Other necrotizing vasculopathies (M31)
Clinical Information
Giant Cell Arteritis - A systemic autoimmune disorder that typically affects medium and large ARTERIES, usually leading to occlusive granulomatous vasculitis with transmural infiltrate containing multinucleated GIANT CELLS. The TEMPORAL ARTERY is commonly involved. This disorder appears primarily in people over the age of 50. Symptoms include FEVER; FATIGUE; HEADACHE; visual impairment; pain in the jaw and tongue; and aggravation of pain by cold temperatures. (From Adams et al., Principles of Neurology, 6th ed)
Granulomatosis with Polyangiitis - A multisystemic disease of a complex genetic background. It is characterized by inflammation of the blood vessels (VASCULITIS) leading to damage in any number of organs. The common features include granulomatous inflammation of the RESPIRATORY TRACT and KIDNEYS. Most patients have measurable autoantibodies (ANTINEUTROPHIL CYTOPLASMIC ANTIBODIES) against MYELOBLASTIN.
Microscopic Polyangiitis - A primary systemic vasculitis of small- and some medium-sized vessels. It is characterized by a tropism for kidneys and lungs, positive association with anti-neutrophil cytoplasmic antibodies (ANCA), and a paucity of immunoglobulin deposits in vessel walls.
Polymyalgia Rheumatica - A syndrome in the elderly characterized by proximal joint and muscle pain, high erythrocyte sedimentation rate, and a self-limiting course. Pain is usually accompanied by evidence of an inflammatory reaction. Women are affected twice as commonly as men and Caucasians more frequently than other groups. The condition is frequently associated with GIANT CELL ARTERITIS and some theories pose the possibility that the two diseases arise from a single etiology or even that they are the same entity.
Rheumatoid Vasculitis - Necrotizing VASCULITIS of small and medium size vessels, developing as a complication in RHEUMATOID ARTHRITIS patients. It is characterized by peripheral vascular lesions, cutaneous ULCERS, peripheral GANGRENE, and MONONEURITIS MULTIPLEX.
Diseases of the musculoskeletal system and connective tissue (M00–M99)
Systemic connective tissue disorders (M30-M36)
M31 Other necrotizing vasculopathies
- M31.0 Hypersensitivity angiitis
M31.1 Thrombotic microangiopathy
- M31.10 Thrombotic microangiopathy, unspecified
- M31.11 Hematopoietic stem cell transplantation-associated thrombotic microangiopathy [HSCT-TMA]
- M31.19 Other thrombotic microangiopathy
- M31.2 Lethal midline granuloma
M31.3 Wegener's granulomatosis
- M31.30 Wegener's granulomatosis without renal involvement
- M31.31 Wegener's granulomatosis with renal involvement
- M31.4 Aortic arch syndrome [Takayasu]
- M31.5 Giant cell arteritis with polymyalgia rheumatica
- M31.6 Other giant cell arteritis
- M31.7 Microscopic polyangiitis
- M31.8 Other specified necrotizing vasculopathies
- M31.9 Necrotizing vasculopathy, unspecified
Other necrotizing vasculopathies (M31)