Term Title | ICD-CM-10 Codes | Term Notes |
Pseudohermaphroditism » 5-alpha-reductase Deficiency | E29.1 | |
Jaundice Yellow » absence or Deficiency of enzyme system for bilirubin conjugation (congenital) | P59.8 | |
Disorder Of » acid phosphatase Deficiency | E83.39 | |
Syndrome » acquired | | See: Human, immunoDeficiency virus (HIV) disease; |
Syndrome » acquired immunoDeficiency | | See: Human, immunoDeficiency virus (HIV) disease; |
Immunodeficiency » adenosine-deaminase Deficiency | D81.30 | See Also: Deficiency, adenosine deaminase; |
Short Shortening Shortness » aggrecan Deficiency | E34.328 | |
Anemia Essential General Hemoglobin Deficiency Infantile Primary Profound » amino-acid-Deficiency | D53.0 | |
Amylopectinosis (brancher enzyme Deficiency) | E74.03 | |
Anemia (essential) (general) (hemoglobin Deficiency) (infantile) (primary) (profound) | D64.9 | |
Aneurin Deficiency | E51.9 | |
Syndrome » antibody Deficiency | D80.9 | |
Defect Defective » antibody immunoDeficiency | D80.9 | |
Hypercoagulable State » antithrombin (III) Deficiency | D68.59 | |
Avitaminosis (multiple) | E56.9 | See Also: Deficiency, vitamin; |
Anemia Essential General Hemoglobin Deficiency Infantile Primary Profound » B12 Deficiency (dietary) pernicious | D51.0 | |
Mucopolysaccharidosis » beta-gluduronidase Deficiency | E76.29 | |
Calciferol (vitamin D) Deficiency | E55.9 | |
Sequelae Of » calcium Deficiency | E64.8 | |
Calorie Deficiency or malnutrition | E46 | See Also: Malnutrition; |
Muscle Muscular » carnitine (palmityltransferase) Deficiency | E71.314 | |
CDKL5 (Cyclin-Dependent Kinase-Like 5 Deficiency Disorder) | G40.42 | |
Chromatopsia | | See: Deficiency, color vision; |
Deficiency Deficient » clotting (blood) | D68.9 | See Also: Deficiency, coagulation factor; |
Deficiency Deficient » clotting factor NEC | D68.2 | See Also: Deficiency, factor; |
Deficiency Deficient » clotting factor NEC (hereditary) | D68.2 | See Also: Deficiency, factor; |
Defect Defective » coagulation (factor) | D68.9 | See Also: Deficiency, factor; |
Disease Diseased » coagulation factor Deficiency (congenital) | | See: Defect, coagulation; |
Blindness Acquired Congenital Both Eyes » color | | See: Deficiency, color vision; |
Color blindness | | See: Deficiency, color vision; |
Anemia Essential General Hemoglobin Deficiency Infantile Primary Profound » combined B12 and folate Deficiency | D53.1 | |
Syndrome » combined immunity Deficiency | D81.9 | |
Hypothyroidism Acquired » congenital | | See: Syndrome, iodine- Deficiency, congenital; |
Deficiency Deficient » congenital syndrome | | See: Syndrome, iodine-Deficiency, congenital; |
Syndrome » congenital, associated with enzyme Deficiency | E25.0 | |
Disorder Of » Cyclin-Dependent Kinase-Like 5 Deficiency (CDKL5) | G40.42 | |
Cystathionine synthase Deficiency | E72.11 | |
Defect Defective » decreased platelet adhesion and selective Deficiency of high-molecular-weight multimers | D68.020 | See Also: Disease, von Willebrand; |
Acid » Deficiency | | |
Anemia Essential General Hemoglobin Deficiency Infantile Primary Profound » Deficiency | | |
Mental » Deficiency | | See: Disability, intellectual; |
Anemia Essential General Hemoglobin Deficiency Infantile Primary Profound » Deficiency | D53.9 | |
Inappropriate » Deficiency | E23.2 | |
Polyglandular » Deficiency | E31.0 | |
Disorder Of » Deficiency (familial) | E78.6 | |
Polyneuropathy Peripheral » Deficiency (of) | | |
Protein » Deficiency NEC | | See: Malnutrition; |
Deficiency, deficient | | |
Zinc » Deficiency, dietary | E60 | |
Deficit | | See Also: Deficiency; |
Dextrinosis, limit (debrancher enzyme Deficiency) | E74.03 | |
