoadenylate 3'-nucleotidase
Deficiency of phosphoamidase
Deficiency of phosphoglucokinase
Deficiency of phosphogluconate dehydrogenase
Deficiency of phosphogluconate dehydrogenase
Deficiency of phosphoglycerate kinase
Deficiency of phosphoglycerate mutase
Deficiency of phosphoketolase
Deficiency of phospholipase A>2<
Deficiency of phospholipase C
Deficiency of phospholipase D
Deficiency of phosphomevalonate kinase
Deficiency of phosphomonoesterase
Deficiency of phosphopantothenate-cysteine ligase
Deficiency of phosphoprotein phosphatase
Deficiency of phosphoribokinase
Deficiency of phosphoribosylamine-glycine ligase
Deficiency of phosphoribosylaminoimidazole carboxylase
Deficiency of phosphoribosylaminoimidazolecarboxamide formyltransferase
Deficiency of phosphoribosylaminoimidazole-succinocarboxamide synthase
Deficiency of phosphoribosylformylglycinamidine cyclo-ligase
Deficiency of phosphoribosylformylglycinamidine synthase
Deficiency of phosphoribosylglycinamide formyltransferase
Deficiency of phosphoric diester hydrolase
Deficiency of phosphoric monoester hydrolase
Deficiency of phosphorus-oxygen lyase
Deficiency of phosphorylase phosphatase
Deficiency of phosphoserine phosphatase
Deficiency of phosphotransferase
Deficiency of plasmin
Deficiency of polygalacturonase
Deficiency of polyribonucleotide nucleotidyltransferase
Deficiency of progesterone 11alpha-monooxygenase
Deficiency of prolidase
Deficiency of prolinase
Deficiency of proline dipeptidase
Deficiency of prolyl dipeptidase
Deficiency of propionyl-coenzyme A carboxylase
Deficiency of protein kinase
Deficiency of protocatechuate 3,4-dioxygenase
Deficiency of pyridoxal kinase
Deficiency of pyridoxamine-phosphate oxidase
Deficiency of pyrophosphotransferase
Deficiency of pyrroline-2-carboxylate reductase
Deficiency of pyrroline-5-carboxylate reductase
Deficiency of pyruvate decarboxylase
Deficiency of quinate dehydrogenase
Deficiency of racemase
Deficiency of reduced nicotinamide adenine dinucleotide dehydrogenase
Deficiency of reduced nicotinamide adenine dinucleotide phosphate dehydrogenase
Deficiency of reduced nicotinamide adenine dinucleotide phosphate-ferrihemoprotein reductase
Deficiency of reductase
Deficiency of renin
Deficiency of retinal isomerase
Deficiency of retinyl-palmitate esterase
Deficiency of rhamnulokinase
Deficiency of riboflavin kinase
Deficiency of riboflavin mononucleotide adenylyltransferase
Deficiency of ribokinase
Deficiency of ribonuclease
Deficiency of ribose-5-phosphate isomerase
Deficiency of ribose-phosphate pyrophosphokinase
Deficiency of ribosomal cathepsin
Deficiency of ribosomal neutral proteinase
Deficiency of ribosylnicotinamide kinase
Deficiency of ribulokinase
Deficiency of ribulose-phosphate 3-epimerase
Deficiency of sarcosine oxidase
Deficiency of sedoheptulokinase
Deficiency of serine carboxypeptidase
Deficiency of serine proteinase
Deficiency of serine-transfer ribonucleic acid ligase
Deficiency of shikimate dehydrogenase
Deficiency of sialidase
Deficiency of squalene monooxygenase
Deficiency of steroid 11-beta-monooxygenase
Deficiency of steroid 17-alpha-monooxygenase
Deficiency of steroid 21-monooxygenase
Deficiency of steroid delta-isomerase
Deficiency of succinate- coenzyme A ligase
Deficiency of succinate dehydrogenase
Deficiency of succinate-coenzyme A ligase
Deficiency of succinate-coenzyme A ligase
Deficiency of succinyl-coenzyme A hydrolase
Deficiency of sulfatase
Deficiency of sulfate adenylyltransferase
Deficiency of sulfinoalanine decarboxylase
Deficiency of sulfite reductase
Deficiency of sulfotransferase
Deficiency of sulfuric ester hydrolase
Deficiency of sulfurtransferase
Deficiency of tannase
Deficiency of thetin-homocysteine methyltransferase
Deficiency of thiamin pyridinylase
Deficiency of thiamin pyrophosphokinase
Deficiency of thioethanolamine acetyltransferase
Deficiency of thioether hydrolase
Deficiency of thiolester hydrolase
Deficiency of thiosulfate sulfurtransferase
Deficiency of threonine aldolase
Deficiency of threonine dehydratase
Deficiency of threonine-transfer ribonucleic acid ligase
Deficiency of thymidine phosphorylase
Deficiency of transacylase
Deficiency of transaldolase
Deficiency of transcarbamoylase
Deficiency of transcarboxylase
Deficiency of transferase
Deficiency of transformiminase
Deficiency of transformylase
Deficiency of transhydroxymethylase
Deficiency of transketolase
Deficiency of triacylglycerol lipase
Deficiency of trimetaphosphatase
Deficiency of triokinase
Deficiency of tripeptide aminopeptidase
Deficiency of triphosphoric monoester hydrolase
Deficiency of tropinesterase
Deficiency of true cholinesterase
Deficiency of trypsin
Deficiency of tryptophan 2,3-dioxygenase
Deficiency of tryptophan 5-monooxygenase
Deficiency of tryptophan-transfer ribonucleic acid ligase
Deficiency of tyraminase
Deficiency of tyrosine aminotransferase
Deficiency of tyrosine decarboxylase
Deficiency of tyrosine-transfer ribonucleic acid ligase
Deficiency of unspecific monooxygenase
Deficiency of uracil dehydrogenase
Deficiency of uracil phosphoribosyltransferase
Deficiency of urate oxidase
Deficiency of urease
Deficiency of uridine diphosphate-glucose dehydrogenase
Deficiency of uridine diphosphate-glucose-hexose-1-phosphate uridylyltransferase
Deficiency of uridine phosphorylase
Deficiency of uridine triphosphate-glucose-1-phosphate uridylyltransferase
Deficiency of uronolactonase
Deficiency of valine-transfer ribonucleic acid ligase
Deficiency of w-amidase
Deficiency of xanthine oxidase
Deficiency of xylan endo-1,3-beta-xylosidase
Deficiency of xylulokinase
Disorder involving deficiency of steryl-sulfatase
Glycerol kinase deficiency - contiguous gene syndrome
Hereditary angioedema
Hereditary angioedema with normal C1 esterase inhibitor activity
Metachromatic leukodystrophy due to deficiency of cerebroside sulfatase activator
Muscle L-lactate dehydrogenase deficiency
Pancreatic alpha-amylase deficiency
Phosphoglycerokinase deficiency
Specific enzyme deficiency
Succinate-coenzyme Q reductase deficiency
Ubiquinone dehydrogenase

