2024 ICD-10-CM Diagnosis Code G31.89

Approximate Synonyms

The following clinical terms are approximate synonyms or lay terms that might be used to identify the correct diagnosis code:

• 3-Methylglutaconic aciduria type 4
• 3-methylglutaconic aciduria type IV with sensorineural deafness, encephalopathy and Leigh-like syndrome
• Acute cerebellar syndrome
• Argyrophilic grain disease
• Arteriopathic granular atrophy of cerebral cortex
• Autoimmune cerebellar degeneration
• Autosomal dominant striatal neurodegeneration
• Autosomal recessive cerebral atrophy
• Axonal neuropathy
• Beta-propeller protein-associated neurodegeneration
• Cerebellar ataxia associated with another disorder
• Cerebellar deficiency syndrome
• Cerebral degeneration in childhood
• Childhood-onset motor and cognitive regression syndrome with extrapyramidal movement disorder
• Chorea co-occurrent and due to dentatorubropallidoluysian degeneration
• Chorea co-occurrent and due to Huntington disease-like condition
• Chorea co-occurrent and due to Huntington disease-like condition
• Chorea co-occurrent and due to Huntington disease-like condition
• Chorea due to chronic hepatocerebral degeneration
• Chorea due to hereditary ataxia
• Chorea due to heredodegenerative disorder
• Chorea due to heredodegenerative disorder
• Chorea due to Huntington disease-like 1
• Chorea due to Huntington disease-like 2
• Chorea due to Huntington disease-like 3
• Chronic hepatocerebral degeneration
• Coenzyme A synthase protein associated neurodegeneration
• Congenital cerebellar cortical atrophy
• Congenital microcephaly, severe encephalopathy, progressive cerebral atrophy syndrome
• Corneal cerebellar syndrome
• Corticostriatal-spinal degeneration
• Cystic degeneration of brain
• Dentatorubropallidoluysian degeneration
• Dentatorubropallidoluysian degeneration
• Diffuse cerebral and cerebellar atrophy, intractable seizures, progressive microcephaly syndrome
• Disorder of valine metabolism
• Early-onset progressive diffuse brain atrophy, microcephaly, muscle weakness, optic atrophy syndrome
• Early-onset progressive encephalopathy, hearing loss, pons hypoplasia, brain atrophy syndrome
• Early-onset progressive neurodegeneration, blindness, ataxia, spasticity syndrome
• Fatal post-viral neurodegenerative disorder
• Fatty acid hydroxylase associated neurodegeneration
• Generalized dystonia
• Global developmental delay, visual anomalies, progressive cerebellar atrophy, truncal hypotonia syndrome
• Hereditary acantholytic dermatosis
• Hereditary cerebellar atrophy
• Hereditary cerebellar atrophy
• Hereditary cerebellar atrophy
• Hereditary cerebellar atrophy
• Hereditary cerebellar atrophy
• Hereditary cerebellar atrophy
• Hereditary degenerative disease of central nervous system
• Huntington disease-like 1
• Huntington disease-like 3
• Huntington disease-like syndrome
• Huntington disease-like syndrome
• Huntington disease-like syndrome
• Huntington disease-like syndrome
• Huntington disease-like syndrome due to C9ORF72 expansions
• Hypomyelinating leukodystrophy with atrophy of basal ganglia and cerebellum
• Inborn error of amino acid metabolism
• Infantile cerebral and cerebellar atrophy with postnatal progressive microcephaly
• Infantile neuroaxonal dystrophy
• Infantile spasms, psychomotor retardation, progressive brain atrophy, basal ganglia disease syndrome
• Infantile-onset axonal motor and sensory neuropathy, optic atrophy, neurodegenerative syndrome
• Juvenile cerebellar degeneration AND myoclonus
• Juvenile-onset diabetes mellitus, central and peripheral neurodegeneration syndrome
• Keratosis follicularis, dwarfism, cerebral atrophy syndrome
• Kufor Rakeb syndrome
• Late cortical cerebellar atrophy
• Late infantile and juvenile neuroaxonal dystrophy
• MEPAN syndrome
• Mitochondrial membrane protein associated neurodegeneration
• NADHX dehydratase deficiency
• NADHX epimerase deficiency
• Neuroaxonal dystrophy
• Neurodegeneration due to 3-hydroxyisobutyryl coenzyme A hydrolase deficiency
• Neurodevelopmental delay, seizures, ophthalmic anomalies, osteopenia, cerebellar atrophy syndrome
• Olivopontocerebellar atrophy and deafness
• Olivopontocerebellar degeneration
• PCNA-related progressive neurodegenerative photosensitivity syndrome
• Pineal degeneration
• PRKAR1B-related neurodegenerative dementia with intermediate filaments
• Progressive cerebello-cerebral atrophy
• Progressive encephalopathy with edema, hypsarrhythmia, and optic atrophy-like syndrome
• Progressive neuronal degeneration of childhood
• Progressive neuronal degeneration without liver cirrhosis
• Second cranial nerve finding
• Severe neurodegenerative syndrome with lipodystrophy
• Sporadic cerebellar degeneration
• Synucleinopathy
• TUBB4A-related leukodystrophy
• USP18 deficiency
• X-linked neurodegenerative syndrome Bertini type
• X-linked neurodegenerative syndrome Hamel type