Disease Diseased » diaphorase Deficiency | D74.0 | |
Dichromat, dichromatopsia (congenital) | | See: Deficiency, color vision; |
Inadequate Inadequacy » diet (causing nutritional Deficiency) | E63.9 | |
Stomatitis Denture Ulcerative » dietary Deficiency | E53.0 | |
Anemia Essential General Hemoglobin Deficiency Infantile Primary Profound » dietary vitamin B12 Deficiency | D51.3 | |
DIRA (Deficiency of interleukin 1 receptor antagonist) | M04.8 | |
DPD (dihydropyrimidine dehydrogenase Deficiency) | E88.89 | |
Immunodeficiency » due to adenosine deaminase Deficiency | D81.31 | |
Gastritis Simple » due to diet Deficiency | E63.9 | |
Neuropathy Neuropathic » due to dietary Deficiency | D51.3 | |
Polyneuropathy Peripheral » due to dietary Deficiency | D51.3 | |
Stomatitis Denture Ulcerative » due to dietary or vitamin Deficiency | E53.0 | |
Anemia Essential General Hemoglobin Deficiency Infantile Primary Profound » due to dietary vitamin B12 Deficiency | D51.3 | |
Degeneration Degenerative » due to dietary vitamin B12 Deficiency | D51.3 | |
Anemia Essential General Hemoglobin Deficiency Infantile Primary Profound » due to enzyme Deficiency specified type NEC | D55.8 | |
Dementia Degenerative Primary Old Age Persisting Unspecified Severity Without Behavioral Disturbance Psychotic Disturbance Mood Disturbance And Anxiety » due to iodine Deficiency | E01.8 | See Also: Dementia, in, diseases specified elsewhere; |
Goiter Plunging Substernal » due to iodine-Deficiency | E01.1 | |
Goiter Plunging Substernal » endemic (iodine-Deficiency) | E01.2 | |
Anemia Essential General Hemoglobin Deficiency Infantile Primary Profound » enzyme-Deficiency, drug-induced | D59.2 | |
Ergosterol Deficiency (vitamin D) | E55.9 | |
Anemia Essential General Hemoglobin Deficiency Infantile Primary Profound » erythrocytic glutathione Deficiency | D55.1 | |
Deficiency Deficient » factor | | See Also: Deficiency, coagulation; |
Disorder Of » familial lecithin cholesterol acyltransferase Deficiency | E78.6 | |
Anemia Essential General Hemoglobin Deficiency Infantile Primary Profound » folate (folic acid) Deficiency | D52.9 | |
Disorder Of » fructokinase Deficiency | E74.11 | |
Fructokinase Deficiency | E74.11 | |
Fructose 1,6 diphosphatase Deficiency | E74.19 | |
Disorder Of » fructose-1, 6-diphosphatase Deficiency | E74.19 | |
Galactokinase Deficiency | E74.29 | |
Disease Diseased » glucose-6-phosphatase Deficiency | E74.01 | |
Anemia Essential General Hemoglobin Deficiency Infantile Primary Profound » glucose-6-phosphate dehydrogenase Deficiency | D55.0 | |
Anemia Essential General Hemoglobin Deficiency Infantile Primary Profound » glucose-6-phosphate dehydrogenase (G6PD) Deficiency | D55.0 | |
GLUT1 Deficiency syndrome 1, infantile onset | E74.810 | |
GLUT1 Deficiency syndrome 2, childhood onset | E74.810 | |
Anemia Essential General Hemoglobin Deficiency Infantile Primary Profound » glutathione-reductase Deficiency | D55.1 | |
Disease Diseased » Hageman (congenital factor XII Deficiency) | D68.2 | |
Hageman's factor defect, Deficiency or disease | D68.2 | |
Anemia Essential General Hemoglobin Deficiency Infantile Primary Profound » hexokinase Deficiency | D55.29 | |
HIV | B20 | See Also: Human, immunoDeficiency virus; |
Test Tests Testing For » HIV (human immunoDeficiency virus) | | |
Homogentisate 1,2-dioxygenase Deficiency | E70.29 | |
Virus Viral » human immunoDeficiency (HIV) | | See: Human, immunoDeficiency virus (HIV) disease; |
Disease Diseased » human immunoDeficiency (HIV) | B20 | |
Admission For » human immunoDeficiency virus | Z71.7 | |
Disease Diseased » human immunoDeficiency virus (HIV) | B20 | |
