ICD-10 Diagnosis Code D76.3

Other histiocytosis syndromes

Diagnosis Code D76.3

ICD-10: D76.3
Short Description: Other histiocytosis syndromes
Long Description: Other histiocytosis syndromes
This is the 2018 version of the ICD-10-CM diagnosis code D76.3

Valid for Submission
The code D76.3 is valid for submission for HIPAA-covered transactions.

Code Classification
  • Diseases of the blood and blood-forming organs and certain disorders involving the immune mechanism (D50–D89)
    • Other disorders of blood and blood-forming organs (D70-D77)
      • Oth dis with lymphoreticular and reticulohistiocytic tissue (D76)

Information for Medical Professionals

Diagnostic Related Groups
The diagnosis code D76.3 is grouped in the following Diagnostic Related Group(s) (MS-DRG V35.0)


Convert to ICD-9 Additional informationCallout TooltipGeneral Equivalence Map
The ICD-10 and ICD-9 GEMs are used to facilitate linking between the diagnosis codes in ICD-9-CM and the new ICD-10-CM code set. The GEMs are the raw material from which providers, health information vendors and payers can derive specific applied mappings to meet their needs.

  • Benign cephalic histiocytosis
  • Benign neoplasm of fibrous tissue of skin
  • Benign tumor of dermis
  • Benign tumor of iris
  • Chronic histiocytosis
  • Combined phagocytic defect
  • Cutaneous reticulohistiocytosis
  • Diffuse normolipemic plane xanthomatosis
  • Familial sea-blue histiocytosis
  • Fibrous tissue neoplasm of skin
  • Genetic disorder of lipid storage
  • Hemolytic erythrophagocytic syndrome
  • Hemophagocytic syndrome
  • Histiocytic syndrome
  • Histiocytosis-lymphadenopathy plus syndrome
  • Iris nodule
  • Juvenile xanthogranuloma
  • Juvenile xanthogranuloma of iris
  • Juvenile xanthogranuloma of skin
  • Malakoplakia
  • Mucinous histiocytosis of the colon
  • Multiple eruptive juvenile xanthogranuloma
  • Necrobiotic xanthogranuloma
  • Necrobiotic xanthogranuloma with paraproteinemia
  • Non-Langerhans cell histiocytic dermatosis
  • Panniculitis secondary to histiocytic disorder
  • Periodontitis co-occurrent and due to histiocytosis syndrome
  • Polyostotic sclerosing histiocytosis
  • Retroperitoneal xanthogranuloma
  • Sea-blue histiocyte syndrome
  • Sinus histiocytosis with massive lymphadenopathy
  • Solitary eruptive xanthogranuloma
  • Solitary reticulohistiocytoma
  • Subcutaneous xanthogranulomatosis
  • Tumor of iris
  • Undetermined cell histiocytosis
  • Xanthogranuloma
  • Xanthogranuloma of choroid plexus

Index of Diseases and Injuries
References found for the code D76.3 in the Index of Diseases and Injuries:

Information for Patients

Lymphatic Diseases

The lymphatic system is a network of tissues and organs. It is made up of

  • Lymph - a fluid that contains white blood cells that defend against germs
  • Lymph vessels - vessels that carry lymph throughout your body. They are different from blood vessels.
  • Lymph nodes - glands found throughout the lymph vessels. Along with your spleen, these nodes are where white blood cells fight infection.

Your bone marrow and thymus produce the cells in lymph. They are part of the system, too.

The lymphatic system clears away infection and keeps your body fluids in balance. If it's not working properly, fluid builds in your tissues and causes swelling, called lymphedema. Other lymphatic system problems can include infections, blockage, and cancer.

  • Cancer and lymph nodes (Medical Encyclopedia)
  • Cystic hygroma (Medical Encyclopedia)
  • Groin lump (Medical Encyclopedia)
  • Lymph node biopsy (Medical Encyclopedia)
  • Lymph system (Medical Encyclopedia)
  • Lymphadenitis (Medical Encyclopedia)
  • Lymphangitis (Medical Encyclopedia)
  • Lymphofollicular hyperplasia (Medical Encyclopedia)
  • Neck lump (Medical Encyclopedia)
  • Swollen lymph nodes (Medical Encyclopedia)

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