Index to Diseases and Injuries

References found for the code 277.6 in the Index of Diseases and Injuries:

Angioedema allergic any site with urticaria 995.1
- hereditary 277.6

Angioneurotic edema allergic any site with urticaria 995.1
- hereditary 277.6

Deficiency deficient
- biotinidase 277.6
- bradykinase 1 277.6
- dihydropyrimidine dehydrogenase DPD 277.6
- enzymes circulating NEC NEC "Not elsewhere classifiable"
  This abbreviation in the index represents “other specified” when a specific code is not available for a condition the index directs the coder to the “other specified” code in the tabular. SEE ALSO See Also
  A “see also” instruction following a main term in the index instructs that there is another main term that may also be referenced that may provide additional index entries that may be useful. It is not necessary to follow the “see also” note when the original main term provides the necessary code. Deficiency by specific enzyme 277.6

Dihydropyrimidine dehydrogenase disease DPD 277.6

DPD dihydropyrimidine dehydrogenase deficiency 277.6

Edema edematous 782.3
- angioneurotic allergic any site with urticaria 995.1
  - hereditary 277.6
- circumscribed acute 995.1
  - hereditary 277.6
- essential acute 995.1
  - hereditary 277.6
- glottis glottic glottides obstructive passive 478.6
  - allergic 995.1
    - hereditary 277.6
- periodic 995.1
  - hereditary 277.6
- Quincke s 995.1
  - hereditary 277.6

