2024 ICD-10-CM Diagnosis Code L44.0

Pityriasis rubra pilaris

ICD-10-CM Code:
L44.0
ICD-10 Code for:
Pityriasis rubra pilaris
Is Billable?
Yes - Valid for Submission
Chronic Condition Indicator: [1]
Chronic
Code Navigator:

Code Classification

  • Diseases of the skin and subcutaneous tissue
    (L00–L99)
    • Papulosquamous disorders
      (L40-L45)
      • Other papulosquamous disorders
        (L44)

L44.0 is a billable diagnosis code used to specify a medical diagnosis of pityriasis rubra pilaris. The code is valid during the current fiscal year for the submission of HIPAA-covered transactions from October 01, 2023 through September 30, 2024.

Approximate Synonyms

The following clinical terms are approximate synonyms or lay terms that might be used to identify the correct diagnosis code:

  • Adult pityriasis rubra pilaris
  • Atypical adult pityriasis rubra pilaris
  • Atypical juvenile pityriasis rubra pilaris
  • Circumscribed juvenile pityriasis rubra pilaris
  • Classical adult pityriasis rubra pilaris
  • Classical juvenile pityriasis rubra pilaris
  • Disorder of skin due to human immunodeficiency virus infection
  • Juvenile pityriasis rubra pilaris
  • Nail dystrophy due to pityriasis rubra pilaris
  • Pityriasis rubra pilaris
  • Pityriasis rubra pilaris
  • Pityriasis rubra pilaris
  • Pityriasis rubra pilaris due to human immunodeficiency virus infection

Clinical Classification

Clinical Information

  • Pityriasis Rubra Pilaris

    a chronic skin disease characterized by small follicular papules, disseminated reddish-brown scaly patches, and often, palmoplantar hyperkeratosis. the papules are about the size of a pin and topped by a horny plug.
  • Pityriasis Rubra Pilaris

    a rare cutaneous disorder of unknown etiology characterized by the presence of reddish-orange scaly plaques, palmoplantar keratoderma, keratotic follicular papules, and confluent erythematous areas with areas of normal skin between the lesions.

Index to Diseases and Injuries References

The following annotation back-references for this diagnosis code are found in the injuries and diseases index. The Index to Diseases and Injuries is an alphabetical listing of medical terms, with each term mapped to one or more ICD-10-CM code(s).

Convert L44.0 to ICD-9-CM

  • ICD-9-CM Code: 696.4 - Pityriasis rubra pilaris
    Approximate Flag - The approximate mapping means there is not an exact match between the ICD-10 and ICD-9 codes and the mapped code is not a precise representation of the original code.
  • ICD-9-CM Code: 696.8 - Psorias related dis NEC
    Approximate Flag - The approximate mapping means there is not an exact match between the ICD-10 and ICD-9 codes and the mapped code is not a precise representation of the original code.

Patient Education


Skin Conditions

What does your skin do?

Your skin is your body's largest organ. It covers the entire outside of your body. There are many ways that your skin protects your body and helps keep you healthy. For example, it:

  • Holds body fluids in, which helps prevent you from getting dehydrated
  • Keeps out harmful germs, which helps prevent infections
  • Helps you feel things like heat, cold, and pain
  • Helps control your body temperature
  • Makes vitamin D when the sun shines on it
  • Shields your body against heat and light

What problems and conditions can affect your skin?

There are many different problems and conditions which can affect your skin. Some of them can cause uncomfortable symptoms, such as itching, burning, redness, and rashes. They might also affect your appearance. Some of the more common skin conditions include:

  • Acne, which causes pimples when hair follicles under your skin get clogged up
  • Burns
  • Cuts and scrapes
  • Dandruff, flaking of the skin on your scalp (the top of your head)
  • Eczema (atopic dermatitis), which causes inflammation, redness, and irritation of the skin
  • Hives, which are red and sometimes itchy bumps on your skin
  • Insect bites
  • Psoriasis, which causes itchy, scaly red patches
  • Skin cancer
  • Skin infections

How can I keep my skin healthy?

Since your skin protects your body in many ways, it's important to try to keep your skin healthy. For example, you can:

  • Wear the right protective equipment, like gloves, long sleeves, knee and elbow pads, or helmets to protect against cuts, bumps and scrapes.
  • If you do get a cut or scrape, clean it right away with soap and warm water. Put on a bandage to protect it while it heals.
  • When you are spending time outdoors, wear long sleeves and pants and use insect repellant to prevent insect bites.
  • Prevent sunburn by covering up and using sunscreen when outdoors.
  • Wash your hands often with soap and water.
  • When you take a shower or bath, use warm (not hot) water. Use mild cleansers and wash gently (don't scrub).
  • Use moisturizers, like lotions, creams, or ointments, to prevent dry skin.

NIH: National Institute of Arthritis and Musculoskeletal and Skin Diseases


[Learn More in MedlinePlus]

Familial pityriasis rubra pilaris

Familial pityriasis rubra pilaris is a rare genetic condition that affects the skin. The name of the condition reflects its major features: The term "pityriasis" refers to scaling; "rubra" means redness; and "pilaris" suggests the involvement of hair follicles in this disorder. Affected individuals have a salmon-colored skin rash covered in fine scales. This rash occurs in patches all over the body, with distinct areas of unaffected skin between the patches. Affected individuals also develop bumps called follicular keratoses that occur around hair follicles. The skin on the palms of the hands and soles of the feet often becomes thick, hard, and callused, a condition known as palmoplantar keratoderma.

Researchers have distinguished six types of pityriasis rubra pilaris based on the features of the disorder and the age at which signs and symptoms appear. The familial form is usually considered part of type V, which is also known as the atypical juvenile type. People with familial pityriasis rubra pilaris typically have skin abnormalities from birth or early childhood, and these skin problems persist throughout life.


[Learn More in MedlinePlus]

Code History

  • FY 2024 - No Change, effective from 10/1/2023 through 9/30/2024
  • FY 2023 - No Change, effective from 10/1/2022 through 9/30/2023
  • FY 2022 - No Change, effective from 10/1/2021 through 9/30/2022
  • FY 2021 - No Change, effective from 10/1/2020 through 9/30/2021
  • FY 2020 - No Change, effective from 10/1/2019 through 9/30/2020
  • FY 2019 - No Change, effective from 10/1/2018 through 9/30/2019
  • FY 2018 - No Change, effective from 10/1/2017 through 9/30/2018
  • FY 2017 - No Change, effective from 10/1/2016 through 9/30/2017
  • FY 2016 - New Code, effective from 10/1/2015 through 9/30/2016. This was the first year ICD-10-CM was implemented into the HIPAA code set.

Footnotes

[1] Chronic - a chronic condition code indicates a condition lasting 12 months or longer and its effect on the patient based on one or both of the following criteria:

  • The condition results in the need for ongoing intervention with medical products,treatment, services, and special equipment
  • The condition places limitations on self-care, independent living, and social interactions.