2024 ICD-10-CM Diagnosis Code G60.0

Hereditary motor and sensory neuropathy

ICD-10-CM Code:
G60.0
ICD-10 Code for:
Hereditary motor and sensory neuropathy
Is Billable?
Yes - Valid for Submission
Chronic Condition Indicator: [1]
Chronic
Code Navigator:

Code Classification

  • Diseases of the nervous system
    (G00–G99)
    • Polyneuropathies and other disorders of the peripheral nervous system
      (G60-G65)
      • Hereditary and idiopathic neuropathy
        (G60)

G60.0 is a billable diagnosis code used to specify a medical diagnosis of hereditary motor and sensory neuropathy. The code is valid during the current fiscal year for the submission of HIPAA-covered transactions from October 01, 2023 through September 30, 2024.

Approximate Synonyms

The following clinical terms are approximate synonyms or lay terms that might be used to identify the correct diagnosis code:

  • 46,XY gonadal dysgenesis, motor and sensory neuropathy syndrome
  • Acute hepatic failure
  • Acute infantile liver failure, cerebellar ataxia, peripheral sensory motor neuropathy syndrome
  • Autosomal dominant Charcot-Marie-Tooth disease type 2
  • Autosomal dominant Charcot-Marie-Tooth disease type 2 due to DGAT2 mutation
  • Autosomal dominant Charcot-Marie-Tooth disease type 2 due to KIF5A mutation
  • Autosomal dominant Charcot-Marie-Tooth disease type 2 due to TFG mutation
  • Autosomal dominant Charcot-Marie-Tooth disease type 2 with giant axons
  • Autosomal dominant Charcot-Marie-Tooth disease type 2A1
  • Autosomal dominant Charcot-Marie-Tooth disease type 2A2
  • Autosomal dominant Charcot-Marie-Tooth disease type 2B
  • Autosomal dominant Charcot-Marie-Tooth disease type 2C
  • Autosomal dominant Charcot-Marie-Tooth disease type 2D
  • Autosomal dominant Charcot-Marie-Tooth disease type 2DD
  • Autosomal dominant Charcot-Marie-Tooth disease type 2E
  • Autosomal dominant Charcot-Marie-Tooth disease type 2F
  • Autosomal dominant Charcot-Marie-Tooth disease type 2G
  • Autosomal dominant Charcot-Marie-Tooth disease type 2I
  • Autosomal dominant Charcot-Marie-Tooth disease type 2J
  • Autosomal dominant Charcot-Marie-Tooth disease type 2K
  • Autosomal dominant Charcot-Marie-Tooth disease type 2L
  • Autosomal dominant Charcot-Marie-Tooth disease type 2M
  • Autosomal dominant Charcot-Marie-Tooth disease type 2N
  • Autosomal dominant Charcot-Marie-Tooth disease type 2O
  • Autosomal dominant Charcot-Marie-Tooth disease type 2Q
  • Autosomal dominant Charcot-Marie-Tooth disease type 2U
  • Autosomal dominant Charcot-Marie-Tooth disease type 2V
  • Autosomal dominant Charcot-Marie-Tooth disease type 2W
  • Autosomal dominant Charcot-Marie-Tooth disease type 2Y
  • Autosomal dominant Charcot-Marie-Tooth disease type 2Z
  • Autosomal dominant distal axonal motor neuropathy, myofibrillar myopathy syndrome
  • Autosomal dominant distal hereditary motor neuropathy
  • Autosomal dominant distal hereditary motor neuropathy
  • Autosomal dominant intermediate Charcot-Marie-Tooth disease type A
  • Autosomal dominant intermediate Charcot-Marie-Tooth disease type B
  • Autosomal dominant intermediate Charcot-Marie-Tooth disease type C
  • Autosomal dominant intermediate Charcot-Marie-Tooth disease type D
  • Autosomal dominant intermediate Charcot-Marie-Tooth disease type E
  • Autosomal dominant intermediate Charcot-Marie-Tooth disease type F
  • Autosomal dominant intermediate Charcot-Marie-Tooth disease with neuropathic pain
  • Autosomal dominant slowed nerve conduction velocity
  • Autosomal recessive axonal Charcot-Marie-Tooth disease due to copper metabolism defect
  • Autosomal recessive Charcot-Marie-Tooth disease type 2
  • Autosomal recessive Charcot-Marie-Tooth disease type 2
  • Autosomal recessive Charcot-Marie-Tooth disease type 2X
  • Autosomal recessive Charcot-Marie-Tooth disease with hoarseness
  • Autosomal recessive distal hereditary motor neuropathy
  • Autosomal recessive intermediate Charcot-Marie-Tooth disease type A
  • Autosomal recessive intermediate Charcot-Marie-Tooth disease type B
  • Autosomal recessive intermediate Charcot-Marie-Tooth disease type C