Giant
- urticaria 995.1
  - hereditary 277.6

Opisthognathism 524.00

Periodic SEE ALSO See Also
A “see also” instruction following a main term in the index instructs that there is another main term that may also be referenced that may provide additional index entries that may be useful. It is not necessary to follow the “see also” note when the original main term provides the necessary code. condition
- edema 995.1
  - hereditary 277.6

Urticaria 708.9
- with angioneurotic edema 995.1
  - hereditary 277.6
- giant 995.1
  - hereditary 277.6
- gigantea 995.1
  - hereditary 277.6
- larynx 995.1
  - hereditary 277.6

ICD-9 Footnotes

General Equivalence Map Definitions
The ICD-9 and ICD-10 GEMs are used to facilitate linking between the diagnosis codes in ICD-9-CM and the new ICD-10-CM code set. The GEMs are the raw material from which providers, health information vendors and payers can derive specific applied mappings to meet their needs.

Approximate Flag - The approximate flag is on, indicating that the relationship between the code in the source system and the code in the target system is an approximate equivalent.
No Map Flag - The no map flag indicates that a code in the source system is not linked to any code in the target system.
Combination Flag - The combination flag indicates that more than one code in the target system is required to satisfy the full equivalent meaning of a code in the source system.

Index of Diseases and Injuries Definitions

And - The word "and" should be interpreted to mean either "and" or "or" when it appears in a title.
Code also note - A "code also" note instructs that two codes may be required to fully describe a condition, but this note does not provide sequencing direction.
Code first - Certain conditions have both an underlying etiology and multiple body system manifestations due to the underlying etiology. For such conditions, the ICD-10-CM has a coding convention that requires the underlying condition be sequenced first followed by the manifestation. Wherever such a combination exists, there is a "use additional code" note at the etiology code, and a "code first" note at the manifestation code. These instructional notes indicate the proper sequencing order of the codes, etiology followed by manifestation.
Type 1 Excludes Notes - A type 1 Excludes note is a pure excludes note. It means "NOT CODED HERE!" An Excludes1 note indicates that the code excluded should never be used at the same time as the code above the Excludes1 note. An Excludes1 is used when two conditions cannot occur together, such as a congenital form versus an acquired form of the same condition.
Type 2 Excludes Notes - A type 2 Excludes note represents "Not included here". An excludes2 note indicates that the condition excluded is not part of the condition represented by the code, but a patient may have both conditions at the same time. When an Excludes2 note appears under a code, it is acceptable to use both the code and the excluded code together, when appropriate.
Includes Notes - This note appears immediately under a three character code title to further define, or give examples of, the content of the category.
Inclusion terms - List of terms is included under some codes. These terms are the conditions for which that code is to be used. The terms may be synonyms of the code title, or, in the case of "other specified" codes, the terms are a list of the various conditions assigned to that code. The inclusion terms are not necessarily exhaustive. Additional terms found only in the Alphabetic Index may also be assigned to a code.
NEC "Not elsewhere classifiable" - This abbreviation in the Alphabetic Index represents "other specified". When a specific code is not available for a condition, the Alphabetic Index directs the coder to the "other specified” code in the Tabular List.
NOS "Not otherwise specified" - This abbreviation is the equivalent of unspecified.
See - The "see" instruction following a main term in the Alphabetic Index indicates that another term should be referenced. It is necessary to go to the main term referenced with the "see" note to locate the correct code.
See Also - A "see also" instruction following a main term in the Alphabetic Index instructs that there is another main term that may also be referenced that may provide additional Alphabetic Index entries that may be useful. It is not necessary to follow the "see also" note when the original main term provides the necessary code.
7th Characters - Certain ICD-10-CM categories have applicable 7th characters. The applicable 7th character is required for all codes within the category, or as the notes in the Tabular List instruct. The 7th character must always be the 7th character in the data field. If a code that requires a 7th character is not 6 characters, a placeholder X must be used to fill in the empty characters.
With - The word "with" should be interpreted to mean "associated with" or "due to" when it appears in a code title, the Alphabetic Index, or an instructional note in the Tabular List. The word "with" in the Alphabetic Index is sequenced immediately following the main term, not in alphabetical order.

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