2024 ICD-10-CM Diagnosis Code Q61.4

Renal dysplasia

ICD-10-CM Code:
Q61.4
ICD-10 Code for:
Renal dysplasia
Is Billable?
Yes - Valid for Submission
Chronic Condition Indicator: [1]
Chronic
Code Navigator:

Code Classification

  • Congenital malformations, deformations and chromosomal abnormalities
    (Q00-Q99)
    • Congenital malformations of the urinary system
      (Q60-Q64)
      • Cystic kidney disease
        (Q61)

Q61.4 is a billable diagnosis code used to specify a medical diagnosis of renal dysplasia. The code is valid during the current fiscal year for the submission of HIPAA-covered transactions from October 01, 2023 through September 30, 2024. The code is exempt from present on admission (POA) reporting for inpatient admissions to general acute care hospitals.

Approximate Synonyms

The following clinical terms are approximate synonyms or lay terms that might be used to identify the correct diagnosis code:

  • Bilateral multicystic renal dysplasia
  • Bilateral renal dysplasia
  • Bilateral secondary renal dysplasia
  • BRESEK syndrome
  • Cystic dysplasia of kidney
  • Dysplasia of left kidney
  • Dysplasia of left kidney
  • Dysplasia of right kidney
  • Dysplasia of right kidney
  • Fibrosis of pancreas
  • Hydranencephaly
  • Left kidney absent
  • Left renal agenesis
  • Left renal agenesis co-occurrent with right renal dysplasia
  • MARCH syndrome
  • Multicystic renal dysplasia
  • Multiple renal cysts
  • Multiple renal cysts
  • Multiple renal cysts
  • Nephronophthisis
  • Primary renal dysplasia
  • Renal agenesis
  • Renal agenesis
  • Renal dysplasia
  • Renal dysplasia and retinal aplasia
  • Renal dysplasia due to fetal exposure to angiotensin converting enzyme inhibitor
  • Renal hepatic pancreatic dysplasia
  • Retinal pigment epithelial dystrophy
  • Right kidney absent
  • Right renal agenesis
  • Right renal agenesis co-occurrent with left renal dysplasia
  • Saldino-Mainzer dysplasia
  • Secondary renal dysplasia
  • Thymic, renal, anal, lung dysplasia syndrome
  • Torticollis, keloids, cryptorchidism, renal dysplasia syndrome
  • Ulbright Hodes syndrome
  • Unilateral multicystic renal dysplasia

Clinical Classification

Clinical Information

  • Hydranencephaly

    a congenital condition where the greater portions of the cerebral hemispheres and corpus striatum are replaced by csf and glial tissue. the meninges and the skull are well formed, which is consistent with earlier normal embryogenesis of the telencephalon. bilateral occlusions of the internal carotid arteries in utero is a potential mechanism. clinical features include intact brainstem reflexes without evidence of higher cortical activity. (menkes, textbook of child neurology, 5th ed, p307)
  • Bilateral Renal Agenesis

    a congenital abnormality characterized by the absence of both kidneys.
  • Renal Agenesis

    a congenital abnormality characterized by the absence of one or both kidneys.
  • Unilateral Renal Agenesis|Congenital Single Kidney|Congenital Solitary Kidney|Congenital Solitary Kidney

    a congenital abnormality characterized by the presence of only one kidney.
  • Bilateral Renal Dysplasia

    a finding of congenital malformations in both kidneys characterized by the presence of cysts of various sizes, primitive ducts, islands of metaplastic cartilage and undifferentiated mesenchyme, and the absence of cortico-medullary demarcation.
  • Nephrocystin-1|Juvenile Nephronophthisis 1 Protein|NPHP1

    nephrocystin-1 (732 aa, ~83 kda) is encoded by the human nphp1 gene. this protein is involved in the modulation of signaling.
  • Nephronophthisis

    progressive tubulointerstitial injury, inherited in an autosomal recessive pattern, caused by mutations in genes involved in ciliary function, which may result in an end stage renal failure.
  • Nephronophthisis 1|Familial Juvenile Nephronophthisis|Juvenile Nephronophthisis|NPH1

    progressive tubulointerstitial nephritis inherited in an autosomal recessive manner. it is caused by mutations in the nphp1 gene. patients present with anemia, polyuria, and polydipsia during childhood. the progressive bilateral kidney damage results in renal failure.
  • NPHP1 Gene|NPHP1|NPHP1|Nephronophthisis 1 (Juvenile) Gene

    this gene is involved in the mediation of signal transduction.
  • NPHP1 wt Allele|FLJ97602|JBTS4|NPH1|Nephronophthisis 1 (Juvenile) wt Allele|SLSN1

    human nphp1 wild-type allele is located in the vicinity of 2q13 and is approximately 83 kb in length. this allele, which encodes nephrocystin-1 protein, plays a role in the progression of adhesion-dependent signaling pathways. mutations in the gene are associated with familial juvenile nephronophthisis type 1, senior-loken syndrome type 1, and joubert syndrome type 4.
  • Hydranencephaly

    a rare congenital brain disorder in which the cerebral hemispheres are absent and replaced by sacs that contain cerebrospinal fluid. signs and symptoms include irritability, increased muscle tone, seizures, and hydrocephalus. the prognosis is poor.