Pregnancy Single Uterine » human immunoDeficiency virus (HIV) | O98.71 | |
Delivery Childbirth Labor » human immunoDeficiency virus (HIV) | O98.72 | |
Puerperal Puerperium Complicated By Complications » human immunoDeficiency virus (HIV) | O98.73 | |
Screening For » human immunoDeficiency virus (HIV) | Z11.4 | |
Screening For » human immunoDeficiency virus (HIV) | Z11.4 | |
Screening For » human immunoDeficiency virus (HIV) | Z11.4 | |
Screening For » human immunoDeficiency virus (HIV) | Z11.4 | |
Contact With » human immunoDeficiency virus (HIV) | Z20.6 | |
Exposure To » human immunoDeficiency virus (HIV) | Z20.6 | |
Counseling For » human immunoDeficiency virus (HIV) | Z71.7 | |
Counseling For » human immunoDeficiency virus (HIV) | Z71.7 | |
Dementia Degenerative Primary Old Age Persisting Unspecified Severity Without Behavioral Disturbance Psychotic Disturbance Mood Disturbance And Anxiety » human immunoDeficiency virus (HIV) disease | B20 | See Also: Dementia, in, diseases specified elsewhere; |
Encephalitis Chronic Hemorrhagic Idiopathic Nonepidemic Spurious Subacute » human immunoDeficiency virus (HIV) disease | B20 | |
Pregnancy Single Uterine » human immunoDeficiency virus (HIV) disease | O98.71 | |
Screening For » human immunoDeficiency virus (HIV) infection | Z11.4 | |
History » human immunoDeficiency virus (HIV) infection | Z83.0 | |
Status Post » human immunoDeficiency virus (HIV) infection, asymptomatic | Z21 | |
Hyperprothrombinemia, causing coagulation factor Deficiency | D68.4 | |
Hypovitaminosis | | See: Deficiency, vitamin; |
Syndrome » immunity Deficiency, combined | D81.9 | |
Deficiency Deficient » immuno | | See: ImmunoDeficiency; |
Syndrome » immunoDeficiency | | |
ImmunoDeficiency | D84.9 | |
Acquired » immunoDeficiency syndrome (AIDS) | B20 | |
Human » immunoDeficiency virus (HIV) disease (infection) | B20 | |
Infection Infected Infective Opportunistic » immunoDeficiency, type 2 (HIV 2) | B97.35 | |
Infection Infected Infective Opportunistic » immunoDeficiency, type 2 (HIV 2) | B97.35 | |
Infection Infected Infective Opportunistic » immunoDeficiency, type 2 (HIV 2) | B97.35 | |
Retrovirus As Cause Of Disease Classified Elsewhere » immunoDeficiency, type 2 (HIV 2) | B97.35 | |
Dietary » inadequacy or Deficiency | E63.9 | |
Anemia Essential General Hemoglobin Deficiency Infantile Primary Profound » intrinsic factor Deficiency | D51.0 | |
Congenital » intrinsic factor Deficiency | D51.0 | |
Goiter Plunging Substernal » iodine-Deficiency | E01.1 | |
Hypothyroidism Acquired » iodine-Deficiency (acquired) | E01.8 | |
Goiter Plunging Substernal » iodine-Deficiency (endemic) | E01.2 | |
Goiter Plunging Substernal » iodine-Deficiency (endemic) | E01.2 | |
Struma » iodine-Deficiency related | E01.1 | |
Disorder Of » iodine-Deficiency related | E01.8 | |
Hypothyroidism Acquired » iodine-Deficiency, acquired | E01.8 | |
Syndrome » iodine-Deficiency, congenital | E00.9 | |
Anemia Essential General Hemoglobin Deficiency Infantile Primary Profound » iron Deficiency | D50.9 | |
Klippel-Feil Deficiency, disease, or syndrome (brevicollis) | Q76.1 | |
Encephalopathy Acute » lack of vitamin | E56.9 | See Also: Deficiency, vitamin; |
Laki-Lorand factor Deficiency | | See: Defect, coagulation, specified type NEC; |
Deficiency Deficient » LCAD (long chain acyl CoA dehydrogenase Deficiency) | E71.310 | |
Glomerulonephritis » lecithin cholesterol acyltransferase Deficiency | E78.6 | |
Short Shortening Shortness » limbed stature, with immunoDeficiency | D82.2 | |
Syndrome » magnesium-Deficiency | R29.0 | |
Deficiency Deficient » MCAD (medium chain acyl CoA dehydrogenase Deficiency) | E71.311 | |
