2024 ICD-10-CM Diagnosis Code E71.318
Other disorders of fatty-acid oxidation
- ICD-10-CM Code:
- E71.318
- ICD-10 Code for:
- Other disorders of fatty-acid oxidation
- Is Billable?
- Yes - Valid for Submission
- Chronic Condition Indicator: [1]
- Chronic
- Code Navigator:
E71.318 is a billable diagnosis code used to specify a medical diagnosis of other disorders of fatty-acid oxidation. The code is valid during the current fiscal year for the submission of HIPAA-covered transactions from October 01, 2023 through September 30, 2024.
Approximate Synonyms
The following clinical terms are approximate synonyms or lay terms that might be used to identify the correct diagnosis code:
- 3-Ketoacyl-CoA triolase deficiency
- Acyl-CoA dehydrogenase 9 deficiency
- Carnitine palmitoyltransferase deficiency
- Carnitine palmitoyltransferase deficiency
- Carnitine palmitoyltransferase II deficiency
- Carnitine palmitoyltransferase II deficiency
- Combined deficiency of long chain 3-hydroxyacyl-CoA dehydrogenase and enoyl-CoA hydratase
- Combined long chain hydroxyacyl-CoA dehydrogenase deficiency
- Deficiency of 2-methylbutyryl-CoA dehydrogenase
- Deficiency of 3-hydroxyacyl-CoA dehydrogenase
- Deficiency of acetyl-CoA acyltransferase
- Deficiency of enoyl-CoA hydratase
- Fatty acid oxidation defect
- Isolated long chain hydroxyacyl-CoA dehydrogenase deficiency
- Mitochondrial trifunctional protein deficiency
- Neonatal form of carnitine palmitoyltransferase II deficiency
- Severe infantile form of carnitine palmitoyltransferase II deficiency
- Succinyl-CoA acetoacetate transferase deficiency
Clinical Classification
Clinical Category is Other specified and unspecified nutritional and metabolic disorders
- CCSR Category Code: END016
- Inpatient Default CCSR: Y - Yes, default inpatient assignment for principal diagnosis or first-listed diagnosis.
- Outpatient Default CCSR: Y - Yes, default outpatient assignment for principal diagnosis or first-listed diagnosis.
Clinical Information
Mitochondrial Trifunctional Protein Deficiency
a rare, autosomal recessive inherited disorder caused by mutations in the hadha and hadhb genes. it is characterized by the deficiency of an enzyme involved in the fatty acid oxidation process. signs and symptoms may appear early or later in life and may be triggered by periods of fasting or illnesses. they include feeding difficulties, lethargy, hypoglycemia, hypotonia, liver abnormalities, heart abnormalities, peripheral neuropathy, coma, and sudden death.
Index to Diseases and Injuries References
The following annotation back-references for this diagnosis code are found in the injuries and diseases index. The Index to Diseases and Injuries is an alphabetical listing of medical terms, with each term mapped to one or more ICD-10-CM code(s).
- - Disorder (of) - See Also: Disease;
- - fatty acid
- - oxidation
- - specified deficiency NEC - E71.318
- - oxidation
- - fatty acid
Convert E71.318 to ICD-9-CM
- ICD-9-CM Code: 277.85 - Disorders acid oxidation
Approximate Flag - The approximate mapping means there is not an exact match between the ICD-10 and ICD-9 codes and the mapped code is not a precise representation of the original code.
Patient Education
Lipid Metabolism Disorders
Metabolism is the process your body uses to make energy from the food you eat. Food is made up of proteins, carbohydrates, and fats. Chemicals in your digestive system (enzymes) break the food parts down into sugars and acids, your body's fuel. Your body can use this fuel right away, or it can store the energy in your body tissues. If you have a metabolic disorder, something goes wrong with this process.
Lipid metabolism disorders, such as Gaucher disease and Tay-Sachs disease, involve lipids. Lipids are fats or fat-like substances. They include oils, fatty acids, waxes, and cholesterol. If you have one of these disorders, you may not have enough enzymes to break down lipids. Or the enzymes may not work properly and your body can't convert the fats into energy. They cause a harmful amount of lipids to build up in your body. Over time, that can damage your cells and tissues, especially in the brain, peripheral nervous system, liver, spleen, and bone marrow. Many of these disorders can be very serious, or sometimes even fatal.
These disorders are inherited. Newborn babies get screened for some of them, using blood tests. If there is a family history of one of these disorders, parents can get genetic testing to see whether they carry the gene. Other genetic tests can tell whether the fetus has the disorder or carries the gene for the disorder.
Enzyme replacement therapies can help with a few of these disorders. For others, there is no treatment. Medicines, blood transfusions, and other procedures may help with complications.
[Learn More in MedlinePlus]
Code History
- FY 2024 - No Change, effective from 10/1/2023 through 9/30/2024
- FY 2023 - No Change, effective from 10/1/2022 through 9/30/2023
- FY 2022 - No Change, effective from 10/1/2021 through 9/30/2022
- FY 2021 - No Change, effective from 10/1/2020 through 9/30/2021
- FY 2020 - No Change, effective from 10/1/2019 through 9/30/2020
- FY 2019 - No Change, effective from 10/1/2018 through 9/30/2019
- FY 2018 - No Change, effective from 10/1/2017 through 9/30/2018
- FY 2017 - No Change, effective from 10/1/2016 through 9/30/2017
- FY 2016 - New Code, effective from 10/1/2015 through 9/30/2016. This was the first year ICD-10-CM was implemented into the HIPAA code set.
Footnotes
[1] Chronic - a chronic condition code indicates a condition lasting 12 months or longer and its effect on the patient based on one or both of the following criteria:
- The condition results in the need for ongoing intervention with medical products,treatment, services, and special equipment
- The condition places limitations on self-care, independent living, and social interactions.