Systemic disorders of connective tissue in diseases classified elsewhere (M36)
Clinical Information
Dermatomyositis - A subacute or chronic inflammatory disease of muscle and skin, marked by proximal muscle weakness and a characteristic skin rash. The illness occurs with approximately equal frequency in children and adults. The skin lesions usually take the form of a purplish rash (or less often an exfoliative dermatitis) involving the nose, cheeks, forehead, upper trunk, and arms. The disease is associated with a complement mediated intramuscular microangiopathy, leading to loss of capillaries, muscle ischemia, muscle-fiber necrosis, and perifascicular atrophy. The childhood form of this disease tends to evolve into a systemic vasculitis. Dermatomyositis may occur in association with malignant neoplasms. (From Adams et al., Principles of Neurology, 6th ed, pp1405-6)
Polymyositis - Diseases characterized by inflammation involving multiple muscles. This may occur as an acute or chronic condition associated with medication toxicity (DRUG TOXICITY); CONNECTIVE TISSUE DISEASES; infections; malignant NEOPLASMS; and other disorders. The term polymyositis is frequently used to refer to a specific clinical entity characterized by subacute or slowly progressing symmetrical weakness primarily affecting the proximal limb and trunk muscles. The illness may occur at any age, but is most frequent in the fourth to sixth decade of life. Weakness of pharyngeal and laryngeal muscles, interstitial lung disease, and inflammation of the myocardium may also occur. Muscle biopsy reveals widespread destruction of segments of muscle fibers and an inflammatory cellular response. (Adams et al., Principles of Neurology, 6th ed, pp1404-9)
Instructional Notations
Type 2 Excludes
A type 2 excludes note represents "Not included here". An excludes2 note indicates that the condition excluded is not part of the condition represented by the code, but a patient may have both conditions at the same time. When an Excludes2 note appears under a code, it is acceptable to use both the code and the excluded code together, when appropriate.
- arthropathies in diseases classified elsewhere M14
Diseases of the musculoskeletal system and connective tissue (M00–M99)
Systemic connective tissue disorders (M30-M36)
M36 Systemic disorders of connective tissue in diseases classified elsewhere
- M36.0 Dermato(poly)myositis in neoplastic disease
- M36.1 Arthropathy in neoplastic disease
- M36.2 Hemophilic arthropathy
- M36.3 Arthropathy in other blood disorders
- M36.4 Arthropathy in hypersensitivity reactions classified elsewhere
- M36.8 Systemic disorders of connective tissue in other diseases classified elsewhere
Systemic disorders of connective tissue in diseases classified elsewhere (M36)