Menadione Deficiency | E56.1 | |
Disorder Of » methylenetetrahydrofolate reductase Deficiency | E72.12 | |
Disorder Of » moral Deficiency | F60.2 | |
MSD (multiple sulfatase Deficiency) | E75.26 | |
Syndrome » muscle Deficiency | Q79.4 | |
Abdomen Abdominal » muscle Deficiency syndrome | Q79.4 | |
Tetany Due To » neonatal (without calcium or magnesium Deficiency) | P71.3 | |
Niacin (amide) Deficiency | E52 | |
Dementia Degenerative Primary Old Age Persisting Unspecified Severity Without Behavioral Disturbance Psychotic Disturbance Mood Disturbance And Anxiety » niacin Deficiency | E52 | See Also: Dementia, in, diseases specified elsewhere; |
Sequelae Of » niacin Deficiency | E64.8 | |
Nicotinic acid Deficiency | E52 | |
Nutrient element Deficiency | E61.9 | |
Anemia Essential General Hemoglobin Deficiency Infantile Primary Profound » nutritional (Deficiency) | D53.9 | |
Arthropathy » nutritional Deficiency | E63.9 | See Also: subcategory M14.8-; |
Sequelae Of » nutritional Deficiency | E64.9 | |
History » nutritional Deficiency | Z86.39 | |
Polyneuropathy Peripheral » nutritional Deficiency NEC | E63.9 | |
Disorder Of » ornithine transcarbamylase Deficiency | E72.4 | |
Orotaciduria, oroticaciduria (congenital) (hereditary) (pyrimidine Deficiency) | E79.89 | |
Aciduria » orotic (congenital) (hereditary) (pyrimidine Deficiency) | E79.89 | |
Disease Diseased » p110d-activating mutation causing senescent T cells, lymphadenopathy, and immunoDeficiency [PASLI] | D81.82 | |
Acid » phosphatase Deficiency | E83.39 | |
Phrynoderma (vitamin A Deficiency) | E50.8 | |
Syndrome » pluriDeficiency | E40 | |
Findings Abnormal Inconclusive Without Diagnosis » potassium (Deficiency) | E87.6 | |
Short Shortening Shortness » primary insulin-like growth factor-1 (IGF-1) Deficiency | E34.321 | |
Hypercoagulable State » protein C Deficiency | D68.59 | |
Hypercoagulable State » protein S Deficiency | D68.59 | |
Anemia Essential General Hemoglobin Deficiency Infantile Primary Profound » protein-Deficiency | D53.0 | |
Disorder Of » pseudovitamin D Deficiency | E83.32 | |
Anemia Essential General Hemoglobin Deficiency Infantile Primary Profound » pyruvate kinase Deficiency | D55.21 | |
Anemia Essential General Hemoglobin Deficiency Infantile Primary Profound » pyruvate kinase Deficiency | D55.21 | |
Perlèche Nec » riboflavin Deficiency | E53.0 | |
Riboflavin Deficiency | E53.0 | |
Disease Diseased » Rosenthal's (factor XI Deficiency) | D68.1 | |
Deficiency Deficient » SCAD (short chain acyl CoA dehydrogenase Deficiency) | E71.312 | |
Sequelae Of » selenium Deficiency | E64.8 | |
Selenium Deficiency, dietary | E59 | |
Deficiency Deficient » sequelae | | See: Sequelae, nutritional Deficiency; |
Nutrition Deficient Or Insufficient » sequelae | | See: Sequelae, nutritional Deficiency; |
Short Shortening Shortness » severe primary insulin-like growth factor-1 Deficiency (SPIGFD) | E34.321 | |
Sideropenia | | See: Anemia, iron Deficiency; |
Findings Abnormal Inconclusive Without Diagnosis » sodium (Deficiency) | E87.1 | |
Nutrition Deficient Or Insufficient » specific element Deficiency | | See: Nutrient element Deficiency, or by element; |
Anemia Essential General Hemoglobin Deficiency Infantile Primary Profound » specified Deficiency NEC | D53.8 | |
Anemia Essential General Hemoglobin Deficiency Infantile Primary Profound » specified Deficiency NEC | D53.8 | |
Disorder Of » specified Deficiency NEC | E71.318 | |
SSADHD (succinic semialdehyde dehydrogenase Deficiency) | E72.81 | |
Stuart Deficiency disease (factor X) | D68.2 | |