Tabular List of Diseases and Injuries

The following annotation back-references are applicable to this diagnosis code. The Tabular List of Diseases and Injuries is a list of ICD-10-CM codes, organized "head to toe" into chapters and sections with coding notes and guidance for inclusions, exclusions, descriptions and more.


Inclusion Terms

Inclusion Terms
These terms are the conditions for which that code is to be used. The terms may be synonyms of the code title, or, in the case of "other specified" codes, the terms are a list of the various conditions assigned to that code. The inclusion terms are not necessarily exhaustive. Additional terms found only in the Alphabetic Index may also be assigned to a code.
  • Multicystic dysplastic kidney
  • Multicystic kidney (development)
  • Multicystic kidney disease
  • Multicystic renal dysplasia

Type 1 Excludes

Type 1 Excludes
A type 1 excludes note is a pure excludes note. It means "NOT CODED HERE!" An Excludes1 note indicates that the code excluded should never be used at the same time as the code above the Excludes1 note. An Excludes1 is used when two conditions cannot occur together, such as a congenital form versus an acquired form of the same condition.

Index to Diseases and Injuries References

The following annotation back-references for this diagnosis code are found in the injuries and diseases index. The Index to Diseases and Injuries is an alphabetical listing of medical terms, with each term mapped to one or more ICD-10-CM code(s).

Present on Admission (POA)

Q61.4 is exempt from POA reporting - The Present on Admission (POA) indicator is used for diagnosis codes included in claims involving inpatient admissions to general acute care hospitals. POA indicators must be reported to CMS on each claim to facilitate the grouping of diagnoses codes into the proper Diagnostic Related Groups (DRG). CMS publishes a listing of specific diagnosis codes that are exempt from the POA reporting requirement. Review other POA exempt codes here.

CMS POA Indicator Options and Definitions

POA IndicatorReason for CodeCMS will pay the CC/MCC DRG?
YDiagnosis was present at time of inpatient admission.YES
NDiagnosis was not present at time of inpatient admission.NO
UDocumentation insufficient to determine if the condition was present at the time of inpatient admission.NO
WClinically undetermined - unable to clinically determine whether the condition was present at the time of inpatient admission.YES
1Unreported/Not used - Exempt from POA reporting. NO

Convert Q61.4 to ICD-9-CM

  • ICD-9-CM Code: 753.15 - Renal dysplasia

Patient Education


Kidney Cysts

A cyst is a fluid-filled sac. You may get simple kidney cysts as you age; they are usually harmless. There are also some diseases which cause kidney cysts. One type is polycystic kidney disease (PKD). It runs in families. In PKD, many cysts grow in the kidneys. This can enlarge the kidneys and make them work poorly. About half of people with the most common type of PKD end up with kidney failure. PKD also causes cysts in other parts of the body, such as the liver.

Often, there are no symptoms at first. Later, symptoms include:

  • Pain in the back and lower sides
  • Headaches
  • Blood in the urine

Doctors diagnose PKD with imaging tests and family history. There is no cure. Treatments can help with symptoms and complications. They include medicines and lifestyle changes, and if there is kidney failure, dialysis or kidney transplants.

Acquired cystic kidney disease (ACKD) happens in people who have chronic kidney disease, especially if they are on dialysis. Unlike PKD, the kidneys are normal sized, and cysts do not form in other parts of the body. ACKD often has no symptoms. Usually, the cysts are harmless and do not need treatment. If they do cause complications, treatments include medicines, draining the cysts, or surgery.

NIH: National Institute of Diabetes and Digestive and Kidney Diseases


[Learn More in MedlinePlus]

Multicystic Dysplastic Kidney

Learn about symptoms, causes, diagnosis, and treatment of multicystic dysplastic kidney, which occurs when a baby’s kidneys do not develop normally in the womb.
[Learn More in MedlinePlus]

Code History

  • FY 2024 - No Change, effective from 10/1/2023 through 9/30/2024
  • FY 2023 - No Change, effective from 10/1/2022 through 9/30/2023
  • FY 2022 - No Change, effective from 10/1/2021 through 9/30/2022
  • FY 2021 - No Change, effective from 10/1/2020 through 9/30/2021
  • FY 2020 - No Change, effective from 10/1/2019 through 9/30/2020
  • FY 2019 - No Change, effective from 10/1/2018 through 9/30/2019
  • FY 2018 - No Change, effective from 10/1/2017 through 9/30/2018
  • FY 2017 - No Change, effective from 10/1/2016 through 9/30/2017
  • FY 2016 - New Code, effective from 10/1/2015 through 9/30/2016. This was the first year ICD-10-CM was implemented into the HIPAA code set.

Footnotes

[1] Chronic - a chronic condition code indicates a condition lasting 12 months or longer and its effect on the patient based on one or both of the following criteria:

  • The condition results in the need for ongoing intervention with medical products,treatment, services, and special equipment
  • The condition places limitations on self-care, independent living, and social interactions.