ICD-10 Diagnosis Code D56.4

Hereditary persistence of fetal hemoglobin [HPFH]

Diagnosis Code D56.4

ICD-10: D56.4
Short Description: Hereditary persistence of fetal hemoglobin [HPFH]
Long Description: Hereditary persistence of fetal hemoglobin [HPFH]
This is the 2018 version of the ICD-10-CM diagnosis code D56.4

Valid for Submission
The code D56.4 is valid for submission for HIPAA-covered transactions.

Code Classification
  • Diseases of the blood and blood-forming organs and certain disorders involving the immune mechanism (D50–D89)
    • Hemolytic anemias (D55-D59)
      • Thalassemia (D56)

Information for Medical Professionals

Diagnostic Related Groups
The diagnosis code D56.4 is grouped in the following Diagnostic Related Group(s) (MS-DRG V34.0)

  • 811 - RED BLOOD CELL DISORDERS WITH MCC
  • 812 - RED BLOOD CELL DISORDERS WITHOUT MCC

Convert to ICD-9 Additional informationCallout TooltipGeneral Equivalence Map
The ICD-10 and ICD-9 GEMs are used to facilitate linking between the diagnosis codes in ICD-9-CM and the new ICD-10-CM code set. The GEMs are the raw material from which providers, health information vendors and payers can derive specific applied mappings to meet their needs.

Synonyms
  • A gamma beta^+^ hereditary persistence of fetal hemoglobin AND beta^0^ thalassemia in cis
  • beta^+^ Thalassemia
  • beta^+^ Thalassemia
  • beta^0^ Thalassemia
  • delta beta Thalassemia
  • delta beta^0^ Thalassemia
  • Hereditary persistence of fetal hemoglobin
  • Hereditary persistence of fetal hemoglobin A gamma beta^+^ thalassemia
  • Hereditary persistence of fetal hemoglobin deletion type
  • Hereditary persistence of fetal hemoglobin delta beta^0^ thalassemia
  • Hereditary persistence of fetal hemoglobin G gamma beta^+^ thalassemia
  • Hereditary persistence of fetal hemoglobin linked to beta-globulin gene cluster
  • Hereditary persistence of fetal hemoglobin thalassemia
  • Hereditary persistence of fetal hemoglobin unlinked to beta-globulin gene cluster
  • Hereditary persistence of fetal hemoglobin, nondeletion type

Information for Patients


Thalassemia

Also called: Cooley's anemia, Mediterranean anemia

Thalassemias are inherited blood disorders. If you have one, your body makes fewer healthy red blood cells and less hemoglobin. Hemoglobin is a protein that carries oxygen to the body. That leads to anemia. Thalassemias occur most often among people of Italian, Greek, Middle Eastern, Southern Asian, and African descent.

Thalassemias can be mild or severe. Some people have no symptoms or mild anemia. The most common severe type in the United States is called Cooley's anemia. It usually appears during the first two years of life. People with it may have severe anemia, slowed growth and delayed puberty, and problems with the spleen, liver, heart, or bones.

Doctors diagnose thalassemias using blood tests. Treatments include blood transfusions and treatment to remove excess iron from the body. If you have mild symptoms or no symptoms, you may not need treatment. In some severe cases, you may need a bone marrow transplant.

NIH: National Heart, Lung, and Blood Institute

  • Thalassemia (Medical Encyclopedia)


[Read More]
Previous Code
Previous Code D56.3
Next Code
D56.5 Next Code