Disease Diseased » Stuart-Prower (congenital factor X Deficiency) | D68.2 | |
Stuart-Prower factor Deficiency (factor X) | D68.2 | |
Disease Diseased » Stuart's (congenital factor X Deficiency) | D68.2 | |
Hypothyroidism Acquired » subclinical, iodine-Deficiency related | E02 | |
Positive » test, human immunoDeficiency virus (HIV) | R75 | |
Thiamin Deficiency | E51.9 | |
Sequelae Of » thiamine Deficiency | E64.8 | |
Thiaminic Deficiency with beriberi | E51.11 | |
Alymphocytosis » thymic (with immunoDeficiency) | D82.1 | |
Aplasia » thymic, with immunoDeficiency | D82.1 | |
Dysplasia » thymic, with immunoDeficiency | D82.1 | |
Hypoplasia Hypoplastic » thymic, with immunoDeficiency | D82.1 | |
Tocopherol Deficiency | E56.0 | |
Anemia Essential General Hemoglobin Deficiency Infantile Primary Profound » transcobalamin II Deficiency | D51.2 | |
Deficiency Deficient » type 1 (without SCID) (without severe combined immunoDeficiency) | D81.39 | |
Xerophthalmia Vitamin A Deficiency » unrelated to vitamin A Deficiency | | See: Keratoconjunctivitis; |
Common » variable immunoDeficiency | | See: ImmunoDeficiency, common variable; |
Deficiency Deficient » viosterol | | See: Deficiency, calciferol; |
Viosterol Deficiency | | See: Deficiency, calciferol; |
Disturbance S » vitamin | | See: Deficiency, vitamin; |
Xerosis » vitamin A Deficiency | E50.0 | |
Spots Spotting In Of » vitamin A Deficiency | E50.1 | |
Xerosis » vitamin A Deficiency | E50.1 | |
Xerosis » vitamin A Deficiency | E50.2 | |
Xerosis » vitamin A Deficiency | E50.3 | |
Keratitis Nodular Nonulcerative Simple Zonular » vitamin A Deficiency | E50.4 | |
Keratomalacia » vitamin A Deficiency | E50.4 | |
Amblyopia Congenital Ex Anopsia Partial Suppression » vitamin A Deficiency | E50.5 | |
Blindness Acquired Congenital Both Eyes » vitamin A Deficiency | E50.5 | |
Hemeralopia Day Blindness » vitamin A Deficiency | E50.5 | |
Scar Scarring » vitamin A Deficiency | E50.6 | |
Keratosis » vitamin A Deficiency | E50.8 | |
Keratosis » vitamin A Deficiency | E50.8 | |
Xeroderma » vitamin A Deficiency | E50.8 | |
Encephalopathy Acute » vitamin B Deficiency NEC | E53.9 | |
Degeneration Degenerative » vitamin B12 Deficiency | E53.8 | |
Degeneration Degenerative » vitamin B12 Deficiency | E53.8 | |
Dementia Degenerative Primary Old Age Persisting Unspecified Severity Without Behavioral Disturbance Psychotic Disturbance Mood Disturbance And Anxiety » vitamin B12 Deficiency | E53.8 | See Also: Dementia, in, diseases specified elsewhere; |
Polyneuropathy Peripheral » vitamin B12 Deficiency | E53.8 | |
Cheilosis Angular » vitamin B2 (riboflavin) Deficiency | E53.0 | |
Perlèche Nec » vitamin B2 (riboflavin) Deficiency | E53.0 | |
Syndrome » vitamin B6 Deficiency | E53.1 | |
Stomatitis Denture Ulcerative » vitamin Deficiency | | |
Vitamin Deficiency | | See: Deficiency, vitamin; |
Sequelae Of » vitamin Deficiency NEC | E64.8 | |
Defect Defective » vitamin K Deficiency | D68.4 | |
Deficiency Deficient » vitamin K Deficiency | D68.4 | |
Deprivation » vitamins | | See: Deficiency, vitamin; |
Deficiency Deficient » VLCAD (very long chain acyl CoA dehydrogenase Deficiency) | E71.310 | |
Disease Diseased » with acid maltase Deficiency | E74.02 | |
Hypoplasia Hypoplastic » with immunoDeficiency | D82.1 | |
Hypermobility Hypermotility » with intrinsic sphincter Deficiency | N36.43 | |
Deficiency Deficient » with severe combined immunoDeficiency (SCID) | D81.31 | |
Disease Diseased » without acid maltase Deficiency | E74.05 | |
Xerophthalmia (vitamin A Deficiency) | E50.7 | |
Agammaglobulinemia Acquired Secondary Nonfamilial » X-linked (with growth hormone Deficiency) (Bruton) | D80.0 | |