Clinical Information

• Infantile Neuroaxonal Dystrophy

  a rare autosomal recessive neurodegenerative disorder caused by mutations in the pla2g6 gene. it is characterized by the development of swellings called spehroids along the axons of the central nervous system. signs and symptoms appear early in life and include movement difficulties, muscle hypotonia and spasticity, and dementia.

• Acute Motor and Sensory Axonal Neuropathy|Acute Motor And Sensory Axonal Neuropathy|Acute Motor-Sensory Axonal Neuropathy|Acute Motor-Sensory Axonal Neuropathy

  a subtype of guillain-barre syndrome that targets sensory motor axons, and is characterized by acute onset of quadriparesis, distal sensory loss, areflexia, and respiratory insufficiency.

• Acute Motor Axonal Neuropathy|AMAN

  a subtype of guillain-barre syndrome that targets motor axons, and is characterized by symmetric limb weakness, diffuse areflexia, facial and oropharyngeal muscle weakness, and respiratory insufficiency.

• Axonal Neuropathy

  any nerve disorder affecting the axon of a nerve.

• GAN wt Allele|GAN1|Giant Axonal Neuropathy (Gigaxonin) Gene|Gigaxonin wt Allele|KLHL16

  human gan wild-type allele is located in the vicinity of 16q24.1 and is approximately 65 kb in length. this allele, which encodes gigaxonin protein, is involved in both ubiquitination and neurofilament structure. mutation of the gene is associated with giant axonal neuropathy.

• Giant Axonal Neuropathy

  a rare inherited disorder affecting the neurofilaments. it is caused by mutations in the gan gene. it is characterized by the presence of abnormally large nerve cell axons. signs and symptoms include difficulty walking, sensory disturbances, lack of motor coordination and abnormal reflexes in the limbs.

• Spinocerebellar Ataxia, Autosomal Recessive, with Axonal Neuropathy 2|AOA2|Ataxia with Oculomotor Apraxia Type 2|SCAN2

  an autosomal recessive condition caused by mutation(s) in the setx gene, encoding probable helicase senataxin. it is characterized by juvenile onset progressive cerebellar ataxia, axonal sensorimotor peripheral neuropathy, and increased concentrations of serum alpha-fetoprotein. oculomotor apraxia is common, but is not always present.

Convert G31.89 to ICD-9-CM

• ICD-9-CM Code: 331.89 - Cereb degeneration NEC
  Approximate Flag - The approximate mapping means there is not an exact match between the ICD-10 and ICD-9 codes and the mapped code is not a precise representation of the original code.

Code History

• FY 2024 - No Change, effective from 10/1/2023 through 9/30/2024
• FY 2023 - No Change, effective from 10/1/2022 through 9/30/2023
• FY 2022 - No Change, effective from 10/1/2021 through 9/30/2022
• FY 2021 - No Change, effective from 10/1/2020 through 9/30/2021
• FY 2020 - No Change, effective from 10/1/2019 through 9/30/2020
• FY 2019 - No Change, effective from 10/1/2018 through 9/30/2019
• FY 2018 - No Change, effective from 10/1/2017 through 9/30/2018
• FY 2017 - No Change, effective from 10/1/2016 through 9/30/2017
• FY 2016 - New Code, effective from 10/1/2015 through 9/30/2016. This was the first year ICD-10-CM was implemented into the HIPAA code set.