  • Autosomal recessive intermediate Charcot-Marie-Tooth disease type D
  • Autosomal recessive lethal neonatal axonal sensorimotor polyneuropathy
  • Axonal neuropathy
  • Axonal neuropathy
  • Axonal neuropathy
  • Charcot-Marie-Tooth disease type 2B1
  • Charcot-Marie-Tooth disease type 2B2
  • Charcot-Marie-Tooth disease type 2B5
  • Charcot-Marie-Tooth disease type 2H
  • Charcot-Marie-Tooth disease type 2P
  • Charcot-Marie-Tooth disease type 2R
  • Charcot-Marie-Tooth disease type 2S
  • Charcot-Marie-Tooth disease type 2T
  • Charcot-Marie-Tooth disease type 4
  • Charcot-Marie-Tooth disease type 4A
  • Charcot-Marie-Tooth disease type 4B1
  • Charcot-Marie-Tooth disease type 4B2
  • Charcot-Marie-Tooth disease type 4B3
  • Charcot-Marie-Tooth disease type 4C
  • Charcot-Marie-Tooth disease type 4D
  • Charcot-Marie-Tooth disease type 4E
  • Charcot-Marie-Tooth disease type 4F
  • Charcot-Marie-Tooth disease type 4G
  • Charcot-Marie-Tooth disease type 4H
  • Charcot-Marie-Tooth disease type 4J
  • Charcot-Marie-Tooth disease type ID
  • Charcot-Marie-Tooth disease type IE
  • Charcot-Marie-Tooth disease type IF
  • Charcot-Marie-Tooth disease, deafness, intellectual disability syndrome
  • Charcot-Marie-Tooth disease, type IA
  • Charcot-Marie-Tooth disease, type IB
  • Charcot-Marie-Tooth disease, type IC
  • Charcot-Marie-Tooth disease, type II
  • Charcot-Marie-Tooth Neuropathy Type 4
  • Congenital axonal neuropathy with encephalopathy
  • Congenital polyneuropathy
  • Déjérine-Sottas disease
  • Disorder of copper metabolism
  • Distal hereditary motor neuropathy type 5
  • Distal hereditary motor neuropathy type 7
  • Distal spinal muscular atrophy
  • DNAJB2-related Charcot-Marie-Tooth disease type 2
  • Hereditary hypertrophic neuropathy with paraproteinemia
  • Hereditary liability to pressure palsies
  • Hereditary motor and sensory neuropathy
  • Hereditary motor and sensory neuropathy Okinawa type
  • Hereditary motor and sensory neuropathy with acrodystrophy
  • Hereditary motor and sensory neuropathy with optic atrophy
  • Hereditary motor and sensory neuropathy with retinitis pigmentosa
  • Hereditary sensorimotor neuropathy with hyperelastic skin
  • Hereditary sensory and autonomic neuropathy type 1B
  • Hereditary sensory and autonomic neuropathy type I
  • Hereditary sensory and autonomic neuropathy type II
  • Hereditary sensory and autonomic neuropathy with deafness and global delay
  • Hereditary sensory autonomic neuropathy type IA
  • Hereditary sensory autonomic neuropathy type IC
  • Hereditary sensory autonomic neuropathy type ID
  • Hereditary sensory autonomic neuropathy type IE
  • Hereditary sensory autonomic neuropathy type IIA
  • Hereditary sensory autonomic neuropathy type IIB
  • Hereditary sensory-motor neuropathy, type I
  • Hereditary thermosensitive neuropathy
  • Hypertrophic interstitial neuropathy
  • Infantile-onset axonal motor and sensory neuropathy, optic atrophy, neurodegenerative syndrome
  • Microcephalus, complex motor and sensory axonal neuropathy syndrome
  • Mixed sensory-motor polyneuropathy
  • Mixed sensory-motor polyneuropathy
  • MME-related autosomal dominant Charcot Marie Tooth disease type 2
  • Motor polyneuropathy
  • Motor polyneuropathy
  • Palmoplantar keratoderma, hereditary motor and sensory neuropathy syndrome
  • Paralysis of glottis
  • Peripheral axonal neuropathy
  • PMP2-related Charcot-Marie-Tooth disease type 1
  • Roussy-Lévy syndrome
  • Sensory polyneuropathy
  • Sensory polyneuropathy
  • Severe early-onset axonal neuropathy due to mitofusin 2 deficiency
  • SURF1-related Charcot-Marie-Tooth disease type 4
  • Vocal cord paralysis
  • X-linked Charcot-Marie-Tooth disease type 1
  • X-linked Charcot-Marie-Tooth disease type 2
  • X-linked Charcot-Marie-Tooth disease type 3
  • X-linked Charcot-Marie-Tooth disease type 4
  • X-linked Charcot-Marie-Tooth disease type 5
  • X-linked Charcot-Marie-Tooth disease type 6
  • X-linked distal hereditary motor neuropathy
  • X-linked hereditary motor and sensory neuropathy
  • Young adult-onset distal hereditary motor neuropathy

Clinical Classification

Clinical Information

  • Vocal Cord Paralysis

    congenital or acquired paralysis of one or both vocal cords. this condition is caused by defects in the central nervous system, the vagus nerve and branches of laryngeal nerves. common symptoms are voice disorders including hoarseness or aphonia.
  • Acute Motor and Sensory Axonal Neuropathy|Acute Motor And Sensory Axonal Neuropathy|Acute Motor-Sensory Axonal Neuropathy|Acute Motor-Sensory Axonal Neuropathy

    a subtype of guillain-barre syndrome that targets sensory motor axons, and is characterized by acute onset of quadriparesis, distal sensory loss, areflexia, and respiratory insufficiency.
  • Acute Motor Axonal Neuropathy|AMAN

    a subtype of guillain-barre syndrome that targets motor axons, and is characterized by symmetric limb weakness, diffuse areflexia, facial and oropharyngeal muscle weakness, and respiratory insufficiency.
  • Axonal Neuropathy

    any nerve disorder affecting the axon of a nerve.
  • GAN wt Allele|GAN1|Giant Axonal Neuropathy (Gigaxonin) Gene|Gigaxonin wt Allele|KLHL16

    human gan wild-type allele is located in the vicinity of 16q24.1 and is approximately 65 kb in length. this allele, which encodes gigaxonin protein, is involved in both ubiquitination and neurofilament structure. mutation of the gene is associated with giant axonal neuropathy.
  • Giant Axonal Neuropathy

    a rare inherited disorder affecting the neurofilaments. it is caused by mutations in the gan gene. it is characterized by the presence of abnormally large nerve cell axons. signs and symptoms include difficulty walking, sensory disturbances, lack of motor coordination and abnormal reflexes in the limbs.
  • Spinocerebellar Ataxia, Autosomal Recessive, with Axonal Neuropathy 2|AOA2|Ataxia with Oculomotor Apraxia Type 2|SCAN2

    an autosomal recessive condition caused by mutation(s) in the setx gene, encoding probable helicase senataxin. it is characterized by juvenile onset progressive cerebellar ataxia, axonal sensorimotor peripheral neuropathy, and increased concentrations of serum alpha-fetoprotein. oculomotor apraxia is common, but is not always present.

Tabular List of Diseases and Injuries

The following annotation back-references are applicable to this diagnosis code. The Tabular List of Diseases and Injuries is a list of ICD-10-CM codes, organized "head to toe" into chapters and sections with coding notes and guidance for inclusions, exclusions, descriptions and more.


Inclusion Terms

Inclusion Terms
These terms are the conditions for which that code is to be used. The terms may be synonyms of the code title, or, in the case of "other specified" codes, the terms are a list of the various conditions assigned to that code. The inclusion terms are not necessarily exhaustive. Additional terms found only in the Alphabetic Index may also be assigned to a code.
  • Charcot-Marie-Tooth disease
  • Déjérine-Sottas disease
  • Hereditary motor and sensory neuropathy, types I-IV
  • Hypertrophic neuropathy of infancy
  • Peroneal muscular atrophy (axonal type) (hypertrophic type)
  • Roussy-Levy syndrome

Index to Diseases and Injuries References

The following annotation back-references for this diagnosis code are found in the injuries and diseases index. The Index to Diseases and Injuries is an alphabetical listing of medical terms, with each term mapped to one or more ICD-10-CM code(s).

Convert G60.0 to ICD-9-CM

  • ICD-9-CM Code: 356.0 - Hered periph neuropathy
    Approximate Flag - The approximate mapping means there is not an exact match between the ICD-10 and ICD-9 codes and the mapped code is not a precise representation of the original code.
  • ICD-9-CM Code: 356.1 - Peroneal muscle atrophy
    Approximate Flag - The approximate mapping means there is not an exact match between the ICD-10 and ICD-9 codes and the mapped code is not a precise representation of the original code.
  • ICD-9-CM Code: 356.2 - Hered sensory neuropathy
    Approximate Flag - The approximate mapping means there is not an exact match between the ICD-10 and ICD-9 codes and the mapped code is not a precise representation of the original code.

Patient Education


Charcot-Marie-Tooth disease

Charcot-Marie-Tooth disease encompasses a group of disorders called hereditary sensory and motor neuropathies that damage the peripheral nerves. Peripheral nerves connect the brain and spinal cord to muscles and to sensory cells that detect sensations such as touch, pain, heat, and sound. Damage to the peripheral nerves that worsens over time can result in alteration or loss of sensation and wasting (atrophy) of muscles in the feet, legs, and hands.

Charcot-Marie-Tooth disease usually becomes apparent in adolescence or early adulthood, but onset may occur anytime from early childhood through late adulthood. Symptoms of Charcot-Marie-Tooth disease vary in severity and age of onset even among members of the same family. Some people never realize they have the disorder because their symptoms are so mild, but most have a moderate amount of physical disability. A small percentage of people experience severe weakness or other problems which, in very rare cases, can be life-threatening. In most affected individuals, however, Charcot-Marie-Tooth disease does not affect life expectancy.

Typically, the earliest symptoms of Charcot-Marie-Tooth disease result from muscle atrophy in the feet. Affected individuals may have foot abnormalities such as high arches (pes cavus), flat feet (pes planus), or curled toes (hammer toes). They often have difficulty flexing the foot or walking on the heel of the foot. These difficulties may cause a higher than normal step (steppage gait) and increase the risk of ankle injuries and tripping. As the disease worsens, muscles in the lower legs usually weaken, but leg and foot problems rarely require the use of a wheelchair.

Affected individuals may also develop weakness in the hands, causing difficulty with daily activities such as writing, fastening buttons, and turning doorknobs. People with Charcot-Marie-Tooth disease typically experience a decreased sensitivity to touch, heat, and cold in the feet and lower legs, but occasionally feel aching or burning sensations. In rare cases, affected individuals have loss of vision or gradual hearing loss that sometimes leads to deafness.

There are several types of Charcot-Marie-Tooth disease, which are differentiated by their effects on nerve cells and patterns of inheritance. Type 1 (CMT1) is characterized by abnormalities in myelin, the fatty substance that covers nerve cells, protecting them and helping to transmit nerve impulses. These abnormalities slow the transmission of nerve impulses and can affect the health of the nerve fiber. Type 2 (CMT2) is characterized by abnormalities in the fiber, or axon, that extends from a nerve cell body to muscles or to sense organs. These abnormalities reduce the strength of the nerve impulse. People with CMT2 may develop amyotrophic lateral sclerosis (ALS), a condition characterized by progressive muscle weakness, a loss of muscle mass, and an inability to control movement. In forms of Charcot-Marie-Tooth disease classified as intermediate type, the nerve impulses are both slowed and reduced in strength, probably due to abnormalities in both myelin and axons. Type 4 (CMT4) is distinguished from the other types by its pattern of inheritance; it can affect either the axons or the myelin. Type X Charcot-Marie-Tooth disease (CMTX) is caused by mutations in genes on the X chromosome, one of the two sex chromosomes. Within the various types of Charcot-Marie-Tooth disease, subtypes (such as CMT1A, CMT1B, CMT2A, CMT4A, and CMTX1) indicate different genetic causes.

Sometimes other, historical names are used to refer to particular forms of  Charcot-Marie-Tooth disease. For example, Roussy-Levy syndrome is a form of CMT11 with the additional feature of rhythmic shaking (tremors).  Dejerine-Sottas syndrome is a term sometimes used to describe a severe, early childhood form of Charcot-Marie-Tooth disease; it is also sometimes called type 3 (CMT3). Depending on the specific gene that is altered, this severe, early-onset form of the disorder may also be classified as CMT1 or CMT4. CMTX5 is also known as Rosenberg-Chutorian syndrome.


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Code History

  • FY 2024 - No Change, effective from 10/1/2023 through 9/30/2024
  • FY 2023 - No Change, effective from 10/1/2022 through 9/30/2023
  • FY 2022 - No Change, effective from 10/1/2021 through 9/30/2022
  • FY 2021 - No Change, effective from 10/1/2020 through 9/30/2021
  • FY 2020 - No Change, effective from 10/1/2019 through 9/30/2020
  • FY 2019 - No Change, effective from 10/1/2018 through 9/30/2019
  • FY 2018 - No Change, effective from 10/1/2017 through 9/30/2018
  • FY 2017 - No Change, effective from 10/1/2016 through 9/30/2017
  • FY 2016 - New Code, effective from 10/1/2015 through 9/30/2016. This was the first year ICD-10-CM was implemented into the HIPAA code set.

Footnotes

[1] Chronic - a chronic condition code indicates a condition lasting 12 months or longer and its effect on the patient based on one or both of the following criteria:

  • The condition results in the need for ongoing intervention with medical products,treatment, services, and special equipment
  • The condition places limitations on self-care, independent living, and social interactions.